<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1405-9940</journal-id>
<journal-title><![CDATA[Archivos de cardiología de México]]></journal-title>
<abbrev-journal-title><![CDATA[Arch. Cardiol. Méx.]]></abbrev-journal-title>
<issn>1405-9940</issn>
<publisher>
<publisher-name><![CDATA[Instituto Nacional de Cardiología Ignacio Chávez]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1405-99402025000200143</article-id>
<article-id pub-id-type="doi">10.24875/acm.24000057</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Circulación coronaria dependiente del ventrículo derecho en atresia pulmonar con septum ventricular íntegro. A propósito de tres pacientes sin atresia de los ostium coronarios. ¿Es necesaria una maniobra de descompresión percutánea transitoria?]]></article-title>
<article-title xml:lang="en"><![CDATA[Right ventricle-dependent coronary circulation in pulmonary atresia with intact ventricular septum. About three patients without coronary ostium atresia. Is a transient percutaneous decompression maneuver necessary?]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Colín-Ortiz]]></surname>
<given-names><![CDATA[José L.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López-Andrade]]></surname>
<given-names><![CDATA[Cecilia E.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Nacional de Pediatría Departamento de Cardiología Pediátrica ]]></institution>
<addr-line><![CDATA[ Ciudad de México]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>06</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>06</month>
<year>2025</year>
</pub-date>
<volume>95</volume>
<numero>2</numero>
<fpage>143</fpage>
<lpage>153</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1405-99402025000200143&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1405-99402025000200143&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1405-99402025000200143&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Objetivo: La atresia pulmonar con septum ventricular íntegro (AP-SVI) es una cardiopatía congénita poco frecuente que se caracteriza por un amplio espectro morfológico que puede estar asociado a anomalías en la circulación coronaria como: sinusoides, fístulas, estenosis o atresia. Algunos pacientes no presentan fístulas ventrículo-coronarias ni sinusoides intramiocárdicos, otros pacientes sí presentan conexiones ventrículo-coronarias, pero solo algunos de estos últimos tendrán circulación coronaria dependiente del ventrículo derecho (CCVDD); establecer oportunamente el diagnóstico de CCVDD es primordial, ya que el pronóstico de estos pacientes generalmente es fatal. Existen reportes de pacientes con este tipo de circulación coronaria (CCVDD) que son llevados a fisiología univentricular, pero esta opción de tratamiento sigue siendo controversial, por lo que el propósito de este manuscrito es compartir tres casos con AP-SVI y CCVDD, su desenlace y las reflexiones que nos aportan.  Método: Se realizó un estudio transversal, descriptivo, observacional de los pacientes con AP-SVI y CCVDD sin atresia de los ostium coronarios en el periodo de estudio.  Resultados: Se identificaron tres pacientes, se describen las características clínicas, angiográficas y su evolución, además se describe de forma teórica una nueva técnica o maniobra para la descompresión transitoria vía percutánea del ventrículo derecho para aquellos casos donde exista duda de la CCVDD.  Conclusiones: Un diagnóstico preciso en relación con la existencia de la CCVDD es vital. En algunos casos la interpretación de la angiografía para el diagnóstico de la CCVDD puede ser difícil de precisar y en muchos casos puede ser dependiente del operador, sin embargo consideramos necesario disponer de una técnica o maniobra que pueda determinar objetivamente y sin dudas la CCVDD en aquellos casos donde la angiografía no sea totalmente concluyente y así poder ofrecer la mejor opción terapéutica.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Objective: Pulmonary atresia with intact ventricular septum (PA-IVS) is a rare congenital heart disease characterized by a wide morphological spectrum that can be associated with abnormalities in the coronary circulation such as sinusoids, fistulas, stenosis or atresia. Some patients do not present ventriculo-coronary fistulas or intramyocardial sinusoids, other patients do present ventriculo-coronary connections, but only some of the latter will have right ventricle-dependent coronary circulation (RVDCC); timely establishment of the diagnosis of RVDCC is essential, since the prognosis of these patients is generally fatal. There are reports of patients with this type of coronary circulation (RVDCC) who were undergone to univentricular physiology, but this treatment option remains controversial, so the purpose of this manuscript is to share three cases with PA-IVS and RVDCC, their outcome and the reflections they provide us.  Method: We conducted a cross-sectional, descriptive, observational study of patients with PA-IVS and RVDCC without atresia of the coronary ostium during the study period.  Results: Three patients were identified, the clinical and angiographic characteristics and their evolution are described, and a new technique or maneuver for transient percutaneous decompress of the right ventricle is described theoretically for those cases where there is doubt about RVDCC during the angiographic study.  Conclusions: An accurate diagnosis regarding the existence of RVDCC is vital. In some cases, the interpretation of angiography for the diagnosis of RVDCC can be difficult to pinpoint and in many cases, it can be operator dependent, however we consider that is necessary to have a technique or maneuver that can objectively and without doubts determine RVDCC in those cases where angiography is not totally conclusive and thus be able to offer the best therapeutic option.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Atresia pulmonar con septum ventricular íntegro]]></kwd>
<kwd lng="es"><![CDATA[Circulación coronaria dependiente del ventrículo derecho]]></kwd>
<kwd lng="es"><![CDATA[Conexiones ventrículo-coronarias]]></kwd>
<kwd lng="es"><![CDATA[Descompresión del ventrículo derecho]]></kwd>
<kwd lng="en"><![CDATA[Pulmonary atresia with intact ventricular septum]]></kwd>
<kwd lng="en"><![CDATA[Right ventricle-dependent coronary circulation]]></kwd>
<kwd lng="en"><![CDATA[Ventriculo-coronary connections]]></kwd>
<kwd lng="en"><![CDATA[Rigth ventricle decompression]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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