<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1870-7203</journal-id>
<journal-title><![CDATA[Acta médica Grupo Ángeles]]></journal-title>
<abbrev-journal-title><![CDATA[Acta méd. Grupo Ángeles]]></abbrev-journal-title>
<issn>1870-7203</issn>
<publisher>
<publisher-name><![CDATA[Grupo Ángeles, Servicios de Salud]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1870-72032021000400535</article-id>
<article-id pub-id-type="doi">10.35366/102541</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Consideraciones perioperatorias en un lactante con síndrome de Noonan]]></article-title>
<article-title xml:lang="en"><![CDATA[Perioperative considerations in an infant with Noonan syndrome]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[González Lumbreras]]></surname>
<given-names><![CDATA[Aniza Surinam]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Díaz Fosado]]></surname>
<given-names><![CDATA[Luis Alfonso]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Asz Sigall]]></surname>
<given-names><![CDATA[José]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fernández Soto]]></surname>
<given-names><![CDATA[José Rodrigo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Medina de la Rosa]]></surname>
<given-names><![CDATA[Edoardo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ramírez Morales]]></surname>
<given-names><![CDATA[Karina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Angeles Lomas  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>México</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Angeles Lomas  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>México</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Angeles Lomas  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>México</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Instituto Mexicano del Seguro Social Centro Médico ABC Unidad Médica de Atención Ambulatoria No. 42]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2021</year>
</pub-date>
<volume>19</volume>
<numero>4</numero>
<fpage>535</fpage>
<lpage>538</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1870-72032021000400535&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1870-72032021000400535&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1870-72032021000400535&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: El síndrome de Noonan es una enfermedad congénita que pertenece a la familia de rasopatías, síndromes causados por mutaciones en genes que codifican la vía de señalización RAS-MAPK. Es un síndrome multisistémico relacionado con cardiopatías, coagulopatías, criptorquidia, retraso mental, anomalías cerebrovasculares, renales y linfáticas. Se observan facies características, en muchas ocasiones asociadas a vía aérea difícil, lo que plantea un reto para el anestesiólogo. A continuación, se describe el caso de un lactante con diagnóstico de síndrome de Noonan con criptorquidia bilateral a quien se le realizó una orquidopexia laparoscópica bajo anestesia general. Los datos clínicos que consideramos para la elección de la técnica anestésica fueron: cardiopatía congénita, vía aérea difícil, acceso vascular poco visible secundario a linfedema periférico.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Noonan syndrome is a congenital disease belonging to the rasopathy family, caused by mutations in the RAS-MAPK pathway. It is a multisystemic syndrome commonly associated with structural heart disease, coagulopathies, cryptorchidism, cerebrovascular anomalies, and cognitive impairment, as well as renal and lymphoid alterations. Patients usually show typical facial anomalies and a difficult airway, which might portend a challenge for the anesthesiologist. We present the case of an infant with Noonan syndrome and bilateral cryptorchidism, treated with laparoscopic orchidopexy under general anesthesia. Anesthesiology approach was selected based on the history of congenital heart disease, difficult airway, and difficult vascular access secondary to peripheral lymphedema.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Noonan]]></kwd>
<kwd lng="es"><![CDATA[anestesia general]]></kwd>
<kwd lng="es"><![CDATA[vía aérea difícil]]></kwd>
<kwd lng="es"><![CDATA[cardiopatía congénita]]></kwd>
<kwd lng="en"><![CDATA[Noonan syndrome]]></kwd>
<kwd lng="en"><![CDATA[general anesthesia]]></kwd>
<kwd lng="en"><![CDATA[difficult airway]]></kwd>
<kwd lng="en"><![CDATA[congenital heart disease]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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