<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0028-3746</journal-id>
<journal-title><![CDATA[Neumología y cirugía de tórax]]></journal-title>
<abbrev-journal-title><![CDATA[Neumol. cir. torax]]></abbrev-journal-title>
<issn>0028-3746</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Neumología y Cirugía de Tórax; Instituto Nacional de Enfermedades Respiratorias Ismael Cosío Villegas; Sociedad Cubana de Neumología; Sociedad Paraguaya de Neumología; Sociedad Boliviana de Neumología.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0028-37462024000100017</article-id>
<article-id pub-id-type="doi">10.35366/118572</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Traqueobroncopatía osteocondroplásica como causa de estenosis severa de la vía aérea. Reporte de caso y revisión de la literatura]]></article-title>
<article-title xml:lang="en"><![CDATA[Tracheobronchopathia osteochondroplastica as a cause of severe airway stenosis. Case report and literature review]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Siado-Guerrero]]></surname>
<given-names><![CDATA[Sergio Andrés]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Motta-Aguirre]]></surname>
<given-names><![CDATA[María Paula]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Valverde-Cortés]]></surname>
<given-names><![CDATA[Julián Andrés]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lara-Sánchez]]></surname>
<given-names><![CDATA[Rodrigo Armando]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad El Bosque Clínica Medilaser ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Clínica Medilaser  ]]></institution>
<addr-line><![CDATA[Neiva Huila]]></addr-line>
<country>Colombia</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2024</year>
</pub-date>
<volume>83</volume>
<numero>1</numero>
<fpage>17</fpage>
<lpage>21</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0028-37462024000100017&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0028-37462024000100017&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0028-37462024000100017&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: La traqueobroncopatía osteocondroplásica es una patología poco frecuente, con una tasa de incidencia de entre 0.25 y 0.3% en autopsias y aproximadamente en 0.01 a 0.8% en hallazgos broncoscópicos. En nuestro medio, no contamos con estadísticas específicas debido a su rara presentación y diagnóstico. Su etiología aún no está bien establecida; aunque se plantea asociación con déficit de inmunoglobulina A y la proteína 2 morfogenética de hueso, además de posibles infecciones por gérmenes o micobacterias. Clínicamente, se caracteriza por la aparición de lesiones nodulares de aspecto osteocartilaginoso en la submucosa de las vías respiratorias centrales del paciente, que pueden protruir hacia la luz traqueal o bronquial, ocasionando generalmente síntomas inespecíficos como tos, hemoptisis, disnea, sibilancias e infecciones respiratorias recurrentes y, como en el caso de nuestro paciente, falla ventilatoria. Presentamos el reporte de un caso de un paciente que ingresó a nuestra institución con un cuadro de tos y disnea que lo llevó a falla ventilatoria, requiriendo inicialmente manejo con ventilación mecánica no invasiva. Posteriormente, se realizaron estudios de extensión que evidenciaron en la tomografía de tórax la presencia de lesiones calcificadas y nódulos en la vía aérea superior. Estas lesiones se confirmaron mediante broncoscopia, mostrando características osteocartilaginosas. El reporte patológico de la biopsia de dichas lesiones fue compatible con traqueobroncopatía osteocondroplásica. El paciente fue tratado con antibiótico y dilataciones neumáticas de las lesiones obstructivas en la vía aérea superior. Posteriormente, presentó una evolución clínica adecuada, resolviendo la falla ventilatoria y siendo dado de alta sin requerimientos de oxígeno suplementario ni soportes adicionales.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Tracheobronchopathia osteochondroplastica is a rare condition, with an incidence rate between 0.25 and 0.3% in autopsy studies and approximately 0.01 to 0.8% in bronchoscopic findings. In our setting, we do not have specific statistics due to its rare presentation and diagnosis. Its etiology is still not well established, although it has been associated with immunoglobulin A deficiency and bone morphogenetic protein 2, as well as possible infections by bacteria or mycobacteria. Clinically, it is characterized by the appearance of osteocartilaginous nodular lesions in the submucosa of the central airways, which may protrude into the tracheal or bronchial lumen, generally causing nonspecific symptoms such as cough, hemoptysis, dyspnea, wheezing, and recurrent respiratory infections, and, as in the case of our patient, ventilatory failure. We present the case report of a patient who was admitted to our institution with a history of cough and dyspnea, leading to ventilatory failure, initially requiring non-invasive mechanical ventilation (NIMV). Further studies revealed the presence of calcified lesions and nodules in the upper airway on chest tomography. These lesions were confirmed by bronchoscopy, showing osteocartilaginous characteristics. The pathological report of the biopsy of these lesions was consistent with tracheobronchopathia osteochondroplastica. The patient was treated with antibiotic coverage and pneumatic dilations of the obstructive lesions in the upper airway. Subsequently, the patient showed adequate clinical improvement, resolving the ventilatory failure and being discharged without the need for supplemental oxygen or additional support.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[traqueobroncopatía osteocondroplásica]]></kwd>
<kwd lng="es"><![CDATA[obstrucción vía aérea]]></kwd>
<kwd lng="es"><![CDATA[estenosis traqueal]]></kwd>
<kwd lng="es"><![CDATA[displasia benigna de la tráquea]]></kwd>
<kwd lng="en"><![CDATA[tracheobronchopathia osteochondroplastica]]></kwd>
<kwd lng="en"><![CDATA[airway obstruction]]></kwd>
<kwd lng="en"><![CDATA[tracheal stenosis]]></kwd>
<kwd lng="en"><![CDATA[benign tracheal dysplasia]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Abali]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[A rare case of rapidly progressive tracheobronchopathia osteochondroplastica]]></article-title>
