<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1870-199X</journal-id>
<journal-title><![CDATA[Revista odontológica mexicana]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Odont. Mex]]></abbrev-journal-title>
<issn>1870-199X</issn>
<publisher>
<publisher-name><![CDATA[Universidad Nacional Autónoma de México, Facultad de Odontología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1870-199X2010000100063</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Rehabilitación bucal bajo anestesia general en el síndrome de Alagille. Reporte de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Oral rehabilitaton with general anesthesia in Alagille syndrome. Case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Espinosa Victoria]]></surname>
<given-names><![CDATA[Lilia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Teja Ángeles]]></surname>
<given-names><![CDATA[Eduardo de la]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Durán Gutiérrez]]></surname>
<given-names><![CDATA[Luis Américo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gaitán Cepeda]]></surname>
<given-names><![CDATA[Luis Alberto]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,INP  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,INP  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,INP  ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,UNAM DEPeI Departamento de Patología Experimental]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2010</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2010</year>
</pub-date>
<volume>14</volume>
<numero>1</numero>
<fpage>63</fpage>
<lpage>68</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1870-199X2010000100063&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1870-199X2010000100063&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1870-199X2010000100063&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: El síndrome de Alagille es un desorden multisistémico, autosómico dominante con manifestaciones clínicas variables, principalmente afecta el hígado, conductos biliares, riñones, corazón, ojos, y tejido óseo. Presenta una incidencia de 1 en 100,000 nacidos vivos. Es importante eliminar focos infecciosos en la cavidad bucal de estos pacientes por la susceptibilidad a presentar procesos infecciosos e incluso sepsis por inmunodepresión inherente al síndrome. Este artículo describe el caso de un paciente con diagnóstico de síndrome de Alagille y el plan de tratamiento multidisciplinario para llevar a cabo la rehabilitación bucal bajo anestesia general, cabe destacar que el paciente presentaba pigmentación completa de la dentición primaria de color verde a causa de la bilirrubina; el tratamiento fue radical para la eliminación de focos infecciosos, anteponiéndose la salud del paciente a la estética.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: The Alagille syndrome is a multi-systemic disorder, it is inherited as an autosomal dominant trait, with variable clinical manifestations, mainly affects the liver, and biliary conduits, kidneys, heart, eyes, and an unusual butterfly shape of the bones of the spinal column. The estimated prevalence of Alagille syndrome is 1 in 100,000 live births. It is important to eliminate caries in the buccal cavity of these patients by the susceptibility to present infectious processes and sepsis by inherent immunological depression of the syndrome. This article describes the case of a patient with diagnosis of Alagille Syndrome and the multidisciplinary treatment to carry out the buccal rehabilitation under general anesthesia, it is important to inform that the patient presented complete green pigmentation of the primary dentition, because of the bilirubin, the treatment was radical for the elimination of infectious centers, putting in front the health of patient to the aesthetic one.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Alagille]]></kwd>
<kwd lng="es"><![CDATA[rehabilitación bucal]]></kwd>
<kwd lng="es"><![CDATA[inmunosupresión]]></kwd>
<kwd lng="es"><![CDATA[dientes verdes]]></kwd>
<kwd lng="en"><![CDATA[Alagille syndrome]]></kwd>
<kwd lng="en"><![CDATA[buccal rehabilitation]]></kwd>
<kwd lng="en"><![CDATA[immunosuppression]]></kwd>
<kwd lng="en"><![CDATA[green teeth]]></kwd>
</kwd-group>
</article-meta>
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