<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0028-3746</journal-id>
<journal-title><![CDATA[Neumología y cirugía de tórax]]></journal-title>
<abbrev-journal-title><![CDATA[Neumol. cir. torax]]></abbrev-journal-title>
<issn>0028-3746</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Neumología y Cirugía de Tórax; Instituto Nacional de Enfermedades Respiratorias Ismael Cosío Villegas; Sociedad Cubana de Neumología; Sociedad Paraguaya de Neumología; Sociedad Boliviana de Neumología.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0028-37462023000100038</article-id>
<article-id pub-id-type="doi">10.35366/114228</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Discinesia ciliar primaria. Causa de infecciones respiratorias recurrentes: serie de tres casos]]></article-title>
<article-title xml:lang="en"><![CDATA[Primary ciliary dyskinesia. Cause of recurrent respiratory infections: three case series]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Leal-Jiménez]]></surname>
<given-names><![CDATA[Elizabeth]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Avilés-Ramírez]]></surname>
<given-names><![CDATA[Brenda Aidé]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Reyes-Rosales]]></surname>
<given-names><![CDATA[Mariana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Médico Naval SEMAR  ]]></institution>
<addr-line><![CDATA[Ciudad de México ]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2023</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2023</year>
</pub-date>
<volume>82</volume>
<numero>1</numero>
<fpage>38</fpage>
<lpage>41</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0028-37462023000100038&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0028-37462023000100038&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0028-37462023000100038&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: La discinesia ciliar primaria es una enfermedad genética poco frecuente, autosómica recesiva, que afecta el movimiento ciliar. Las manifestaciones clínicas de la enfermedad pueden presentarse desde el nacimiento con un síndrome de dificultad respiratoria o durante la infancia con tos crónica productiva y rinosinusitis no estacional, infecciones respiratorias recurrentes que incluso requieran manejo intrahospitalario, por lo que se deberá considerar como parte del abordaje de estudio de infecciones recurrentes en el paciente pediátrico. Casos clínicos: se investigó la evolución y antecedentes de importancia de tres pacientes derechohabientes de la Secretaría de Marina con reciente diagnóstico de discinesia ciliar primaria por microscopia electrónica y panel genético; presentaron cuadros de infecciones recurrentes en la infancia, los cuales requirieron manejo intrahospitalario en varias ocasiones. El objetivo del presente artículo es tener presente la enfermedad como una causa de infecciones recurrentes de vías respiratorias para realizar un adecuado abordaje, evitando secuelas en nuestros pacientes secundario a un diagnóstico tardío.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Primary ciliary dyskinesia is a rare autosomal recessive genetic disease affecting ciliary movement. The clinical manifestations of the disease can present from birth with respiratory distress syndrome or during childhood with chronic productive cough and non-seasonal rhinosinusitis, recurrent respiratory infections that even require in-hospital management, so it should be considered as part of the approach to study recurrent infections in the pediatric patient. Clinical cases: we investigated the evolution and relevant history of three patients entitled to the Secretary of the Navy with recent diagnosis of primary ciliary dyskinesia by electron microscopy and genetic panel who presented recurrent infections in childhood, which required in-hospital management on several occasions. The aim of this article is to keep in mind the disease as a cause of recurrent respiratory tract infections in order to perform an adequate approach, avoiding sequelae in our patients secondary to a late diagnosis.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[discinesia ciliar]]></kwd>
<kwd lng="es"><![CDATA[infecciones respiratorias]]></kwd>
<kwd lng="es"><![CDATA[tos crónica]]></kwd>
<kwd lng="en"><![CDATA[ciliary dyskinesia]]></kwd>
<kwd lng="en"><![CDATA[respiratory infections]]></kwd>
<kwd lng="en"><![CDATA[chronic cough]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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