<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2448-8771</journal-id>
<journal-title><![CDATA[Anestesia en México]]></journal-title>
<abbrev-journal-title><![CDATA[Anest. Méx.]]></abbrev-journal-title>
<issn>2448-8771</issn>
<publisher>
<publisher-name><![CDATA[Federación Mexicana de Colegios de Anestesiología A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2448-87712017000300042</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Insensibilidad Congénita al Dolor: Sufriendo sin dolor]]></article-title>
<article-title xml:lang="en"><![CDATA[Syndrome of congenital insensitivity to pain: suffering without pain]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Romero-Guillén]]></surname>
<given-names><![CDATA[LP]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pavia-Vega]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Saquelares-Rodriguez]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Hurtado-Reyes]]></surname>
<given-names><![CDATA[IC]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rojas-Zarco]]></surname>
<given-names><![CDATA[EM]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sánchez-Tapia]]></surname>
<given-names><![CDATA[MA]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Aguirre-María]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Médico ABC  ]]></institution>
<addr-line><![CDATA[ Ciudad de México]]></addr-line>
<country>México</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Centro Médico ABC  ]]></institution>
<addr-line><![CDATA[Ciudad de México ]]></addr-line>
<country>México</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Centro Médico ABC  ]]></institution>
<addr-line><![CDATA[Ciudad de México ]]></addr-line>
<country>México</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Centro Médico ABC  ]]></institution>
<addr-line><![CDATA[ciudad de México ]]></addr-line>
<country>México</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Centro Médico ABC  ]]></institution>
<addr-line><![CDATA[Ciudad de México ]]></addr-line>
<country>México</country>
</aff>
<aff id="Af6">
<institution><![CDATA[,Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán  ]]></institution>
<addr-line><![CDATA[ciudad de México ]]></addr-line>
<country>México</country>
</aff>
<aff id="Af7">
<institution><![CDATA[,Hospital Shriners para Niños  ]]></institution>
<addr-line><![CDATA[Ciudad de México ]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2017</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2017</year>
</pub-date>
<volume>29</volume>
<numero>3</numero>
<fpage>42</fpage>
<lpage>47</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2448-87712017000300042&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2448-87712017000300042&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2448-87712017000300042&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen La insensibilidad congénita al dolor es una enfermedad extremadamente rara. Afecta a niños a edades muy temprana de la vida. Existen cinco tipos hereditarios diferentes de neuropatías con trastornos en la sensibilidad de carácter autosómico. Todas las variedades se caracterizan por insensibilidad al dolor, mutilaciones principalmente de las falanges distales de los dedos, los dientes frecuentemente producen lesiones a los tejidos blandos de la boca y de la lengua. Algunas de estas variedades de enfermedad se acompañan de trastornos mentales e hidrosis. No existe tratamiento alguno y frecuentemente ocurre la muerte a edades tempranas de la vida. Tampoco existe un manejo anestésico específico.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Congenital insensitivity to pain is an extremely rare dis - ease. It affects children at very early ages of life. There are five different hereditary neuropathies with disorders in the sensitivity of autosomal characater. All varieties are characterized by insensitivity to pain, mutilation mainly of the distal phalanges of the fingers, teeth frequently pro-duce injury to the soft tissues of the mouth and tongue. Some of these varieties of disease have mental disorders and hidrosis. There is no treatment and death at an early age of life often occurs. There is not a specific anaesthetic management.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Insensibilidad congénita al dolor]]></kwd>
<kwd lng="es"><![CDATA[sufrimiento sin dolor]]></kwd>
<kwd lng="es"><![CDATA[analgesia general congénita pura]]></kwd>
<kwd lng="en"><![CDATA[Congenital insensitivity to pain]]></kwd>
<kwd lng="en"><![CDATA[suffering no pain]]></kwd>
<kwd lng="en"><![CDATA[congenital pure general analgesia]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Dearborn]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[A case of congenital general pure analgesia]]></article-title>
<source><![CDATA[J Nerv Ment Dis]]></source>
<year>1932</year>
<volume>75</volume>
<page-range>612</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Pimienta]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Mercado]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Almanza]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<source><![CDATA[Insensibilidad congénita al dolor. Elementos]]></source>
<year>2016</year>
<volume>101</volume>
<page-range>13-120</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Fatela]]></surname>
<given-names><![CDATA[LV]]></given-names>
</name>
<name>
<surname><![CDATA[Acedo]]></surname>
<given-names><![CDATA[MS]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Trastornos de la reactividad al dolor]]></article-title>
<source><![CDATA[Rev. Soc. Esp. Dolor]]></source>
<year>2004</year>
<volume>11</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>31-7</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Zlotnik]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Natanel]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Kutz]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Boyko]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Brotfain]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Gruenbaum]]></surname>
<given-names><![CDATA[BF]]></given-names>
</name>
<name>
<surname><![CDATA[Gruenbaum]]></surname>
<given-names><![CDATA[SE]]></given-names>
</name>
<name>
<surname><![CDATA[Bodner]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Anesthetic management of patients with congenital insensitivity to pain with anhidrosis A retrospective analysis of 358 procedures performed under general anesthesia]]></article-title>
<source><![CDATA[Anesth Analg]]></source>
<year>2015</year>
<volume>121</volume>
