<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2954-3835</journal-id>
<journal-title><![CDATA[Cardiovascular and metabolic science]]></journal-title>
<abbrev-journal-title><![CDATA[Cardiovasc. metab. sci]]></abbrev-journal-title>
<issn>2954-3835</issn>
<publisher>
<publisher-name><![CDATA[Asociación Nacional de Cardiólogos de México A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2954-38352024000100016</article-id>
<article-id pub-id-type="doi">10.35366/115000</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Complete heart block in an adult patient with isolated congenitally corrected transposition of the great arteries and situs inversus]]></article-title>
<article-title xml:lang="es"><![CDATA[Bloqueo auriculoventricular completo en un paciente adulto con transposición congénitamente corregida de grandes arterias aisladas y situs inversus]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Alanís-Naranjo]]></surname>
<given-names><![CDATA[José Martín]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Galeana-Abarca]]></surname>
<given-names><![CDATA[Cielmar]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Campos-Garcilazo]]></surname>
<given-names><![CDATA[Virginia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,ISSSTE Hospital Regional 1o de Octubre ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,ISSSTE Hospital Regional 1o de Octubre ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,ISSSTE Hospital Regional 1o de Octubre ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2024</year>
</pub-date>
<volume>35</volume>
<numero>1</numero>
<fpage>16</fpage>
<lpage>21</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2954-38352024000100016&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2954-38352024000100016&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2954-38352024000100016&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Congenitally corrected transposition of the great arteries (ccTGA) is a rare congenital heart disease. Many patients remain asymptomatic when no cardiac lesions are present (isolated ccTGA). In ccTGA, the atrioventricular conduction system may be abnormal, resulting in progressive dysfunction and, eventually, a Complete Heart Block (CHB). In ccTGA with situs inversus, the conduction pathway resembles a normal tract, but the atrioventricular node is located posteriorly. Compared with situs solitus, spontaneous CHB is uncommon in ccTGA patients with situs inversus. We report the case of a 40-year-old female without previous medical conditions or having a family or personal history of heart disease presented with loss of consciousness. At admission, electrocardiography revealed bradycardia, CHB, and hypertrophy of the right ventricle. Cardiovascular imaging tests detected an isolated ccTGA with situs inversus and levocardia. The Holter monitor revealed intermittent CHB. Exercise testing demonstrated chronotropic incompetence. An epicardial pacemaker was implanted, and the patient was discharged symptom-free. At a two-years follow-up remains asymptomatic. This case illustrates the importance of cardiovascular imaging in defining cardiac anatomy, ruling out other congenital heart defects, and facilitating pacing therapy in complex congenital heart disease. Congenital heart disease patients should be treated by a multidisciplinary team with expertise in permanent pacing.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: La transposición congénitamente corregida de grandes arterias (TccGA) es una cardiopatía congénita poco común. Muchos pacientes permanecen asintomáticos cuando no hay lesiones cardiacas presentes (TccGA aislada). En la TccGA, el sistema de conducción auriculoventricular puede ser anormal, lo que resulta en una disfunción progresiva y, finalmente, en un bloqueo auriculoventricular (BAV) completo. En la TccGA con situs inversus, la vía de conducción se asemeja a un tracto normal, pero el nódulo auriculoventricular se ubica posteriormente. En comparación con el situs solitus, el BAV completo espontáneo es poco común en pacientes con TccGA con situs inversus. Se presenta el caso de una mujer de 40 años sin enfermedades previas ni con antecedentes familiares o personales de cardiopatías que presentó pérdida de conciencia. Al ingreso, el electrocardiograma reveló bradicardia, BAV completo e hipertrofia del ventrículo derecho. Estudios de imagen cardiaca detectaron una TccGA aislada con situs inversus y levocardia. El monitoreo Holter reveló BAV completo intermitente. Las pruebas de esfuerzo demostraron incompetencia cronotrópica. Se le implantó un marcapasos epicárdico y la paciente fue dada de alta asintomática. Tras dos años de seguimiento permaneció asintomática. Este caso ilustra la importancia de imagen cardiovascular para definir la anatomía cardiaca, descartar otras cardiopatías congénitas y facilitar la terapia de estimulación cardiaca en cardiopatías congénitas complejas. Los pacientes con cardiopatías congénitas deben ser tratados por un equipo multidisciplinario con experiencia en estimulación cardiaca permanente.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[congenitally corrected transposition of the great arteries]]></kwd>
<kwd lng="en"><![CDATA[complete heart block]]></kwd>
<kwd lng="en"><![CDATA[congenital heart disease]]></kwd>
<kwd lng="en"><![CDATA[adult]]></kwd>
<kwd lng="en"><![CDATA[situs inversus]]></kwd>
<kwd lng="es"><![CDATA[transposición congénitamente corregida de grandes arterias]]></kwd>
<kwd lng="es"><![CDATA[bloqueo auriculoventricular completo]]></kwd>
<kwd lng="es"><![CDATA[cardiopatía congénita]]></kwd>
<kwd lng="es"><![CDATA[adulto]]></kwd>
<kwd lng="es"><![CDATA[situs inversus]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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