<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0035-0052</journal-id>
<journal-title><![CDATA[Revista mexicana de pediatría]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. mex. pediatr.]]></abbrev-journal-title>
<issn>0035-0052</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Pediatría A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0035-00522019000200071</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Caso familiar de ictiosis laminar]]></article-title>
<article-title xml:lang="en"><![CDATA[A familial case of lamellar ichthyosis]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Morales-González]]></surname>
<given-names><![CDATA[Luis Ángel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Hernández-Pallares]]></surname>
<given-names><![CDATA[Remedios]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Salinas-Meritú]]></surname>
<given-names><![CDATA[Armando]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto de Salud del Estado de México Hospital General de Cuautitlán &#8220;Gral. José Vicente Villada&#8221; ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>México</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto de Salud del Estado de México Hospital General de Cuautitlán &#8220;Gral. José Vicente Villada&#8221; Servicio de Pediatría]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>04</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>04</month>
<year>2019</year>
</pub-date>
<volume>86</volume>
<numero>2</numero>
<fpage>71</fpage>
<lpage>74</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0035-00522019000200071&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0035-00522019000200071&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0035-00522019000200071&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen:  Introducción:  El término &#8220;bebé colodión&#8221; hace referencia a una presentación clínica al nacimiento de grupo diagnóstico llamado ictiosis congénita que tiene un tipo de herencia autosómica recesiva. Se presenta un caso de recurrencia de ictiosis congénita en una misma familia, lo cual es una condición poco informada.  Caso clínico:  Recién nacida (RN) de 37 semanas de gestación, producto de la segunda gesta. Padres consanguíneos en cuarto grado. La primera hija tuvo diagnóstico de ictiosis y falleció a los tres meses. La actual RN fue hospitalizada en la Unidad de Neonatología ya que al nacimiento se detectó una membrana colodión en la piel, sugestiva de una forma de ictiosis congénita; al no presentar láminas de queratina, se estableció el diagnóstico clínico de ictiosis tipo laminar. Se manejó con precauciones de contacto, analgesia y lubricación de la piel. Evolucionó con descamación y aumento de las fisuras, que posteriormente empezaron a disminuir y quedó una membrana residual; egresó sin problemas.  Conclusiones:  La ictiosis congénita es una condición rara, pero que con los datos clínicos y antecedentes se puede llegar al diagnóstico clínico. El asesoramiento genético es primordial para que las familias conozcan el riesgo de presentación en su descendencia.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract:  Introduction:  &#8220;Collodion baby&#8221; refers to a group called congenital ichthyosis, which has an autosomal recessive inheritance. We present a recurrent case of congenital ichthyosis in the same family, which rarely occurs.  Clinical case:  Female newborn of 37 weeks gestation, product of second pregnancy. Parents were consanguineous, in fourth grade. Their first daughter was diagnosed with ichthyosis and died three months later. The current newborn was hospitalized in the Neonatal Unit since at birth a skin collodion membrane was detected. With this condition it was suspected a form of congenital ichthyosis, probably of the laminar ichthyosis type. The patient was handled with precautions of contact, analgesia and lubrication of the skin. She evolved with peeling and increased fissures, which subsequently began to decrease and a residual membrane remained; she was discharged from the hospital without problems.  Conclusions:  Congenital ichthyosis is a rare condition, but since it has certain particular clinical data, the diagnosis can be reached. Genetic counseling is essential for families to know the risk of presentation in their offspring.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Bebé colodión]]></kwd>
<kwd lng="es"><![CDATA[ictiosis congénita]]></kwd>
<kwd lng="es"><![CDATA[ictiosis laminar]]></kwd>
<kwd lng="en"><![CDATA[Baby collodion]]></kwd>
<kwd lng="en"><![CDATA[congenital ichthyosis]]></kwd>
<kwd lng="en"><![CDATA[laminar ichthyosis]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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