<page-range>1316-20</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Mobini]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Javadzadeh]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Forghanizadeh]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Neuropathic osteroarthropathy in a patient with congenital insensitivity to pain]]></article-title>
<source><![CDATA[Arch Iran Med]]></source>
<year>2009</year>
<volume>12</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>599-602</page-range></nlm-citation>
</ref>
<ref id="B6">
<nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Pimienta]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<source><![CDATA[Insensibilidad congénita al dolor: Sufriendo sin dolor]]></source>
<year>2016</year>
<page-range>13-20</page-range><publisher-name><![CDATA[Benemérita Universidad Autónoma de Puebla]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Nagasako]]></surname>
<given-names><![CDATA[EM]]></given-names>
</name>
<name>
<surname><![CDATA[Oaklander]]></surname>
<given-names><![CDATA[AL]]></given-names>
</name>
<name>
<surname><![CDATA[Dworkin]]></surname>
<given-names><![CDATA[RH]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Congenital insensitivity to pain an update]]></article-title>
<source><![CDATA[Pain]]></source>
<year>2003</year>
<volume>101</volume>
<page-range>213-9</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bolgul]]></surname>
<given-names><![CDATA[BS]]></given-names>
</name>
<name>
<surname><![CDATA[Hamamci]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Agackiran]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Celenk]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Ayna]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Congenital insensitivity to pain A case report with dental implications]]></article-title>
<source><![CDATA[HK J Paediatr]]></source>
<year>2010</year>
<volume>15</volume>
<page-range>234-7</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Nagasako]]></surname>
<given-names><![CDATA[EM]]></given-names>
</name>
<name>
<surname><![CDATA[Oaklander]]></surname>
<given-names><![CDATA[AL]]></given-names>
</name>
<name>
<surname><![CDATA[Dworkin]]></surname>
<given-names><![CDATA[RH]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Congenital insensitivity to pain an update]]></article-title>
<source><![CDATA[Pain]]></source>
<year>2003</year>
<volume>101</volume>
<page-range>213-9</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Degrandi-Oliveira]]></surname>
<given-names><![CDATA[CR]]></given-names>
</name>
<name>
<surname><![CDATA[Paris]]></surname>
<given-names><![CDATA[VC]]></given-names>
</name>
<name>
<surname><![CDATA[Augusto-Pereira]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Anesthesia in a patient with congenital insensitivity to pain and anhidrosis]]></article-title>
<collab>Thyrso de Lara FS</collab>
<source><![CDATA[Rev. Bras. Anestesiol]]></source>
<year>2009</year>
<volume>59</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>602-9</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Brandes]]></surname>
<given-names><![CDATA[IF]]></given-names>
</name>
<name>
<surname><![CDATA[Stuth]]></surname>
<given-names><![CDATA[EAE]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Use of BIS monitor in a child with congenital insensitivity to pain with anhidrosis]]></article-title>
<source><![CDATA[Paediatric Anaesthesia]]></source>
<year>2006</year>
<volume>16</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>466-70</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Okuda]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Arai]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Miwa]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Hiroki]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Anaesthetic to pain with anhidrosis]]></article-title>
<source><![CDATA[Paediatr Anaesth]]></source>
<year>2000</year>
<volume>10</volume>
<page-range>545-8</page-range></nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Rodríguez Pérez]]></surname>
<given-names><![CDATA[MV]]></given-names>
</name>
<name>
<surname><![CDATA[Fernández Daza]]></surname>
<given-names><![CDATA[PL]]></given-names>
</name>
<name>
<surname><![CDATA[Cruz-Villaseñor]]></surname>
<given-names><![CDATA[JA]]></given-names>
</name>
<name>
<surname><![CDATA[Cendón Ortega]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Anaya Perdomo]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Sánchez Mercado]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Anestesia epidural a un niño con fractura de fémure insensibilidad congénita al dolor/epidural anesthesia for femoral fracture repair in a boy with congenital insensitivity to pain]]></article-title>
<source><![CDATA[Rev Esp Anestesiol Reanim]]></source>
<year>2002</year>
<volume>49</volume>
<numero>10</numero>
<issue>10</issue>
<page-range>555-7</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Lee]]></surname>
<given-names><![CDATA[ST]]></given-names>
</name>
<name>
<surname><![CDATA[Lee]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Lee]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Kim]]></surname>
<given-names><![CDATA[JW]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Clinical and genetic analysis of Korean patients with congenital insensitivity to pain with anhidrosis]]></article-title>
<source><![CDATA[Muscle Nerve]]></source>
<year>2009</year>
<volume>40</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>855-9</page-range></nlm-citation>
</ref>
<ref id="B15">
<label>15</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Álvarez]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Aristizábal]]></surname>
<given-names><![CDATA[LSP]]></given-names>
</name>
<name>
<surname><![CDATA[Chaparro]]></surname>
<given-names><![CDATA[LE]]></given-names>
</name>
<name>
<surname><![CDATA[Ramírez]]></surname>
<given-names><![CDATA[LJ]]></given-names>
</name>
<name>
<surname><![CDATA[Sarassa]]></surname>
<given-names><![CDATA[VCA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Indiferencia congénita al dolor]]></article-title>
<source><![CDATA[Rev. Col. Anest]]></source>
<year>2010</year>
<volume>38</volume>
<page-range>528-35</page-range></nlm-citation>
</ref>
<ref id="B16">
<label>16</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Nabiyev]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Kara]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Aksoy]]></surname>
<given-names><![CDATA[MC]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Multidisciplinary assessment of congenital insensitivity to pain syndrome]]></article-title>
<source><![CDATA[Child&amp;apos;s Nervous System]]></source>
<year>2016</year>
<volume>32</volume>
<page-range>1741-4</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
