<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2954-3835</journal-id>
<journal-title><![CDATA[Cardiovascular and metabolic science]]></journal-title>
<abbrev-journal-title><![CDATA[Cardiovasc. metab. sci]]></abbrev-journal-title>
<issn>2954-3835</issn>
<publisher>
<publisher-name><![CDATA[Asociación Nacional de Cardiólogos de México A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2954-38352020000100025</article-id>
<article-id pub-id-type="doi">10.35366/93259</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[An uncommon cause of atrioventricular block in young patients: Kearns-Sayre syndrome]]></article-title>
<article-title xml:lang="es"><![CDATA[Una causa infrecuente de bloqueo auriculoventricular en pacientes jóvenes: síndrome de Kearns-Sayre]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Posada-Vélez]]></surname>
<given-names><![CDATA[Verónica]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gómez]]></surname>
<given-names><![CDATA[Andrés]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Díaz]]></surname>
<given-names><![CDATA[Juan Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
<xref ref-type="aff" rid="A a"/>
<xref ref-type="aff" rid="A5 "/>
<xref ref-type="aff" rid="Af6"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Aristizábal]]></surname>
<given-names><![CDATA[Julián]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
<xref ref-type="aff" rid="A a"/>
<xref ref-type="aff" rid="A5 "/>
<xref ref-type="aff" rid="Af6"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Marín]]></surname>
<given-names><![CDATA[Jorge]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
<xref ref-type="aff" rid="A a"/>
<xref ref-type="aff" rid="A6"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Velásquez]]></surname>
<given-names><![CDATA[Jorge]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
<xref ref-type="aff" rid="A a"/>
<xref ref-type="aff" rid="A5 "/>
<xref ref-type="aff" rid="Af6"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Uribe]]></surname>
<given-names><![CDATA[William]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Duque]]></surname>
<given-names><![CDATA[Mauricio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad CES  ]]></institution>
<addr-line><![CDATA[Antioquia ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad CES  ]]></institution>
<addr-line><![CDATA[Antioquia ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital General de Medellín  ]]></institution>
<addr-line><![CDATA[Antioquia ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Clínica Las Vegas  ]]></institution>
<addr-line><![CDATA[Antioquia ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Clínica CES  ]]></institution>
<addr-line><![CDATA[Antioquia ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af6">
<institution><![CDATA[,Clínica Somer  ]]></institution>
<addr-line><![CDATA[Antioquia ]]></addr-line>
<country>Colombia</country>
</aff>
<aff id="Af7">
<institution><![CDATA[,Clínica Las Américas  ]]></institution>
<addr-line><![CDATA[Antioquia ]]></addr-line>
<country>Colombia</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2020</year>
</pub-date>
<volume>31</volume>
<numero>1</numero>
<fpage>25</fpage>
<lpage>29</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2954-38352020000100025&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2954-38352020000100025&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2954-38352020000100025&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Kearns-Sayre syndrome (KSS) is a rare cause of complete atrioventricular (AV) block in young patients. This disorder is caused by mitochondrial DNA (mtDNA) deletions, and unlike other mitochondrial diseases, involvement of the cardiac conduction system is frequent. KSS is characterized by the triad of progressive external ophthalmoplegia, pigmentary retinopathy and cardiac conduction system disturbances, with an onset before 20 years of age. We present a case of complete AV block due to this rare condition, which was diagnosed with a muscular biopsy taken at the time of pacemaker implant.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: El síndrome de Kearns-Sayre (SdKS) es una causa infrecuente de bloqueo auriculoventricular (AV) en personas jóvenes. Este desorden es causado por deleciones del ADN mitocondrial (ADNmt), y a diferencia de otras enfermedades mitocondriales, el compromiso del sistema de conducción eléctrica cardiaca es frecuente. El SdKS se caracteriza por la triada de oftalmoplejía progresiva externa, retinopatía pigmentaria y alteraciones en la conducción eléctrica cardiaca, con síntomas que, por lo general, inician antes de los 20 años de edad. Presentamos un caso de bloqueo AV completo debido a esta rara condición, la cual se diagnosticó mediante una biopsia muscular tomada al momento del implante de marcapasos.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Kearns-Sayre syndrome]]></kwd>
<kwd lng="en"><![CDATA[chronic progressive external ophthalmoplegia]]></kwd>
<kwd lng="en"><![CDATA[blepharoptosis]]></kwd>
<kwd lng="en"><![CDATA[heart block]]></kwd>
<kwd lng="en"><![CDATA[mitochondrial myopathy]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de Kearns-Sayre]]></kwd>
<kwd lng="es"><![CDATA[oftalmoplejía externa crónica progresiva]]></kwd>
<kwd lng="es"><![CDATA[blefaroptosis]]></kwd>
<kwd lng="es"><![CDATA[bloqueo cardiaco]]></kwd>
<kwd lng="es"><![CDATA[miopatía mitocondrial]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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