<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2565-005X</journal-id>
<journal-title><![CDATA[Gaceta mexicana de oncología]]></journal-title>
<abbrev-journal-title><![CDATA[Gac. mex. oncol.]]></abbrev-journal-title>
<issn>2565-005X</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Oncología A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2565-005X2019000500012</article-id>
<article-id pub-id-type="doi">10.24875/j.gamo.19000096</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Tumor anexial en el síndrome de Mayer-Rokitansky-Küster- Hauser. Presentación de un caso clínico y revisión de la literatura]]></article-title>
<article-title xml:lang="en"><![CDATA[Adnexal tumor in Mayer-Rokitansky-Küster-Hauser syndrome. Presentation of a clinical case and review of the literatura]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Padrón-Rivera]]></surname>
<given-names><![CDATA[Luis Héctor]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Barrera-Franco]]></surname>
<given-names><![CDATA[José Luis]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López-Zavala]]></surname>
<given-names><![CDATA[Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Dolores-Velázquez]]></surname>
<given-names><![CDATA[Rigoberto]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,COE Cirugía Oncológica ]]></institution>
<addr-line><![CDATA[Toluca Estado de México]]></addr-line>
<country>México</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,COE Dirección Centro Oncológico Estatal ]]></institution>
<addr-line><![CDATA[Toluca Estado de México]]></addr-line>
<country>México</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,COE Servicio de Tumores Ginecológicos ]]></institution>
<addr-line><![CDATA[Toluca Estado de México]]></addr-line>
<country>México</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,COE Coordinación de Cirugía Oncológica ]]></institution>
<addr-line><![CDATA[Toluca Estado de México]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2019</year>
</pub-date>
<volume>18</volume>
<fpage>60</fpage>
<lpage>63</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2565-005X2019000500012&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2565-005X2019000500012&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2565-005X2019000500012&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Introducción: El síndrome de Mayer-Rokitansky-Küster-Hauser (MRKH), definido como hipoplasia congénita de las estructuras derivadas de los conductos de Müller, se presenta en pacientes de sexo femenino, generalmente con adecuado desarrollo y con cariotipo 46XX, con una incidencia de 1/5,000, y es la segunda causa de consulta por amenorrea secundaria. Clásicamente se divide en tipo I, o aislada, y tipo II, asociada a otras malformaciones. Se han descrito casos aislados de MRKH asociados a presencia de tumores anexiales.  Caso clínico: Se presenta el caso de una paciente con diagnóstico de MRKH tipo II, con presencia de tumor anexial, que de acuerdo con el índice de Jacobs presenta riesgo de malignidad y que fue tratada en nuestra institución de acuerdo a las guías internacionales de práctica clínica.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Introduction: The Mayer-Rokitansky-Küster-Hauser (MRKH), defined as congenital hypoplasia of the structures derived from the müllerian ducts, occurs in female patients, usually with proper development and karyotype 46XX, with an incidence of 1/5,000, and is the second cause of consultation by secondary amenorrhea. It is classically divided into type I, or isolated, and type II, associated with other malformations. There have been described isolated cases of MRKH associated with the presence of adnexal tumors.  Clinical case: A case of a female patient with a diagnosis of type II MRKH with the presence of adnexal tumor is presented, which according to Jacobs presents risk of malignancy; she was treated at our institution according to international clinical practice guidelines.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[MRKH]]></kwd>
<kwd lng="es"><![CDATA[Tumor anexial]]></kwd>
<kwd lng="es"><![CDATA[Guías Internacionales de práctica clínica]]></kwd>
<kwd lng="en"><![CDATA[MRKH]]></kwd>
<kwd lng="en"><![CDATA[Adnexal tumor]]></kwd>
<kwd lng="en"><![CDATA[International Clinical Practice Guidelines]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Guerrier]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Mouchel]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Pasquier]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Pellerin]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome (congenital absence of uterus and vagina) &#8211;phemotypic manifestations and genetic approaches]]></article-title>
<source><![CDATA[J Negat Results Biomed]]></source>
<year>2006</year>
<volume>5</volume>
<page-range>1</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Morcel]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Camborieux]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Guerrier]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome]]></article-title>
<source><![CDATA[Orphanet J Rare Dis]]></source>
<year>2007</year>
<volume>2</volume>
<page-range>13</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Londra]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Chuong]]></surname>
<given-names><![CDATA[FS]]></given-names>
</name>
<name>
<surname><![CDATA[Kolp]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Mayer-Rokitansky-Küster-Hauser syndrome:a review]]></article-title>
<source><![CDATA[Int J Womens Health]]></source>
<year>2015</year>
<volume>7</volume>
<page-range>865-70</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Ulukus]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Ulukus]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Tavmergen]]></surname>
<given-names><![CDATA[EN]]></given-names>
</name>
<name>
<surname><![CDATA[Terek]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Zekioglu]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Mayer-Rokitansky-Küster-Hauser syndrome with a borderline ovarian serous cystadenoma:A case report]]></article-title>
