<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0300-9041</journal-id>
<journal-title><![CDATA[Ginecología y obstetricia de México]]></journal-title>
<abbrev-journal-title><![CDATA[Ginecol. obstet. Méx.]]></abbrev-journal-title>
<issn>0300-9041</issn>
<publisher>
<publisher-name><![CDATA[Federación Mexicana de Colegios de Obstetricia y Ginecología A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0300-90412019000200139</article-id>
<article-id pub-id-type="doi">10.24245/gom.v87i2.2508</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Herlyn-Werner-Wünderlich: dos modalidades diferentes de manifestación. Reporte de dos casos]]></article-title>
<article-title xml:lang="en"><![CDATA[Herlyn-Werner-Wunderlich syndrome: two different presentation modalities. Report of two cases]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sepúlveda-Agudelo]]></surname>
<given-names><![CDATA[Janer]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Jaimes-Carvajal]]></surname>
<given-names><![CDATA[Hermes]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad Industrial de Santander Departamento de Ginecoobstetricia ]]></institution>
<addr-line><![CDATA[Bucaramanga ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad Industrial de Santander Departamento de Ginecoobstetricia ]]></institution>
<addr-line><![CDATA[Bucaramanga ]]></addr-line>
<country>Colombia</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2019</year>
</pub-date>
<volume>87</volume>
<numero>2</numero>
<fpage>139</fpage>
<lpage>145</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0300-90412019000200139&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0300-90412019000200139&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0300-90412019000200139&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  ANTECEDENTES: El síndrome de Herlyn-Werner-Wünderlich es una anomalía congénita mülleriana rara, que se caracteriza por la asociación entre útero didelfo, obstrucción del tabique vaginal y agenesia renal.  PRIMER CASO:  Paciente de 13 años, con dolor pélvico severo de 8 días de evolución. Durante el examen físico refirió dolor abdominal generalizado. La ecografía pélvica abdominal mostró: útero bicorne con hematocolpos y la resonancia magnética nuclear: útero único con hematocolpos y agenesia renal derecha. En la laparoscopia se evidenció el útero didelfo, con hematosalpinx, síndrome adherencial moderado de epiplón y focos de endometriosis. Se efectuaron la incisión del tabique vaginal y su resección. Con esto se consiguió el drenaje completo del hematocolpos y fue posible la vaginoplastia; la paciente tuvo buena evolución.  SEGUNDO CASO:  Paciente de 30 años, con dismenorrea, dolor pélvico y ciclos regulares. En el examen físico se observaron dos cuellos uterinos: el derecho de aspecto normal y el izquierdo puntiforme. La ecografía mostró: útero didelfo con colección líquida en el medio. La resonancia magnética reportó: útero didelfo y agenesia renal izquierda. En la histeroscopia se evidenció, en el cuello derecho y a la mitad del útero una cavidad tubular. El endometrio y ostium derecho normal. El cuello izquierdo era rudimentario y puntiforme, con salida de material purulento. La laparoscopia evidenció dos hemiúteros con trompas y ovarios normales.  CONCLUSIÓN: El diagnóstico temprano de esta anomalía congénita disminuye la morbilidad a largo plazo, la posibilidad de endometriosis, deterioro de la fertilidad y las complicaciones obstétricas. El tratamiento es con técnicas de mínimo acceso que ofrecen más ventajas: magnificación del campo quirúrgico, menor dolor posoperatorio, recuperación más rápida y mejor resultado estético.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  BACKGROUND: The Herlyn-Werner-Wünderlich syndrome is a rare Müllerian congenital anomaly, characterized by the association between didelphus uterus, obstruction of the vaginal septum and renal agenesia.  FIRST CASE:  Patient of 13 years, with severe pelvic pain of 8 days of evolution. During the physical examination he reported generalized abdominal pain. Abdominal pelvic ultrasound showed: bicornuate uterus with hematocolpos and nuclear magnetic resonance: single uterus with hematocolpos and right renal agenesis. In laparoscopy the didelphus uterus was evidenced, with hematosalpinx, moderate adherent adhesion syndrome and foci of endometriosis. The incision of the vaginal septum and its resection were made. With this, complete drainage of the hematocolpos was achieved and vaginoplasty was possible; the patient had a good evolution.  SECOND CASE:  Patient of 30 years, with dysmenorrhea, pelvic pain and regular cycles. In the physical examination two uterine necks were observed: the right one of normal aspect and the left one punctate. The ultrasound showed: uterus didelphy with liquid collection in the middle. Magnetic resonance reported: didelphys uterus and left renal agenesis. The hysteroscopy revealed a tubular cavity in the right neck and in the middle of the uterus. The endometrium and normal right ostium. The left neck was rudimentary and punctate, with leakage of purulent material. The laparoscopy showed two hemiutero with normal tubes and ovaries.  CONCLUSION:  Early diagnosis of this congenital anomaly decreases long-term morbidity, the possibility of endometriosis, impaired fertility and obstetric complications. The treatment is with minimal access techniques that offer more advantages than open surgery.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Herlyn-Werner-Wünderlich]]></kwd>
<kwd lng="es"><![CDATA[útero didelfo]]></kwd>
<kwd lng="es"><![CDATA[hematocolpos]]></kwd>
<kwd lng="es"><![CDATA[anomalías urogenitales]]></kwd>
<kwd lng="es"><![CDATA[anomalías uriogenitales]]></kwd>
<kwd lng="es"><![CDATA[laparoscopia]]></kwd>
<kwd lng="es"><![CDATA[fertilidad]]></kwd>
<kwd lng="en"><![CDATA[Herlyn-Werner-Wünderlich syndrome]]></kwd>
<kwd lng="en"><![CDATA[Didelphus uterus]]></kwd>
<kwd lng="en"><![CDATA[Hematocolpos]]></kwd>
<kwd lng="en"><![CDATA[Uterine anomalities]]></kwd>
<kwd lng="en"><![CDATA[Urogenital abnormalities]]></kwd>
<kwd lng="en"><![CDATA[Laparoscopy]]></kwd>
<kwd lng="en"><![CDATA[Fertility]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Smith]]></surname>
<given-names><![CDATA[NA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome: management and follow-up]]></article-title>
<source><![CDATA[Fertil Steril]]></source>
<year>2007</year>
<volume>87</volume>
<page-range>918-22</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Zhu]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[New Classification of Herlyn-Werner-Wunderlich Syndrome]]></article-title>
