<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1870-199X</journal-id>
<journal-title><![CDATA[Revista odontológica mexicana]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Odont. Mex]]></abbrev-journal-title>
<issn>1870-199X</issn>
<publisher>
<publisher-name><![CDATA[Universidad Nacional Autónoma de México, Facultad de Odontología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1870-199X2020000400283</article-id>
<article-id pub-id-type="doi">10.22201/fo.1870199xp.2020.24.4.81550</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Manifestaciones bucales en el síndrome de Peutz-Jeghers: presentación de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Oral manifestations in Peutz-Jeghers syndrome: presentation of a case]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Tiol-Carrillo]]></surname>
<given-names><![CDATA[Agustín]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad Autónoma Metropolitana  ]]></institution>
<addr-line><![CDATA[Xochimilco Ciudad de México]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<volume>24</volume>
<numero>4</numero>
<fpage>283</fpage>
<lpage>289</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1870-199X2020000400283&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1870-199X2020000400283&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1870-199X2020000400283&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen Introducción: El síndrome de Peutz-Jeghers (SPJ) es una alteración genética con manifestaciones bucales características, se manifiesta a través de manchas marrones o negruzcas que aparecen de forma diseminada en piel y mucosa bucal durante los primeros años de vida, además de un alto riesgo de desarrollar pólipos gastrointestinales capaces de producir obstrucción intestinal, daño intestinal isquémico del colon que pueden conducir al paciente a la muerte. Objetivo: Describir las manifestaciones clínicas del SPJ mediante una revisión de la literatura y la presentación de un caso clínico. Resultados: Se expone la etiología así como las manifestaciones sistémicas y bucales más características del SPJ y se correlacionan con el caso clínico presentado de un paciente de 11 años de edad. Conclusiones: Existen numerosas enfermedades genéticas con específicas manifestaciones craneofaciales y bucales que exigen al estomatólogo contar con los conocimientos mínimos necesarios en la identificación de manifestaciones propias de cada síndrome, tal es el caso del SPJ que presenta afecciones peribucales e intrabucales conocidas como hipermelanosis mucocutáneas, hallazgos patognomónicos de esta condición.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Introduction: Peutz-Jeghers Syndrome (PJS) is a genetic alteration with oral manifestations through brown or blackish spots that spread over the skin and oral mucosa during the first years of life; it is also a high risk of developing gastrointestinal polyps that can lead to intestinal obstruction and ischemic intestinal damage to the colon, which can lead to death. Objective: To describe the clinical manifestations of PJS through a review of the literature and the presentation of a clinical case. Results: The etiology as well as the most characteristic systemic and oral manifestations of PJS, are exposed and correlate with the clinical case of an 11-year-old male patient. Conclusions: Numerous genetic diseases with specific craniofacial and oral manifestations require the stomatologist to have the minimum knowledge necessary to identify them; such is the case of PJS, which presents peri and intraoral affections known as mucocutaneous melanosis, pathognomonic findings of this condition.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Peutz-Jeghers]]></kwd>
<kwd lng="es"><![CDATA[hipermelanosis mucocutánea]]></kwd>
<kwd lng="es"><![CDATA[máculas bucales de origen genético]]></kwd>
<kwd lng="es"><![CDATA[genética en odontología]]></kwd>
<kwd lng="en"><![CDATA[Peutz-Jeghers syndrome]]></kwd>
<kwd lng="en"><![CDATA[mucocutaneous melanosis]]></kwd>
<kwd lng="en"><![CDATA[genetic buccal macules]]></kwd>
<kwd lng="en"><![CDATA[genetics in dentistry]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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