<source><![CDATA[Ege Tip Dergisl]]></source>
<year>2002</year>
<volume>41</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>255-7</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sook]]></surname>
<given-names><![CDATA[BH]]></given-names>
</name>
<name>
<surname><![CDATA[Ryu]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Kim]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Kim]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
<name>
<surname><![CDATA[Song]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Cancer of the supernumerary ovary in Mayer-Rokitansky-Küster-Hauser Syndrome:A case report]]></article-title>
<source><![CDATA[Oncol Lett]]></source>
<year>2013</year>
<volume>5</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>598-600</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Silva]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Wickramasinghe]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
<name>
<surname><![CDATA[Gange]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Mayer-Rokitansky-Kuster-Hauser syndrome associated with serous papillary cystadenocarcinoma of the ovary]]></article-title>
<source><![CDATA[Sri Lanka Journal of Obstetrics and Gynaecology]]></source>
<year>2012</year>
<volume>32</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>99-105</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Ghirardini]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Magnani]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Mayer-Rokitansky-Küster-Hauser Syndrome and ovarian cancer. Report of a case]]></article-title>
<source><![CDATA[Clin Exp Obstet Gynecol]]></source>
<year>1995</year>
<volume>22</volume>
<page-range>247-8</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Koonings]]></surname>
<given-names><![CDATA[PP]]></given-names>
</name>
<name>
<surname><![CDATA[Marayati]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Schlaerth]]></surname>
<given-names><![CDATA[JB]]></given-names>
</name>
<name>
<surname><![CDATA[Lobo]]></surname>
<given-names><![CDATA[RA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Mayer-Rokitansky-Küster-Hauser syndrome associated withendodermal sinus tumor of the ovary]]></article-title>
<source><![CDATA[Fertility Sterility]]></source>
<year>1991</year>
<volume>56</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>577-8</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Gallardo]]></surname>
<given-names><![CDATA[Rincón D]]></given-names>
</name>
<name>
<surname><![CDATA[Montalvo]]></surname>
<given-names><![CDATA[Esquivel G]]></given-names>
</name>
<name>
<surname><![CDATA[González]]></surname>
<given-names><![CDATA[Enciso A]]></given-names>
</name>
<name>
<surname><![CDATA[Cantúde]]></surname>
<given-names><![CDATA[León DF]]></given-names>
</name>
<name>
<surname><![CDATA[Isla]]></surname>
<given-names><![CDATA[Ortíz D]]></given-names>
</name>
<name>
<surname><![CDATA[Muñoz]]></surname>
<given-names><![CDATA[González DE]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Onco Guía. Cáncer epitelial de ovario]]></article-title>
<source><![CDATA[Cancerología]]></source>
<year>2011</year>
<volume>6</volume>
<page-range>53-60</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Dodge]]></surname>
<given-names><![CDATA[JE]]></given-names>
</name>
<name>
<surname><![CDATA[Covens]]></surname>
<given-names><![CDATA[AL]]></given-names>
</name>
<name>
<surname><![CDATA[Lacchetti]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Elit]]></surname>
<given-names><![CDATA[LM]]></given-names>
</name>
<name>
<surname><![CDATA[Le]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Devries-Aboud]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Management of a suspicious adnexal mass:a clinical practice guideline]]></article-title>
<source><![CDATA[Curr Oncol]]></source>
<year>2012</year>
<volume>19</volume>
<page-range>244-57</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="">
<collab>Clinical Practice Guidelines in Oncology</collab>
<source><![CDATA[Ovarian Cancer [Internet]. National Comprehensive Cancer Network]]></source>
<year></year>
</nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Jacobs]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
<name>
<surname><![CDATA[Oram]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Fairbanks]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Turner]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Frost]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Grudzinskas]]></surname>
<given-names><![CDATA[JG]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[A risk of malignancy index incorporating CA-125, ultrasound and menopausal status for the accurate preoperative diagnosis of ovarian cancer]]></article-title>
<source><![CDATA[Br J Obstet Gynaecol]]></source>
<year>1990</year>
<volume>97</volume>
<page-range>922-9</page-range></nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Tingulstad]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Hagen]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Skjeldestad]]></surname>
<given-names><![CDATA[FE]]></given-names>
</name>
<name>
<surname><![CDATA[Onsrud]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Kiserud]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Halvorsen]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Evaluation of a risk of malignancy index based on serum CA-125, ultrasound findings and menopausal status in the pre-operative diagnosis of pelvic masses]]></article-title>
<source><![CDATA[Br J Obstet Gynaecol]]></source>
<year>1996</year>
<volume>103</volume>
<page-range>826-31</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<collab>Ovarian Cancer:Recognition and initial management</collab>
<article-title xml:lang=""><![CDATA[Appendix:Risk of malignancy index (RMI I), Clinical Guidance CG122]]></article-title>
<source><![CDATA[National Institute for Health and Care Excelence]]></source>
<year>2011</year>
</nlm-citation>
</ref>
</ref-list>
</back>
</article>