<source><![CDATA[Chin Med J (Engl)]]></source>
<year>2015</year>
<volume>128</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>222-5</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bolonduro]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Uterine Didelphys, Obstructed Hemivagina, and Ipsilateral Renal Agenesis: Presentation and Management]]></article-title>
<source><![CDATA[Journal of Minimally Invasive Gynecology]]></source>
<year>2015</year>
<volume>22</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>313-4</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Piazza]]></surname>
<given-names><![CDATA[MJ]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Uterus Didelphys with Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA Syndrome)]]></article-title>
<source><![CDATA[JBRA Assist Reprod]]></source>
<year>2015</year>
<volume>19</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>259-62</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Ankan]]></surname>
<given-names><![CDATA[I&#304;]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Herlyn-Werner-Wunderlich syndrome (uterus didelphys, blind hemivagina and ipsilateral renal agenesis) - a case report]]></article-title>
<source><![CDATA[J Turk Ger Gynecol Assoc]]></source>
<year>2010</year>
<volume>11</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>107-9</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Pereira]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Hemivaginal septum resection in a patient with a rare variant of Herlyn-Werner-Wunderlich Syndrome]]></article-title>
<source><![CDATA[J Minim Invasive Gynecol]]></source>
<year>2014</year>
<volume>21</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>1113-7</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Tong]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Endometriosis in association with Herlyn-Werner-Wunderlich syndrome]]></article-title>
<source><![CDATA[Fertil Steril]]></source>
<year>2014</year>
<volume>102</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>790-4</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Vercellini]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Asymmetric lateral distribution of obstructed hemivagina and renal agenesis in women with uterus didelphys: institutional case series and a systematic literature review]]></article-title>
<source><![CDATA[Fertil Steril]]></source>
<year>2007</year>
<volume>87</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>719-24</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Wang]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Clinical characteristics and treatment of Herlyn-Werner-Wunderlich syndrome]]></article-title>
<source><![CDATA[Arch Gynecol Obstet]]></source>
<year>2014</year>
<volume>290</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>947-50</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Tzialidou-Palermo]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Diagnostic challenges of hemihematocolpos and dysmenorrhea in adolescents: obstructed hemivagina, didelphys or bicornuate uterus and renal aplasia is a rare female genital malformation]]></article-title>
<source><![CDATA[Arch Gynecol Obstet]]></source>
<year>2012</year>
<volume>286</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>785-91</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Fedele]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Double uterus with obstructed hemivagina and ipsilateral renal agenesis: pelvic anatomic variants in 87 cases]]></article-title>
<source><![CDATA[Hum Reprod]]></source>
<year>2013</year>
<volume>28</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>1580-3</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Del Vescovo]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Herlyn-werner-wunderlich syndrome: MRI findings, radiological guide (two cases and literature review), and differential diagnosis]]></article-title>
<source><![CDATA[BMC Medical Imaging]]></source>
<year>2012</year>
<volume>12</volume>
<numero>4</numero>
<issue>4</issue>
</nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Orazi]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases]]></article-title>
<source><![CDATA[Pediatr Radiol]]></source>
<year>2007</year>
<volume>37</volume>
<numero>7</numero>
<issue>7</issue>
<page-range>657-65</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sen]]></surname>
<given-names><![CDATA[KK]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Magnetic resonance imaging in obstructive Müllerian anomalies]]></article-title>
<source><![CDATA[J Hum Reprod Sci]]></source>
<year>2013</year>
<volume>6</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>162-4</page-range></nlm-citation>
</ref>
<ref id="B15">
<label>15</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bhoil]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Herlyn Werner Wunderlich Syndrome with Hematocolpos: An Unusual Case Report of Full Diagnostic Approach and Treatment]]></article-title>
<source><![CDATA[Int J Fertil Steril]]></source>
<year>2016</year>
<volume>10</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>136-40</page-range></nlm-citation>
</ref>
<ref id="B16">
<label>16</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Acién]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The presentation and management of complex female genital malformations]]></article-title>
<source><![CDATA[Hum Reprod Update]]></source>
<year>2016</year>
<volume>22</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>48-69</page-range></nlm-citation>
</ref>
<ref id="B17">
<label>17</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Tong]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Endometriosis in association with Herlyn-Werner-Wunderlich syndrome]]></article-title>
<source><![CDATA[Fertil Steril]]></source>
<year>2014</year>
<volume>102</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>790-4</page-range></nlm-citation>
</ref>
<ref id="B18">
<label>18</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Nabeshima]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Laparoscopic Strassman metroplasty in a postmenarcheal adolescent girl with Herlyn-Werner-Wunderlich müllerian anomaly variant, obstructed non-communicating didelphic uterus without Gartner duct pseudocyst]]></article-title>
<source><![CDATA[J Minim Invasive Gynecol]]></source>
<year>2013</year>
<volume>20</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>255-8</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