<source><![CDATA[Respir Med Case Rep]]></source>
<year>2023</year>
<volume>43</volume>
<page-range>101853</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Silveira]]></surname>
<given-names><![CDATA[MGM]]></given-names>
</name>
<name>
<surname><![CDATA[Castellano]]></surname>
<given-names><![CDATA[MVCO]]></given-names>
</name>
<name>
<surname><![CDATA[Fuzi]]></surname>
<given-names><![CDATA[CE]]></given-names>
</name>
<name>
<surname><![CDATA[Coletta]]></surname>
<given-names><![CDATA[ENAM]]></given-names>
</name>
<name>
<surname><![CDATA[Spinosa]]></surname>
<given-names><![CDATA[GN]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Tracheobronchopathia osteochondroplastica]]></article-title>
<source><![CDATA[J Bras Pneumol]]></source>
<year>2017</year>
<volume>43</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>151-3</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[García]]></surname>
<given-names><![CDATA[CA]]></given-names>
</name>
<name>
<surname><![CDATA[Sangiovanni]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Zúñiga-Restrepo]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Morales]]></surname>
<given-names><![CDATA[EI]]></given-names>
</name>
<name>
<surname><![CDATA[Sua]]></surname>
<given-names><![CDATA[LF]]></given-names>
</name>
<name>
<surname><![CDATA[Fernández-Trujillo]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Tracheobronchopathia osteochondroplastica-clinical, radiological, and endoscopic correlation: case series and literature review]]></article-title>
<source><![CDATA[J Investig Med High Impact Case Rep]]></source>
<year>2020</year>
<volume>8</volume>
<page-range>2324709620921609</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Jabbardarjani]]></surname>
<given-names><![CDATA[HR]]></given-names>
</name>
<name>
<surname><![CDATA[Radpey]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Kharabian]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Masjedi]]></surname>
<given-names><![CDATA[MR]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Tracheobronchopathia osteochondroplastica: presentation of ten cases and review of the literature]]></article-title>
<source><![CDATA[Lung]]></source>
<year>2008</year>
<volume>186</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>293-7</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Ulasli]]></surname>
<given-names><![CDATA[SS]]></given-names>
</name>
<name>
<surname><![CDATA[Kupeli]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Tracheobronchopathia osteochondroplastica: a review of the literature]]></article-title>
<source><![CDATA[Clin Respir J]]></source>
<year>2015</year>
<volume>9</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>386-91</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Prakash]]></surname>
<given-names><![CDATA[UB]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Tracheobronchopathia osteochondroplastica]]></article-title>
<source><![CDATA[Semin Respir Crit Care Med]]></source>
<year>2002</year>
<volume>23</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>167-75</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Álvarez-Nuño]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Fernández-Morais]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Fernández-Cascón]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Vallejo-Valdezate]]></surname>
<given-names><![CDATA[LA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Traqueobroncopatía osteocondroplásica. Descripción de un caso]]></article-title>
<source><![CDATA[Rev ORL]]></source>
<year>2017</year>
<volume>8</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>243-7</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Hayes]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Tracheopathia osteoplastica misdiagnosed as asthma]]></article-title>
<source><![CDATA[J Asthma]]></source>
<year>2007</year>
<volume>44</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>253-5</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="">
<collab>London SWTranspatholSoc</collab>
<source><![CDATA[1957 undefined. Ossific deposits on the larynx, trachea and bronchi. cir.nii.ac.jp [Internet]]]></source>
<year></year>
</nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Leske]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Lazor]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Coetmeur]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Crestani]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Chatté]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Cordier]]></surname>
<given-names><![CDATA[JF]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Tracheobronchopathia osteochondroplastica: a study of 41 patients]]></article-title>
<collab>Groupe d&#8217;Etudes et de Recherche sur les Maladies &#8220;Orphelines&#8221; Pulmonaires (GERM&#8221;O&#8221;P)</collab>
<source><![CDATA[Medicine (Baltimore)]]></source>
<year>2001</year>
<volume>80</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>378-90</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Marom]]></surname>
<given-names><![CDATA[EM]]></given-names>
</name>
<name>
<surname><![CDATA[Goodman]]></surname>
<given-names><![CDATA[PC]]></given-names>
</name>
<name>
<surname><![CDATA[McAdams]]></surname>
<given-names><![CDATA[HP]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Diffuse abnormalities of the trachea and main bronchi]]></article-title>
<source><![CDATA[AJR Am J Roentgenol]]></source>
<year>2001</year>
<volume>176</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>713-7</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Wang]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
<name>
<surname><![CDATA[Hu]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Liu]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Wang]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Tracheobronchopathia osteochondroplastica: five cases report and literature review]]></article-title>
<source><![CDATA[Ear Nose Throat J]]></source>
<year>2020</year>
<volume>99</volume>
<numero>10</numero>
<issue>10</issue>
<page-range>NP111-8</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
