<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1665-5044</journal-id>
<journal-title><![CDATA[Revista mexicana de neurociencia]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. mex. neurocienc.]]></abbrev-journal-title>
<issn>1665-5044</issn>
<publisher>
<publisher-name><![CDATA[Academia Mexicana de Neurología A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1665-50442022000200057</article-id>
<article-id pub-id-type="doi">10.24875/rmn.21000050</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Frequency, clinical, and paraclinical characteristics of patients with Bickerstaff brainstem encephalitis in a tertiary-referral neurological center]]></article-title>
<article-title xml:lang="es"><![CDATA[Frecuencia, características clínicas y paraclínicas de pacientes con encefalitis de Bickerstaff en un centro neurológico de referencia de tercer nivel]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Aguilar-Parra]]></surname>
<given-names><![CDATA[Lilia G.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez-Jiménez]]></surname>
<given-names><![CDATA[Karla V.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Saráchaga]]></surname>
<given-names><![CDATA[Adib J. De]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bazán-Rodríguez]]></surname>
<given-names><![CDATA[Anna L.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Martínez-Jiménez]]></surname>
<given-names><![CDATA[Eunice]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Galnares-Olalde]]></surname>
<given-names><![CDATA[Javier A.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Kerik-Rotenberg]]></surname>
<given-names><![CDATA[Nora E.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Calleja-Castillo]]></surname>
<given-names><![CDATA[Juan M.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[León-Manriquez]]></surname>
<given-names><![CDATA[Elizabeth]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vargas-Cañas]]></surname>
<given-names><![CDATA[Edwin S.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López-Hernández]]></surname>
<given-names><![CDATA[Juan C.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Nacional de Neurología y Neurocirugía Department of Neurology ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto Nacional de Neurología y Neurocirugía Neuromuscular Diseases Clinic ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Instituto Nacional de Neurología y Neurocirugía Department of Nuclear Medicine ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Instituto Nacional de Neurología y Neurocirugía Department of Emergency ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>04</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>04</month>
<year>2022</year>
</pub-date>
<volume>23</volume>
<numero>2</numero>
<fpage>57</fpage>
<lpage>62</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1665-50442022000200057&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1665-50442022000200057&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1665-50442022000200057&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Background: Bickerstaff brainstem encephalitis (BBE) presents with consciousness impairment, ataxia, ophthalmoplegia, and areflexia.  Objective: We aim to describe the clinical, paraclinical, and imaging features of patients with BBE from a tertiary-referral neurological center.  Methods: A case series was conducted from an ambispective cohort of patients with Guillain-Barré syndrome (GBS) from 2016 to 2021. Subjects &#8805; 18 years and who met Odaka et al. BBE criteria were eligible. Data collected included: age, gender, prior infection, Guillain-Barré disability score (GDS score), time from symptom onset to diagnosis, altered mental state, time from symptom onset to altered mental state, cranial nerve involvement, deep tendon reflexes, ataxia, invasive mechanical ventilation (IMV) requirement, treatment, inpatient delirium, length of stay (days), and protein levels in CSF analysis. Nerve conduction studies (NCS) were performed, as well as neuroimaging (brain magnetic resonance imaging [MRI] and F18-fluorodeoxyglucose PET-CT). Antiganglioside antibodies panel including anti-GQ1b was solicited.  Results: Four patients (1.7%) met the inclusion criteria. Two patients manifested stupor and two showed somnolence throughout the course of the disease. Three patients required IMV due to bulbar dysfunction. None of the NCS met the criteria for any GBS electrophysiological variant. One patient was positive for IgM GM2 antibodies. One patient underwent 18F-FDG PET-CT, showing generalized cortical hypometabolism.  Conclusion: The frequency of BBE in our population is very low (1.7%). IgM GM2 is another anti-ganglioside antibody related to BBE. Imaging studies such as MRI frequently do not present abnormalities and [F18-FDG-PET scan might be a useful study to describe a metabolism pattern to aid the diagnosis of BBE.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Antecedentes: La encefalitis de Bickerstaff (EB) se presenta con alteración del nivel de consciencia, ataxia, oftalmoplejia y arreflexia.  Objetivos: Nuestro objetivo es describir las características clínicas, paraclínicas e imagenológicas de pacientes con EB en un centro neurológico de referencia de tercer nivel.  Métodos: Se realizó una serie de casos de una cohorte ambispectiva de pacientes con Guillain Barré (GB) desde 2016 hasta 2021. Se incluyeron pacientes mayores de 18 años que cumplieron los criterios de Odaka et al. para EB. La información obtenida incluyó: edad, género, infección previa, escala de discapacidad de GB y niveles de proteinas en el LCR, entre otros. Se realizaron estudios de conducción nerviosa, estudios de neuroimagen (RM de encéfalo y 18F-FDG-PET-CT) y panel de anticuerpos antigangliósidos.  Resultados: Cuatro pacientes (1.7%) cumplieron los criterios de inclusión. Dos pacientes presentaron estupor y dos somnolencia a lo largo de la enfermedad. Tres pacientes requirieron ventilación mecánica. Ninguno de los estudios de conducción nerviosa cumplió los criterios para alguna variante electrofisiológica de GB. Un paciente tuvo anticuerpos anti GM2 IgM positivos. A un paciente se le realizó 18F-FDG-PET-CT, mostrando hipometabolismo cortical generalizado.  Conclusiones: La frecuencia de EB en nuestra población es muy baja. El anticuerpo GM2 IgM es otro antigangliósido relacionado a EB. La resonancia magnética no presentó anormalidades y el 18F-FDG-PET-CT podría ser un estudio útil para describir un patrón de metabolismo que ayude en el diagnóstico de EB.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Guillain Barré]]></kwd>
<kwd lng="en"><![CDATA[Bickerstaff]]></kwd>
<kwd lng="en"><![CDATA[Miller fisher]]></kwd>
<kwd lng="en"><![CDATA[Brainstem encephalitis]]></kwd>
<kwd lng="en"><![CDATA[GQ1b]]></kwd>
<kwd lng="en"><![CDATA[Antiganglioside antibodies]]></kwd>
<kwd lng="es"><![CDATA[Guillain Barré]]></kwd>
<kwd lng="es"><![CDATA[Bickerstaff]]></kwd>
<kwd lng="es"><![CDATA[Miller Fisher]]></kwd>
<kwd lng="es"><![CDATA[Encefalitis de tallo]]></kwd>
<kwd lng="es"><![CDATA[GQ1b]]></kwd>
<kwd lng="es"><![CDATA[Aanticuerpos antigangliosidos]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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