<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0028-3746</journal-id>
<journal-title><![CDATA[Neumología y cirugía de tórax]]></journal-title>
<abbrev-journal-title><![CDATA[Neumol. cir. torax]]></abbrev-journal-title>
<issn>0028-3746</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Neumología y Cirugía de Tórax; Instituto Nacional de Enfermedades Respiratorias Ismael Cosío Villegas; Sociedad Cubana de Neumología; Sociedad Paraguaya de Neumología; Sociedad Boliviana de Neumología.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0028-37462018000200132</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Hallazgos polisomnográficos en niños con síndrome de Prader-Willi]]></article-title>
<article-title xml:lang="en"><![CDATA[Polysomnographic findings in children with Prader-Willi syndrome]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Silva-Cruz]]></surname>
<given-names><![CDATA[Tania Margarita]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cruz-Zorrilla]]></surname>
<given-names><![CDATA[Gabriel Eugenio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Alejandre-García]]></surname>
<given-names><![CDATA[Alejandro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cano-Salas]]></surname>
<given-names><![CDATA[María del Carmen]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Torres-Fraga]]></surname>
<given-names><![CDATA[Martha Guadalupe]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Carrillo-Alduenda]]></surname>
<given-names><![CDATA[José Luis]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Nacional de Enfermedades Respiratorias Ismael Cosío Villegas  ]]></institution>
<addr-line><![CDATA[Ciudad de México ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Clínica Somnoscan  ]]></institution>
<addr-line><![CDATA[San Pedro Garza, García Nuevo León]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>06</month>
<year>2018</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>06</month>
<year>2018</year>
</pub-date>
<volume>77</volume>
<numero>2</numero>
<fpage>132</fpage>
<lpage>136</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0028-37462018000200132&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0028-37462018000200132&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0028-37462018000200132&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen:  Antecedentes:  El síndrome de Prader-Willi es un desorden genético con múltiples factores de riesgo para desarrollar trastornos respiratorios del dormir. El objetivo del trabajo es describir los hallazgos polisomnográficos de niños con síndrome de Prader-Willi atendidos en la Clínica de Trastornos Respiratorios del Sueño del Instituto Nacional de Enfermedades Respiratorias Ismael Cosío Villegas, Ciudad de México.  Material y métodos:  Se revisaron registros clínicos del 01/enero/2005 al 31/diciembre/2015. Se incluyeron menores de 18 años de edad, con diagnóstico genético de síndrome de Prader-Willi, estudiados por polisomnografía nocturna. Se eliminaron polisomnografías con tiempo total de sueño menor a cuatro horas y/o eficiencia de sueño menor a 70%.  Resultados:  Se identificaron 4 niños, la mayoría en la adolescencia, todos con obesidad y múltiples comorbilidades. Tres pacientes cumplieron criterio de algún trastorno respiratorio del dormir. Así, 1 presentó hipoventilación durante el sueño, 1 hipoventilación durante el sueño + apnea obstructiva y un tercero con apnea central.  Conclusiones:  Los trastornos respiratorios del dormir son altamente frecuentes entre los paciente con síndrome de Prader-Willi, el trastorno más frecuente fue el síndrome de hipoventilación durante el sueño.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract:  Background:  Prader-Willi syndrome (PWS) is a genetic disorder with multiple risk factors to develop sleep disorders of breathing (SDB). The aim of the study is to describe the polysomnographic findings of children with PWS treated at the Respiratory Sleep Disorders Clinic INER.  Material and methods:  Clinical records were reviewed from January 01, 2005 to December 31, 2015. Children under 18 years of age with genetic diagnosis of PWS studied by nocturnal polysomnography were included. Polysomnograms were eliminated with total sleep time less than 4 hours and/or sleep efficiency less than 70%.  Results:  Four children were identified, mostly in adolescence, all with obesity and multiple comorbidities. Three patients met the criterion of some SDB, 1 had hypoventilation during sleep, 1 hypoventilation during sleep + obstructive apnea and another with central apnea.  Conclusions:  The SDB are highly frequent among patients with PWS, the most frequent disorder was hypoventilation syndrome during sleep.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Prader-Willi]]></kwd>
<kwd lng="es"><![CDATA[hipoventilación]]></kwd>
<kwd lng="es"><![CDATA[apnea del sueño]]></kwd>
<kwd lng="en"><![CDATA[Prader-Willi syndrome]]></kwd>
<kwd lng="en"><![CDATA[hypoventilation]]></kwd>
<kwd lng="en"><![CDATA[sleep apnea]]></kwd>
</kwd-group>
</article-meta>
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