<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1665-5044</journal-id>
<journal-title><![CDATA[Revista mexicana de neurociencia]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. mex. neurocienc.]]></abbrev-journal-title>
<issn>1665-5044</issn>
<publisher>
<publisher-name><![CDATA[Academia Mexicana de Neurología A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1665-50442019000600275</article-id>
<article-id pub-id-type="doi">10.24875/rmn.19000074</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Respiratory complications of amyotrophic lateral sclerosis]]></article-title>
<article-title xml:lang="es"><![CDATA[Complicaciones respiratorias de la esclerosis lateral amiotrófica]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Arroyo-Rojas]]></surname>
<given-names><![CDATA[Monserrat E.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Torres-Fraga]]></surname>
<given-names><![CDATA[Martha G.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez-Reyes]]></surname>
<given-names><![CDATA[Yadira G.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Guerrero-Zúñiga]]></surname>
<given-names><![CDATA[Selene]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Carrillo-Alduenda]]></surname>
<given-names><![CDATA[José L.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Nacional de Enfermedades Respiratorias Ismael Cosío Villegas Sleep Medicine Unit ]]></institution>
<addr-line><![CDATA[Mexico City ]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2019</year>
</pub-date>
<volume>20</volume>
<numero>6</numero>
<fpage>275</fpage>
<lpage>283</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1665-50442019000600275&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1665-50442019000600275&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1665-50442019000600275&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Amyotrophic lateral sclerosis (ALS) is a progressive and fatal neurodegenerative disease that inevitably affects the respiratory system, and part of its treatment focuses on improving symptoms and minimizing its respiratory complications which are the main cause of death; thus, the purpose of the following review is to describe the pulmonary involvement of ALS, to propose diagnostic/monitoring guidelines, and to expose its therapeutic options. The alveolar hypoventilation syndrome and the poor management of bronchial secretion are the main respiratory difficulties secondary to ALS and they are due to the weakness of the muscles that generate respiration; in this way, the periodic assessment of respiratory function is imperative for monitoring and detecting these complications in early stages. The care of patients with ALS should be multidisciplinary and ideally should be performed in specialized centers; non-invasive mechanical ventilation and assisted cough (manual or mechanical) are the two most cost/effective techniques to treat alveolar hypoventilation and poor secretion management to increase survival, improve symptoms, and increase quality of life.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen La esclerosis lateral amiotrófica (ELA) es una enfermedad neurodegenerativa progresiva y mortal que inevitablemente afecta el sistema respiratorio, por lo que parte de su tratamiento se enfoca en mejorar los síntomas y minimizar sus complicaciones respiratorias, que son la principal causa de muerte; así, el objetivo de la siguiente revisión es describir la afectación pulmonar de la ELA, proponer pautas de diagnóstico/monitoreo y exponer sus opciones terapéuticas. El síndrome de hipoventilación alveolar y el mal manejo de secreción bronquial son las principales alteraciones respiratorias secundarias a la ELA y se deben a la debilidad de los músculos que generan respiración. De esta manera, la evaluación periódica de la función respiratoria es imprescindible para controlar y detectar estas complicaciones en las etapas iniciales. La atención de los pacientes con ELA debe ser multidisciplinaria e idealmente debe realizarse en centros especializados. La ventilación mecánica no invasiva y la tos asistida (manual o mecánica) son las dos técnicas más rentables para tratar la hipoventilación alveolar y el manejo deficiente de las secreciones para prolongar la supervivencia, mejorar los síntomas y aumentar la calidad de vida.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Amyotrophic lateral sclerosis]]></kwd>
<kwd lng="en"><![CDATA[Hypoventilation]]></kwd>
<kwd lng="en"><![CDATA[Respiration]]></kwd>
<kwd lng="en"><![CDATA[Artificial]]></kwd>
<kwd lng="en"><![CDATA[Respiratory function tests]]></kwd>
<kwd lng="es"><![CDATA[Esclerosis lateral amiotrófica]]></kwd>
<kwd lng="es"><![CDATA[Hipoventilación alveolar]]></kwd>
<kwd lng="es"><![CDATA[Respiración artificial]]></kwd>
<kwd lng="es"><![CDATA[Pruebas de función respiratoria]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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