<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2448-9190</journal-id>
<journal-title><![CDATA[Revista alergia México]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. alerg. Méx.]]></abbrev-journal-title>
<issn>2448-9190</issn>
<publisher>
<publisher-name><![CDATA[Colegio Mexicano de Inmunología Clínica y Alergia A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2448-91902024000300205</article-id>
<article-id pub-id-type="doi">10.29262/ram.v71i3.1344</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Neumonía necrosante en un paciente con deficiencia selectiva de IgA]]></article-title>
<article-title xml:lang="en"><![CDATA[Necrotizing pneumonia in a patient with selective IgA deficiency]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Núnez-Núñez]]></surname>
<given-names><![CDATA[María Enriqueta]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Monraz-Monteón]]></surname>
<given-names><![CDATA[Denisse]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lona-Reyes]]></surname>
<given-names><![CDATA[Juan Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pozos-Ochoa]]></surname>
<given-names><![CDATA[Luis Iván]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Magallón-Picazo]]></surname>
<given-names><![CDATA[Diego]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bayardo-Gutierrez]]></surname>
<given-names><![CDATA[Beatriz]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Nuevo Hospital Civil de Guadalajara &#8220;Dr. Juan I. Menchaca&#8221;  ]]></institution>
<addr-line><![CDATA[Jalisco México]]></addr-line>
<country>México</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Guadalajara  ]]></institution>
<addr-line><![CDATA[Jalisco México]]></addr-line>
<country>México</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Nuevo Hospital Civil de Guadalajara &#8220;Dr. Juan I. Menchaca&#8221;  ]]></institution>
<addr-line><![CDATA[Jalisco México]]></addr-line>
<country>México</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Nuevo Hospital Civil de Guadalajara &#8220;Dr. Juan I. Menchaca&#8221;  ]]></institution>
<addr-line><![CDATA[Jalisco México]]></addr-line>
<country>México</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Universidad de Guadalajara Centro Universitario de Ciencias de la Salud ]]></institution>
<addr-line><![CDATA[Jalisco México]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>09</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>09</month>
<year>2024</year>
</pub-date>
<volume>71</volume>
<numero>3</numero>
<fpage>205</fpage>
<lpage>211</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2448-91902024000300205&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2448-91902024000300205&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2448-91902024000300205&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Antecedentes: Los errores innatos de la inmunidad se originan por mutaciones monogénicas que deben considerarse en el diagnóstico sugerente de pacientes con infecciones recurrentes o graves, alergias, autoinmunidad, enfermedades autoinflamatorias, insuficiencia de médula ósea y malignidad.  Reporte de caso: Paciente pediátrico de 4 años de edad, género masculino, quien a los dos años tuvo fiebre de 39°C, de difícil control. La radiografía simple de tórax reportó consolidación pulmonar izquierda. El cuadro infeccioso evolucionó a neumonía necrosante del lóbulo superior izquierdo, por lo que se decidió practicar lobectomía. Se sospechó el diagnóstico de algún error innato de la inmunidad. La determinación de inmunoglobulinas séricas informó IgA por debajo de los valores de referencia. A los 4 años continúo con IgA sérica disminuida (5.5 mg/dL).  Conclusión: El diagnóstico de deficiencia selectiva de IgA se establece a partir de los 4 años de vida; sin embargo, debido a la infección grave del paciente aquí reportado, tuvo que implementarse el abordaje diagnóstico en búsqueda de algún error innato de la inmunidad.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Background: Inborn errors of immunity originate from monogenic mutations that should be considered in the suggestive diagnosis of patients with recurrent or severe infections, allergies, autoimmunity, autoinflammatory diseases, bone marrow failure and malignancy.  Case report: Pediatric patient, male, 4 years old, treated in the medical service for fever of 39°C, difficult to control. The simple chest x-ray reported left pulmonary consolidation. The infectious condition evolved into necrotizing pneumonia of the left upper lobe, so it was decided to perform a lobectomy. The diagnosis of some inborn error of immunity was suspected. The determination of serum immunoglobulins reported IgA below the reference values. At 4 years he continued to have decreased serum IgA (5.5 mg/dL).  Conclusion: The diagnosis of selective IgA deficiency is established after 4 years of life; However, due to the patient&#8217;s severe infection, addressing some inborn error of immunity had to be implemented.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Infecciones recurrentes]]></kwd>
<kwd lng="es"><![CDATA[Error innato de la inmunidad]]></kwd>
<kwd lng="es"><![CDATA[Neumonía necrosante]]></kwd>
<kwd lng="es"><![CDATA[Lobectomía]]></kwd>
<kwd lng="es"><![CDATA[IgA]]></kwd>
<kwd lng="es"><![CDATA[Deficiencia selectiva de IgA]]></kwd>
<kwd lng="en"><![CDATA[Recurrent infections]]></kwd>
<kwd lng="en"><![CDATA[Inborn error of immunity]]></kwd>
<kwd lng="en"><![CDATA[Necrotizing pneumonia]]></kwd>
<kwd lng="en"><![CDATA[Lobectomy]]></kwd>
