<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2444-054X</journal-id>
<journal-title><![CDATA[Cirugía y cirujanos]]></journal-title>
<abbrev-journal-title><![CDATA[Cir. cir.]]></abbrev-journal-title>
<issn>2444-054X</issn>
<publisher>
<publisher-name><![CDATA[Academia Mexicana de Cirugía A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2444-054X2023000400576</article-id>
<article-id pub-id-type="doi">10.24875/ciru.21000786</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Manejo anestésico en una niña con síndrome de Loeys-Dietz sometida a recambio completo de arco aórtico]]></article-title>
<article-title xml:lang="en"><![CDATA[Anesthetic management of a child with Loeys-Dietz syndrome undergoing complete aortic arch replacement]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Olabarrieta-Zarain]]></surname>
<given-names><![CDATA[Unai]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Martínez-Santos]]></surname>
<given-names><![CDATA[Leire]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Alberdi-Enríquez]]></surname>
<given-names><![CDATA[Alex]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Guereca-Gala]]></surname>
<given-names><![CDATA[Ane]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bravo-Sevilla]]></surname>
<given-names><![CDATA[Blanca]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Martínez-Ruiz]]></surname>
<given-names><![CDATA[Alberto]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Universitario de Cruces Servicio de Anestesiología, Reanimación y Terapia de Dolor ]]></institution>
<addr-line><![CDATA[Vizcaya ]]></addr-line>
<country>España</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad País Vasco Facultad de Medicina ]]></institution>
<addr-line><![CDATA[Vizcaya ]]></addr-line>
<country>España</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>08</month>
<year>2023</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>08</month>
<year>2023</year>
</pub-date>
<volume>91</volume>
<numero>4</numero>
<fpage>576</fpage>
<lpage>580</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2444-054X2023000400576&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2444-054X2023000400576&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2444-054X2023000400576&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen El síndrome de Loeys-Dietz (SDL) es una enfermedad del tejido conectivo debida a mutaciones del factor de crecimiento transformador beta que provocan formación de aneurismas, malformaciones vasculares y esqueléticas. Tiene mal pronóstico y el fallecimiento sobreviene de media a los 27 años sin tratamiento quirúrgico. A pesar de diagnosticarse en la infancia, es infrecuente la cirugía en niños. Presentamos el caso de una niña de 12 años con SDL y aneurisma múltiple en aorta torácica, programada para recambio completo de arco aórtico, proponiendo estrategias para el manejo anestésico, dada la complejidad y las implicaciones de esta cirugía en la población pediátrica.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Loeys-Dietz syndrome (LDS) is a connective tissue disease related to &#946;-transforming growth factor mutations, which causes aneurysms formation, vascular tortuosity and skeletal manifestations. The prognosis is very poor, and mortality occurs at the age of 27 in patients without surgical treatment. Despite being diagnosed in childhood, is not usual surgical aortic replacement in children. We report a case of 12 years old child with LDS and multiple aneurysms in thoracic aorta, undergoing complete aortic arch replacement and our proposal for the anesthetic management, due to surgical complexity and implications in pediatric population.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Loeys-Dietz]]></kwd>
<kwd lng="es"><![CDATA[Cirugía de arco aórtico]]></kwd>
<kwd lng="es"><![CDATA[Síndromes marfanoides]]></kwd>
<kwd lng="es"><![CDATA[Subluxación cervical]]></kwd>
<kwd lng="es"><![CDATA[Neuroprotección cerebral]]></kwd>
<kwd lng="en"><![CDATA[Loeys Dietz Syndrome]]></kwd>
<kwd lng="en"><![CDATA[Aortic arch surgery]]></kwd>
<kwd lng="en"><![CDATA[Marfan like syndrome]]></kwd>
<kwd lng="en"><![CDATA[Cervical subluxation]]></kwd>
<kwd lng="en"><![CDATA[Brain injury neuroprotection]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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