<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1665-1146</journal-id>
<journal-title><![CDATA[Boletín médico del Hospital Infantil de México]]></journal-title>
<abbrev-journal-title><![CDATA[Bol. Med. Hosp. Infant. Mex.]]></abbrev-journal-title>
<issn>1665-1146</issn>
<publisher>
<publisher-name><![CDATA[Instituto Nacional de Salud, Hospital Infantil de México Federico Gómez]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1665-11462025000500001</article-id>
<article-id pub-id-type="doi">10.24875/bmhim.25000036</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Diagnóstico y tratamiento de bronquiectasias en pacientes pediátricos sin fibrosis quística]]></article-title>
<article-title xml:lang="en"><![CDATA[Diagnosis and treatment of bronchiectasis in pediatric patients without cystic fibrosis]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Munevar-Velandia]]></surname>
<given-names><![CDATA[Alejandra]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Nofal-Ladino]]></surname>
<given-names><![CDATA[Juan]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Restrepo-Gualteros]]></surname>
<given-names><![CDATA[Sonia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Villamil-Osorio]]></surname>
<given-names><![CDATA[Milena]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ramírez]]></surname>
<given-names><![CDATA[Oscar]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López]]></surname>
<given-names><![CDATA[Juan F.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vélez-Tirado]]></surname>
<given-names><![CDATA[Natalia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Castaño-Jaramillo]]></surname>
<given-names><![CDATA[Lina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad El Bosque Facultad de Medicina ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Unisanitas Facultad de Medicina ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,HOMI Fundación Hospital Pediátrico la Misericordia Servicio de Neumología pediátrica ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Universidad Nacional de Colombia Facultad de Medicina ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,HOMI Fundación Hospital Pediátrico la Misericordia Servicio de Infectología Pediátrica ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af6">
<institution><![CDATA[,HOMI Fundación Hospital Pediátrico la Misericordia Servicio de Inmunología Clínica y Alergia Pediátrica ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af7">
<institution><![CDATA[,Universidad El Bosque Grupo de Inmunología Celular y Molecular ]]></institution>
<addr-line><![CDATA[Bogotá ]]></addr-line>
<country>Colombia</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>10</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>10</month>
<year>2025</year>
</pub-date>
<volume>82</volume>
<numero>5</numero>
<fpage>273</fpage>
<lpage>281</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1665-11462025000500001&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1665-11462025000500001&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1665-11462025000500001&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen Las bronquiectasias son anomalías caracterizadas por dilatación permanente de los bronquios; clínicamente se manifiestan con tos crónica, producción de esputo, disnea y exacerbaciones recurrentes. Las bronquiectasias ocurren como resultado de enfermedades genéticas, malformaciones congénitas, obstrucción endobronquial de causa infecciosa e inflamatoria y aspiración crónica, entre otras causas. La dilatación bronquial conlleva alteración de la depuración mucociliar, facilitando el atrapamiento de partículas y microorganismos que ingresan a las vías respiratorias. Los macrófagos y células epiteliales liberan citocinas proinflamatorias que promueven la quimiotaxis de neutrófilos, los cuales liberan enzimas que causan lesión en las células epiteliales, reducen la motilidad ciliar, promueven la hiperplasia glandular y el aumento en la secreción de moco, de esta forma la infección persistente perpetúa la inflamación local en los pacientes con bronquiectasias. El diagnóstico requiere un alto índice de sospecha clínica y la detección precoz permite mejorar los desenlaces clínicos. La tomografía axial computarizada de alta resolución pulmonar es el método de referencia para la confirmación diagnóstica; la realización de historia clínica completa y estudios de extensión iniciales como hemograma, inmunoglobulinas séricas totales, iontoforesis y espirometría permiten evaluar la causa subyacente y determinar la gravedad de la enfermedad. El principal objetivo del manejo es preservar la función pulmonar y detener la progresión de la enfermedad, para lo que se recomienda adoptar hábitos de vida saludables, esquemas de vacunación ampliados, realización de terapia respiratoria y uso temprano de antibióticos en exacerbaciones y colonizaciones por ciertos microorganismos.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Bronchiectasis is characterized by the permanent dilation of bronchi, clinically presenting with chronic cough, sputum production, dyspnea, and recurrent exacerbations. Bronchiectasis can occur due to genetic disorders, congenital malformations, endobronchial obstruction of infectious and inflammatory origin, and chronic aspiration, among other causes. Bronchial dilation leads to impaired mucociliary clearance, trapping particles and microorganisms in the airways. Macrophages and epithelial cells release proinflammatory cytokines that promote neutrophil chemotaxis. Neutrophils release enzymes causing epithelial cell damage, reducing ciliary motility, promoting glandular hyperplasia, and increasing mucus secretion. Persistent infection perpetuates local inflammation in bronchiectasis patients. Diagnosis requires high clinical suspicion and early detection improves clinical outcomes. High-resolution computed tomography is the gold standard for confirmation. A comprehensive medical history, initial assessments with complete blood count, total serum immunoglobulins, iontophoresis, and spirometry help assess the underlying etiology and disease severity. The primary goal is preserving lung function and halting disease progression. This involves adopting healthy lifestyles, expanded vaccination schedules, respiratory therapy, and early antibiotic use for exacerbations and colonization by specific microorganisms.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Enfermedad pulmonar]]></kwd>
<kwd lng="es"><![CDATA[Bronquiectasias]]></kwd>
<kwd lng="es"><![CDATA[Pediatría]]></kwd>
<kwd lng="es"><![CDATA[Enfermedad bronquial]]></kwd>
<kwd lng="es"><![CDATA[Inmunodeficiencias primarias]]></kwd>
<kwd lng="en"><![CDATA[Lung diseases]]></kwd>
<kwd lng="en"><![CDATA[Bronchiectasis]]></kwd>
<kwd lng="en"><![CDATA[Pediatrics]]></kwd>
<kwd lng="en"><![CDATA[Bronchial diseases]]></kwd>
<kwd lng="en"><![CDATA[Primary immunodeficiency diseases]]></kwd>
</kwd-group>
</article-meta>
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