<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2448-8771</journal-id>
<journal-title><![CDATA[Anestesia en México]]></journal-title>
<abbrev-journal-title><![CDATA[Anest. Méx.]]></abbrev-journal-title>
<issn>2448-8771</issn>
<publisher>
<publisher-name><![CDATA[Federación Mexicana de Colegios de Anestesiología A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2448-87712019000100056</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Morquio en cesárea bajo anestesia general: reporte de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Morquio syndrome in cesarean section under general anesthesia: a case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lucio-Medina]]></surname>
<given-names><![CDATA[IM]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rincón-Sánchez]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pizaña-Vázquez]]></surname>
<given-names><![CDATA[SA]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Peña-García]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López-García]]></surname>
<given-names><![CDATA[R.]]></given-names>
</name>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad Autónoma de Tamaulipas Hospital General de Matamoros &#8220;Dr. Alfredo Pumarejo Lafaurie.&#8221; ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital General de Matamoros &#8220;Dr. Alfredo Pumarejo Lafaurie.&#8221;  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital General de Matamoros &#8220;Dr. Alfredo Pumarejo Lafaurie.&#8221;  ]]></institution>
<addr-line><![CDATA[ Tamaulipas]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>04</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>04</month>
<year>2019</year>
</pub-date>
<volume>31</volume>
<numero>1</numero>
<fpage>56</fpage>
<lpage>61</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2448-87712019000100056&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2448-87712019000100056&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2448-87712019000100056&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen Las mucopolisacaridosis (MPS) son un grupo heterogéneo de trastornos metabólicos, generalmente heredados de manera autosómica recesiva, caracterizados por la falta de enzimas útiles para la descomposición de Glicosaminoglicanos (GAGs) (1). Las anormalidades resultantes de la condrogénesis y la posterior osteogénesis (disostosis múltiple) son en gran parte responsables del fenotipo típico con elementos visibles tales como estatura corta, cifoescoliosis, pecho prominente con forma de campana/barril, protuberancia frontal, genu valgum (rodillas inconscientes) y laxitud en las articulaciones (6). Presentamos el caso de una paciente para resolución del embarazo portadora de una mucopolisacaridosis tipo IV. La falta de evidencia bibliográfica sobre este tipo de pacientes obstétricas, es el motivo por el que compartimos nuestra experiencia en el manejo de esta enfermedad.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract The mucopolysaccharidoses (MPS) are an heterogeneous group of metabolic disorders, usually inherited in an autosomal recessive manner, characterised by the lack of enzymes useful for decomposition of glycosaminoglycans (GAGs) (1). Resulting from abnormalities of the chondrogenesis and osteogenesis rear (Dysostosis multiplex) are largely responsible for the typical phenotype with visible elements such as short stature, kyphoscoliosis, chest prominent campaign/barrel-shaped, frontal bossing, genu valgum (unconscious knees) and laxity in the joints (6). We present the case of a patient for resolution of pregnancy carrying a Mucopolysaccharidosis type IV. The lack of evidence literature about this type of obstetric patients, is the reason why we share our experience in the management of this disease.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Morquio]]></kwd>
<kwd lng="es"><![CDATA[mucopolisacaridosis y embarazo]]></kwd>
<kwd lng="es"><![CDATA[anestesia general]]></kwd>
<kwd lng="es"><![CDATA[vía aérea difícil]]></kwd>
<kwd lng="en"><![CDATA[Morquio syndrome]]></kwd>
<kwd lng="en"><![CDATA[Mucopolysaccharidosis and pregnancy]]></kwd>
<kwd lng="en"><![CDATA[general anesthesia]]></kwd>
<kwd lng="en"><![CDATA[difficult airway]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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