<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1665-5044</journal-id>
<journal-title><![CDATA[Revista mexicana de neurociencia]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. mex. neurocienc.]]></abbrev-journal-title>
<issn>1665-5044</issn>
<publisher>
<publisher-name><![CDATA[Academia Mexicana de Neurología A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1665-50442020000600228</article-id>
<article-id pub-id-type="doi">10.24875/rmn.20000099</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Clinical characteristics of Creutzfeldt-Jakob disease in Mexico: A retrospective analysis]]></article-title>
<article-title xml:lang="es"><![CDATA[Características clínicas de la enfermedad de Creutzfledt-Jakob en México: un análisis retrospectivo]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Choreño-Parra]]></surname>
<given-names><![CDATA[José A.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pacheco-Sánchez]]></surname>
<given-names><![CDATA[Francisco J.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
<xref ref-type="aff" rid="A a"/>
<xref ref-type="aff" rid="A4"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez-Nava]]></surname>
<given-names><![CDATA[Alberto I.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
<xref ref-type="aff" rid="A a"/>
<xref ref-type="aff" rid="A4"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[García-Quintero]]></surname>
<given-names><![CDATA[Gabriela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
<xref ref-type="aff" rid="A a"/>
<xref ref-type="aff" rid="A4"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez-Muñoz]]></surname>
<given-names><![CDATA[Patricia E.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Guadarrama-Ortiz]]></surname>
<given-names><![CDATA[Parménides]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Especializado en Neurocirugía y Neurociencias México Department of Neurosurgery ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto Politécnico Nacional Escuela Nacional de Ciencias Biológicas ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Centro Especializado en Neurocirugía y Neurociencias México Internado Médico de Pregrado ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Instituto Politécnico Nacional Escuela Nacional de Medicina y Homeopatía ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<volume>21</volume>
<numero>6</numero>
<fpage>228</fpage>
<lpage>234</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1665-50442020000600228&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1665-50442020000600228&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1665-50442020000600228&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Background: Little is known about the clinical characteristics and significance of Creutzfeldt-Jakob disease (CJD) in Mexico.  Objective: This study aimed to conduct a retrospective revision and analysis of the clinical cases of Mexican patients with CJD available in the literature.  Methods: We systematically searched electronic databases for studies in English and Spanish conducted in Mexico over the period of 1990-2020 that involved Mexican patients with any of the clinical forms of CJD. Clinical variables were extracted from the selected studies that met eligibility criteria. Descriptive statistics were used to characterize the study population.  Results: A total of seven studies were included in the analysis. From these, 29 cases were revised, and their clinical characteristics analyzed. The median age at the time of diagnosis was 54 years (range 23-75 years). CJD was more frequent among females than male patients (male:female ratio 1:1.41). Most patients resided in Mexico City and the State of Mexico, and 93% attended public hospitals. The most frequent form of CJD was sporadic, with only two probable cases of familiar disease. The most common clinical symptoms observed in order or frequency were rapidly progressive dementia (68.9%), cerebellar signs (51.7%), neuropsychiatric symptoms (51.7%), akinetic mutism (51.7%), myoclonus (44,8%), extrapyramidal signs (44.8%), visual disturbances (41.3%), pyramidal signs (31%), and sleep disorders (17.2%). Only 20% of the cases were confirmed by histopathological analysis of brain biopsy or autopsy specimens.  Conclusions: Our study provides an overview of the main clinical characteristics of CJD in Mexican patients.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Antecedentes: Se sabe poco sobre las características clínicas y la importancia de la enfermedad de Creutzfeldt-Jakob (ECJ) en México.  Objetivo: Este estudio tuvo como objetivo realizar una revisión y análisis retrospectivo de los casos clínicos de pacientes mexicanos con ECJ disponibles en la literatura.  Métodos: Se hizo una búsqueda sistemática en bases de datos electrónicas de estudios en inglés y español realizados en México durante el período de 1990 a 2020, que involucraron a pacientes mexicanos con cualquiera de las formas clínicas de ECJ. Se extrajeron variables clínicas de los estudios seleccionados que cumplieron con los criterios de elegibilidad. Se utilizó estadística descriptiva para caracterizar la población de estudio.  Resultados: Se incluyó un total de siete estudios en el análisis. De estos, se revisaron 29 casos y se analizaron sus características clínicas. La mediana de edad en el momento del diagnóstico fue de 54 años (rango de 23 a 75 años). La ECJ fue más frecuente entre las mujeres que entre los hombres (proporción hombre: mujer 1: 1.41). La mayoría de los pacientes residían en la Ciudad de México y el Estado de México y el 93% acudía a hospitales públicos. La forma más frecuente de ECJ fue esporádica, con solo dos casos probables de enfermedad familiar. Los síntomas clínicos más comunes observados en orden o frecuencia fueron demencia rápidamente progresiva (68.9%), signos cerebelosos (51.7%), síntomas neuropsiquiátricos (51.7%), mutismo acinético (51.7%), mioclonías (44.8%), signos extrapiramidales. (44.8%), alteraciones visuales (41.3%), signos piramidales (31%) y trastornos del sueño (17.2%). Solo el 20% de los casos fueron confirmados por análisis histopatológico de biopsias cerebrales o muestras de autopsias.  Conclusiones: En conclusión, nuestro estudio ofrece una visión general de las principales características clínicas de la ECJ en pacientes mexicanos.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Creutzfeldt-Jakob disease]]></kwd>
<kwd lng="en"><![CDATA[Prion]]></kwd>
<kwd lng="en"><![CDATA[Cognitive decline]]></kwd>
<kwd lng="en"><![CDATA[Rapidly progressive dementia]]></kwd>
<kwd lng="en"><![CDATA[Spongiform encephalopathy]]></kwd>
<kwd lng="es"><![CDATA[Enfermedad de Cretuzfeldt-Jakob]]></kwd>
<kwd lng="es"><![CDATA[Prion]]></kwd>
<kwd lng="es"><![CDATA[Deterioro cognitivo]]></kwd>
<kwd lng="es"><![CDATA[Demencia rápidamente progresiva]]></kwd>
<kwd lng="es"><![CDATA[Encefalopatía espongiforme]]></kwd>
</kwd-group>
</article-meta>
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