<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0028-3746</journal-id>
<journal-title><![CDATA[Neumología y cirugía de tórax]]></journal-title>
<abbrev-journal-title><![CDATA[Neumol. cir. torax]]></abbrev-journal-title>
<issn>0028-3746</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Neumología y Cirugía de Tórax; Instituto Nacional de Enfermedades Respiratorias Ismael Cosío Villegas; Sociedad Cubana de Neumología; Sociedad Paraguaya de Neumología; Sociedad Boliviana de Neumología.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0028-37462017000100036</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Granulomatosis eosinofílica con poliangitis: reporte de un caso y revisión de la literatura]]></article-title>
<article-title xml:lang="en"><![CDATA[Eosinophilic granulomatosis with polyangiitis: a case report and literature review]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez-Armendáriz]]></surname>
<given-names><![CDATA[Rubén]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Hernández-Saldaña]]></surname>
<given-names><![CDATA[Raúl]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Hinojos-Gallardo]]></surname>
<given-names><![CDATA[Luis Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ramos-Martínez]]></surname>
<given-names><![CDATA[Ernesto]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Soto-Ramos]]></surname>
<given-names><![CDATA[Mario]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Infantil de Especialidades del Estado de Chihuahua  ]]></institution>
<addr-line><![CDATA[ Chihuahua]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2017</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2017</year>
</pub-date>
<volume>76</volume>
<numero>1</numero>
<fpage>36</fpage>
<lpage>43</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0028-37462017000100036&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0028-37462017000100036&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0028-37462017000100036&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: La granulomatosis eosinofílica con poliangitis (GEPA), anteriormente denominado síndrome de Churg-Strauss (SCS), es un trastorno poco frecuente, de etiología desconocida, caracterizada por una vasculitis necrosante que afecta a vasos de pequeño a mediano calibre. Los pacientes presentan como rasgo característico antecedentes de asma, rinitis alérgica y eosinofilia en sangre periférica. La GEPA, antes denominado SCS es poco común en la infancia. Aunque la GEPA es una vasculitis asociada a la presencia de anticuerpos anticitoplasma de neutrófilo (ANCA), en niños sólo se encuentran en menos del 40% de los casos. La detección temprana de la enfermedad es importante ya que un retraso en el diagnóstico puede llevar a la afectación orgánica de grado variable con resultados fatales. La GEPA de inicio en la infancia representa menos del 2% de los casos de vasculitis en edad pediátrica, y sólo 50 casos de GEPA en menores de 18 años se habían publicado hasta el año 2013. Presentamos el caso de un niño de 13 años de edad con asma de difícil control y deterioro de su estado general, que finalmente fue diagnosticado con GEPA-ANCA negativo.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Eosinophilic granulomatosis with poliangitis (EGPA), formerly called Churg-Strauss syndrome, is a rare disorder of unknown etiology characterized by necrotizing vasculitis that affects small vessels of medium caliber. Asthma, allergic rhinitis and peripheral blood eosinophilia are present in most patients. The EGPA in childhood is a rare clinical condition. Although EGPA is a vasculitis with neutrophil cytoplasmic antibodies related (ANCA) disorder in children, in less than 40% of all vasculitis cases are found. Early detection is important because a delay in diagnosis can lead to organ damage of varying degrees, some of them fatal. EGPA starting in childhood, represents less than 2% of cases of vasculitis in pediatric age and only 50 cases of SCS in children (&lt; 18 years old) had been published before 2013. We report the case of a 13 year old boy with difficult to control asthma and impaired general condition, which was finally diagnosed with EGPA, ANCA-negative.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Granulomatosis eosinofílica con poliangitis]]></kwd>
<kwd lng="es"><![CDATA[GEPA]]></kwd>
<kwd lng="es"><![CDATA[asma]]></kwd>
<kwd lng="es"><![CDATA[Churg-Strauss]]></kwd>
<kwd lng="es"><![CDATA[vasculitis]]></kwd>
<kwd lng="en"><![CDATA[Eosinophilic granulomatosis with polyangiitis]]></kwd>
<kwd lng="en"><![CDATA[EGPA]]></kwd>
<kwd lng="en"><![CDATA[asthma]]></kwd>
<kwd lng="en"><![CDATA[Churg Strauss]]></kwd>
<kwd lng="en"><![CDATA[vasculitis]]></kwd>
</kwd-group>
</article-meta>
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