<kwd lng="en"><![CDATA[IgA]]></kwd>
<kwd lng="en"><![CDATA[Selective IgA deficiency]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bomken]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[van der Werff Ten Bosch]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Attarbaschi]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Current Understanding and Future Research Priorities in Malignancy Associated With Inborn Errors of Immunity and DNA Repair Disorders: The Perspective of an Interdisciplinary Working Group]]></article-title>
<source><![CDATA[Front Immunol]]></source>
<year>2018</year>
<volume>9</volume>
<page-range>1-10</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Tangye]]></surname>
<given-names><![CDATA[SG]]></given-names>
</name>
<name>
<surname><![CDATA[Al-Herz]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
<name>
<surname><![CDATA[Bousfiha]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Human Inborn Errors of Immunity: 2022 Update on the Classification from the International Union of Immunological Societies Expert Committee]]></article-title>
<source><![CDATA[J Clin Immunol]]></source>
<year>2022</year>
<volume>42</volume>
<numero>7</numero>
<issue>7</issue>
<page-range>1473-507</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bonilla]]></surname>
<given-names><![CDATA[FA]]></given-names>
</name>
<name>
<surname><![CDATA[Bernstein]]></surname>
<given-names><![CDATA[IL]]></given-names>
</name>
<name>
<surname><![CDATA[Khan]]></surname>
<given-names><![CDATA[DA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Practice parameter for the diagnosis and management of primary immunodeficiency]]></article-title>
<source><![CDATA[Ann Allergy Asthma Amp Immunol]]></source>
<year>2005</year>
<volume>94</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>S1-S63</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Domínguez]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
<name>
<surname><![CDATA[Giner]]></surname>
<given-names><![CDATA[MT]]></given-names>
</name>
<name>
<surname><![CDATA[Alsina]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Fenotipos clínicos asociados a la deficiencia selectiva de IgA: revisión de 330 casos y propuesta de un protocolo de seguimiento]]></article-title>
<source><![CDATA[An Pediatr]]></source>
<year>2012</year>
<volume>76</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>261-7</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Aytekin]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Tuygun]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Gokce]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Selective IgA Deficiency: Clinical and Laboratory Features of 118 Children in Turkey]]></article-title>
<source><![CDATA[J Clin Immunol]]></source>
<year>2012</year>
<volume>32</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>961-6</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Nurkic]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Numanovic]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Arnautalic]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Diagnostic Significance of Reduced IgA in Children]]></article-title>
<source><![CDATA[Med Arch]]></source>
<year>2014</year>
<volume>68</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>381-3</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Yazdani]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Latif]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Tabassomi]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Clinical phenotype classification for selective immunoglobulin A deficiency]]></article-title>
<source><![CDATA[Expert Rev Clin Immunol]]></source>
<year>2015</year>
<volume>11</volume>
<numero>11</numero>
<issue>11</issue>
<page-range>1245-54</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Mella]]></surname>
<given-names><![CDATA[MA]]></given-names>
</name>
<name>
<surname><![CDATA[Lavrinienko]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Akhi]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Compensatory IgM to the Rescue: Patients with Selective IgA Deficiency Have Increased Natural IgM Antibodies to MAA&#8211;LDL and No Changes in Oral Microbiota]]></article-title>
<source><![CDATA[Immuno Horizons]]></source>
<year>2021</year>
<volume>5</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>170-81</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Lim]]></surname>
<given-names><![CDATA[CK]]></given-names>
</name>
<name>
<surname><![CDATA[Dahle]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Elvin]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Reversal of Immunoglobulin A Deficiency in Children]]></article-title>
<source><![CDATA[J Clin Immunol]]></source>
<year>2014</year>
<volume>35</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>87-91</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Koenen]]></surname>
<given-names><![CDATA[MH]]></given-names>
</name>
<name>
<surname><![CDATA[Bosma]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Roorda]]></surname>
<given-names><![CDATA[UA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[A novel method to standardise serum IgA measurements shows an increased prevalence of IgA deficiency in young children with recurrent respiratory tract infections]]></article-title>
<source><![CDATA[Clin Amp Transl Immunol]]></source>
<year>2021</year>
<volume>10</volume>
<numero>11</numero>
<issue>11</issue>
<page-range>1-10</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
