<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1870-199X</journal-id>
<journal-title><![CDATA[Revista odontológica mexicana]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Odont. Mex]]></abbrev-journal-title>
<issn>1870-199X</issn>
<publisher>
<publisher-name><![CDATA[Universidad Nacional Autónoma de México, Facultad de Odontología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1870-199X2022000400040</article-id>
<article-id pub-id-type="doi">10.22201/fo.1870199xp.2022.26.4.79743</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Desarrollo orofacial y manifestaciones craneofaciales del síndrome de Silver-Russell: presentación de caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Orofacial Development and Craniofacial Manifestations of Silver-Russell Syndrome: Case Report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Santana]]></surname>
<given-names><![CDATA[Daiana Cristina Pereira]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lasso]]></surname>
<given-names><![CDATA[Daniel Maurício Meza]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Santos]]></surname>
<given-names><![CDATA[Luís Cláudio Cardoso]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Borges]]></surname>
<given-names><![CDATA[Eduardo Francisco de Deus]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Azevedo]]></surname>
<given-names><![CDATA[Roberto Almeida-de]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidade Federal da Bahia Faculdade de Odontologia ]]></institution>
<addr-line><![CDATA[Salvador ]]></addr-line>
<country>Brazil</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidade Federal da Bahia Faculdade de Odontologia ]]></institution>
<addr-line><![CDATA[Salvador ]]></addr-line>
<country>Brazil</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>26</volume>
<numero>4</numero>
<fpage>40</fpage>
<lpage>45</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1870-199X2022000400040&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1870-199X2022000400040&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1870-199X2022000400040&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Introducción:  el Síndrome de Silver-Russell es una enfermedad heterogénea en sus manifestaciones clínicas y genéticas, donde se observa restricción de crecimiento pre-natal y pos-natal, macrocefalia relativa, asimetría corporal y algunas características faciales típicas que principalmente incluyen rostro pequeño y triangular, boca grande y comisuras invertidas, frente aumentada, perímetro cefálico normal y micrognatismo.  Objetivo:  detallar los hallazgos craneofaciales a través de una presentación del caso de una paciente con el síndrome referido, atendida por el Centrinho de las Obras Sociales Irmã Dulce, en Salvador, Bahia, Brasil, con el propósito de orientar al odontólogo en relación al diagnóstico y posibles conductas terapéuticas.  Presentación del caso: paciente femenino de ocho años de edad, diagnosticada con el síndrome de Silver-Russell, con bajo peso al nacer y dificultad para ganar peso desde la infancia. Se manifestó con características faciales clásicas del síndrome (rostro triangular, micrognatia, región frontal prominente, comisuras labiales invertidas), además, la presencia de hendidura palatina, un hallazgo poco común en el síndrome. La paciente se encontraba programada para intervención quirúrgica para rehabilitación de la hendidura en el paladar (posterior al aumento de peso estipulado) y acompañamiento orto-quirúrgico complementario.  Conclusiones: en la literatura científica odontológica, hay escasos trabajos que aborden el tema. Enfatizamos la necesidad de un acompañamiento precoz de estos pacientes a fin de identificar, prevenir y corregir las manifestaciones ocasionadas por el síndrome.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Introduction:  Silver-Russell syndrome is a heterogeneous disease in its clinical and genetic manifestations, feature prenatal and postnatal growth restriction, relative macrocephaly, body asymmetry and some typical facial characteristics that mainly include a small and triangular face, large mouth and inverted lip corners, prominent forehead, normal head circumference and micrognathism.  Objective:  To detail the craniofacial findings through the case presentation of a patient with the referred syndrome, attended by the Centrinho das Obras Sociais Irmã Dulce, in Salvador, Bahia, Brazil, with the purpose of guiding the dentist in relation to the diagnosis and possible therapeutic conducts.  Case presentation: An eight-year-old female patient, diagnosed with Silver-Russell syndrome, who presented low birth weight and difficulty gaining weight since childhood. She presented the classic facial characteristics of the syndrome (triangular face, micrognathia, prominent frontal region, inverted lip commissures), in addition to the presence of cleft palate, a rare characteristic in the syndrome. The patient was scheduled for surgery to rehabilitate the cleft in the palate (after stipulated weight gain) and complementary ortho surgical support.  Conclusions:  in the scientific dental literature, there are few works that address the topic. We emphasise the need for early monitoring of these patients in order to identify, prevent and correct the manifestations caused by the syndrome.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Silver-Russell]]></kwd>
<kwd lng="es"><![CDATA[impresión genómica]]></kwd>
<kwd lng="es"><![CDATA[anomalías Craneofaciales]]></kwd>
<kwd lng="en"><![CDATA[Silver-Russell Syndrome]]></kwd>
<kwd lng="en"><![CDATA[genomic imprinting]]></kwd>
<kwd lng="en"><![CDATA[craniofacial anomalies]]></kwd>
</kwd-group>
</article-meta>
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