Abstract

GUTIERREZ-RIVEROL, Karla; LOZADA ROSETE, Karla Guadalupe; DOSTA HERRERA, Juan José  and  CRUZ AVELAR, Agles. Congenital Methemoglobinemia. A Case Report. Rev. Fac. Med. (Méx.) [online]. 2024, vol.67, n.1, pp.17-21.  Epub Mar 01, 2024. ISSN 2448-4865.  https://doi.org/10.22201/fm.24484865e.2024.67.1.03.

Methemoglobinemia occasionally causes cyanosis particularly in congenital methemoglobinemia. Avoidance of exposure to oxidizing agents is important for patients with congenital methemoglobinemia because of their deficient enzymatic pathways and decreased oxygen-carrying capacity. Here, we present a pediatric patient with preoperatively undiagnosed congenital methemoglobinemia who underwent catheterization with probably diagnosis of pulmonar hypertension under general anesthesia. The pediatric patient was a 10-year-old who displayed a low pulse oximetry reading of 92% prior to induction of anesthesia. Methemoglobinemia was first suspected intraoperatively because of a mismatch of SpO2 of finger pulse oximetry and SaO2 of arterial blood, and was later confirmed by multiplewavelength CO-oximetry. The pathophysiology, etiology, clinical manifestations, anesthetic considerations, and treatment options of methemoglobinemia are discussed.

Keywords : Methemoglobinemia; cyanosis; anesthesia; pulse oximetry; pediatric patient.

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