<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2565-005X</journal-id>
<journal-title><![CDATA[Gaceta mexicana de oncología]]></journal-title>
<abbrev-journal-title><![CDATA[Gac. mex. oncol.]]></abbrev-journal-title>
<issn>2565-005X</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Oncología A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2565-005X2025000500046</article-id>
<article-id pub-id-type="doi">10.24875/j.gamo.25000001</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[PEComa retroperitoneal: un tumor raro de comportamiento incierto. Reporte de caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Retroperitoneal PEComa: a rare tumor with uncertain behavior. Case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Reay-Mandujano]]></surname>
<given-names><![CDATA[Erick D.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rueda-Don-Juan]]></surname>
<given-names><![CDATA[Erick]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[García-Sánchez]]></surname>
<given-names><![CDATA[Manuel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ocaña-Lorenzo]]></surname>
<given-names><![CDATA[Rubén]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sánchez-Luna]]></surname>
<given-names><![CDATA[Yetlanezi G.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Médico Nacional La Raza, IMSS Hospital de Especialidades Dr. Antonio Fraga Mouret ]]></institution>
<addr-line><![CDATA[ Ciudad de México]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<volume>24</volume>
<fpage>46</fpage>
<lpage>51</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2565-005X2025000500046&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2565-005X2025000500046&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2565-005X2025000500046&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen El tumor perivascular intraepitelial (PEComa) es una entidad rara cuyo origen se encuentra en el tejido mesenquimatoso. Presentamos el caso de una mujer de 58 años con aumento del volumen abdominal secundario a un PEComa cuya localización retroperitoneal y tamaño es poco frecuente y sugiere un comportamiento maligno, que requiere tratamiento quirúrgico y terapia adyuvante. Su diagnóstico representó un reto por su presentación inespecífica y la baja incidencia de la etiología.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Perivascular epithelioid cell tumor (PEComa) is a rare entity whose origin lies in mesenchymal tissue. We present the case of a 58-year-old woman with abdominal swelling secondary to a PEComa, whose retroperitoneal location and size are uncommon and suggest malignant behavior, requiring surgical treatment and adjuvant therapy. Its diagnosis posed a challenge due to its nonspecific presentation and the low incidence of the etiology.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[PEComa]]></kwd>
<kwd lng="es"><![CDATA[Tumor retroperitoneal]]></kwd>
<kwd lng="es"><![CDATA[Melan-A]]></kwd>
<kwd lng="es"><![CDATA[Actina de músculo liso]]></kwd>
<kwd lng="es"><![CDATA[Reporte de caso]]></kwd>
<kwd lng="en"><![CDATA[PEComa]]></kwd>
<kwd lng="en"><![CDATA[Retroperitoneal tumor]]></kwd>
<kwd lng="en"><![CDATA[Melan-A]]></kwd>
<kwd lng="en"><![CDATA[Smooth muscle actin]]></kwd>
<kwd lng="en"><![CDATA[Case report]]></kwd>
</kwd-group>
</article-meta>
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