<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0186-2391</journal-id>
<journal-title><![CDATA[Acta pediátrica de México]]></journal-title>
<abbrev-journal-title><![CDATA[Acta pediatr. Méx]]></abbrev-journal-title>
<issn>0186-2391</issn>
<publisher>
<publisher-name><![CDATA[Instituto Nacional de Pediatría]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0186-23912017000400237</article-id>
<article-id pub-id-type="doi">10.18233/apm38no4pp237-2431432</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Urgencia hipertensiva secundaria a enfermedad poliquística renal autosómica recesiva en lactante. Reporte de caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Infant hypertensive emergency secondary to autosomic recessive polycystic kidney disease. Case report.]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Quisbert-Cruz]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Zárate-Mondragón]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Nacional de Pediatría  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto Nacional de Pediatría  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>08</month>
<year>2017</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>08</month>
<year>2017</year>
</pub-date>
<volume>38</volume>
<numero>4</numero>
<fpage>237</fpage>
<lpage>243</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0186-23912017000400237&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0186-23912017000400237&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0186-23912017000400237&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen La enfermedad poliquística renal asociada a la fibrosis hepática congénita es una enfermedad hereditaria; se encuentra dentro del espectro de las enfermedades fibroquísticas hepatorrenales. Su frecuencia estimada es de 1 en 20.000 nacidos vivos para la variedad de enfermedad poliquística renal autosómica recesiva y más rara para la variedad autosómica dominante. Se presenta un reporte de caso de un paciente cuyo padecimiento se inició con crisis hipertensiva de difícil control, debido a enfermedad poliquística renal y fibrosis hepática congénita, presentación clínica poco frecuente; cabe mencionar sobre la importancia del control de la tensión arterial para prevenir complicaciones causadas por la hipertensión arterial: hipertrofia cardiaca, falla cardiaca y retinopatía crónica.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Polycystic kidney disease associated with congenital hepatic fibrosis is an inherited disease; it is within the spectrum of diseases hepatorenal fibrocystic. Its estimated frequency is 1 in 20,000 live births for the variety of autosomal recessive polycystic kidney disease and rarer for autosomal dominant variety. One case report is presented about a patient whose illness began with a difficult control hypertensive crisis arises due to polycystic kidney disease and congenital hepatic fibrosis, a rare clinical presentation. Include the importance of controlling blood pressure to prevent complications due to high blood pressure as cardiac hypertrophy, heart failure and chronic retinopathy.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[enfermedad poliquística renal]]></kwd>
<kwd lng="es"><![CDATA[enfermedad hepática congénita]]></kwd>
<kwd lng="es"><![CDATA[urgencia hipertensiva]]></kwd>
<kwd lng="es"><![CDATA[placa ductal]]></kwd>
<kwd lng="en"><![CDATA[polycystic kidney disease]]></kwd>
<kwd lng="en"><![CDATA[congenital liver disease]]></kwd>
<kwd lng="en"><![CDATA[hypertensive emergency]]></kwd>
<kwd lng="en"><![CDATA[ductal plate]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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