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Archivos de cardiología de México
On-line version ISSN 1665-1731Print version ISSN 1405-9940
Abstract
HERNANDEZ-GONZALEZ, Martha et al. Pentalogy of Cantrell: A case report. Arch. Cardiol. Méx. [online]. 2006, vol.76, n.2, pp.202-207. ISSN 1665-1731.
Ectopia cordis is an extremely rare cardiac anomaly. The heart is localized partially or totally outside the thorax cavity. This anomaly occurs as an isolated defect or combined with others midline defects. Cantrell and colleagues described, in 1958, a syndrome including defects of the abdominal wall, sternum, diaphragm, pericardium and heart. There are few successful surgical cases with this pentalogy. We describe a case with this Cantrell's pentalogy. The cardiac malformation was a univentricular heart with pulmonary stenosis. The patient underwent successful surgical palliation with a systemic - to -pulmonary anastomosis and uneventful recovering.
Keywords : Cantrell's pentalogy; Univentricular heart; Surgery in congenital heart disease.