<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2007-4085</journal-id>
<journal-title><![CDATA[Revista mexicana de urología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. mex. urol.]]></abbrev-journal-title>
<issn>2007-4085</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Urología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2007-40852020000400009</article-id>
<article-id pub-id-type="doi">10.48193/revistamexicanadeurologa.v80i4.617</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Angiomiolipoma hemorrágico espontáneo asociado a esclerosis tuberosa que conduce a nefrectomía urgente - Reporte de un caso y revisión de la literatura]]></article-title>
<article-title xml:lang="en"><![CDATA[Spontaneous bleeding from an angiomyolipoma associated with tuberous sclerosis, leading to emergency nephrectomy: A case report and literature review]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gallegos-Sánchez]]></surname>
<given-names><![CDATA[Gustavo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rosales-Velázquez]]></surname>
<given-names><![CDATA[César Eduardo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ruvalcaba-Oceguera]]></surname>
<given-names><![CDATA[Guillermo Enrique]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Aragón-Castro]]></surname>
<given-names><![CDATA[Marco Antonio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gutiérrez-Rosales]]></surname>
<given-names><![CDATA[Rubén]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Velázquez-Morales]]></surname>
<given-names><![CDATA[Igor Octavio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ochoa-Gutiérrez]]></surname>
<given-names><![CDATA[Hugo Enrique]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ordoñez-Jurado]]></surname>
<given-names><![CDATA[Aldo Uriel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Montaño-Roca]]></surname>
<given-names><![CDATA[Benjamín Enrique]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto de Seguridad Social del Estado de México y Municipios Centro Médico Arturo Montiel Rojas ]]></institution>
<addr-line><![CDATA[Toluca ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto Mexicano del Seguro Social Hospital General Regional 251 ]]></institution>
<addr-line><![CDATA[ Estado de México]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>08</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>08</month>
<year>2020</year>
</pub-date>
<volume>80</volume>
<numero>4</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2007-40852020000400009&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2007-40852020000400009&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2007-40852020000400009&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Descripción:  Acudió una mujer de 34 años a urgencias con dolor abdominal moderado en hipocondrio derecho (duración 3h), acompañado de hematuria y distensión abdominal progresiva y dolorosa. La tomografía reveló una tumoración sólida heterogénea de 14 cm, en riñón derecho, con hemorragia en su interior. Por datos de bajo gasto hemodinámico se transfundieron hemoderivados y mantuvo en vigilancia, persistiendo con descenso de hemoglobina hasta 7.2 gr/dl, por lo que se sometió a angioembolización selectiva urgente, tras lo cual remitió temporalmente el sangrado, recurriendo con hematuria y choque hipovolémico, que derivó en tratamiento quirúrgico definitivo mediante nefrectomía total. Su recuperación transcurrió sin incidentes. El examen histopatológico reveló un angiomiolipoma renal con hemorragia extensa.  Relevancia:  El síndrome de Wünderlich (Angiomiolipoma hemorrágico espontáneo) es una entidad rara cuya complicación más grave e indeseable es la hemorragia refractaria, que puede ser mortal.  Implicaciones clínicas:  Es importante la intervención temprana en pacientes con angiomiolipoma hemorrágico para prevenir potenciales complicaciones como hemorragia masiva y poner en riesgo la vida del paciente.  Conclusiones:  En caso de angiomiolipoma con hemorragia intratumoral y síntomas del síndrome de Wünderlich, la nefrectomía total resulta buena opción para preservar la vida del paciente, después del manejo conservador y/o angioembolización selectiva.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Description:  A 34-year-old woman came to the emergency department presenting with moderate abdominal pain in the right hypochondrium (of 3-hour duration), accompanied by hematuria and progressive and painful abdominal distention. A tomography scan revealed a 14 cm heterogenous solid tumor in the right kidney, with intratumoral bleeding. She was given a blood product transfusion due to low hemodynamic output and kept under surveillance. Hemoglobin levels continued to descend, reaching 7.2 g/dl, and so the patient underwent emergency selective angioembolization, and the bleeding temporarily stopped. The hematuria reappeared and the patient went into hypovolemic shock, leading to the definitive surgical treatment of total nephrectomy. Her recovery was uneventful. The histopathologic study reported renal angiomyolipoma with extensive bleeding.  Relevance:  Wunderlich syndrome (angiomyolipoma with spontaneous bleeding) is a rare entity whose most severe and undesirable complication is refractory bleeding, which can be fatal.  Clinical implications:  Early intervention in patients with hemorrhagic angiomyolipoma is important for preventing potentially life-threatening complications, such as massive bleeding.  Conclusions:  In cases of angiomyolipoma with intratumoral bleeding and symptoms of Wunderlich syndrome, total nephrectomy is the best option, after conservative management and/or selective angioembolization, for saving the life of the patient.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Bleeding]]></kwd>
<kwd lng="en"><![CDATA[Kidney]]></kwd>
<kwd lng="en"><![CDATA[Neoplasias]]></kwd>
<kwd lng="en"><![CDATA[Angiomyolipoma]]></kwd>
<kwd lng="es"><![CDATA[Hemorragia]]></kwd>
<kwd lng="es"><![CDATA[riñón]]></kwd>
<kwd lng="es"><![CDATA[neoplasias]]></kwd>
<kwd lng="es"><![CDATA[angiomiolipoma]]></kwd>
</kwd-group>
</article-meta>
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