<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1665-1146</journal-id>
<journal-title><![CDATA[Boletín médico del Hospital Infantil de México]]></journal-title>
<abbrev-journal-title><![CDATA[Bol. Med. Hosp. Infant. Mex.]]></abbrev-journal-title>
<issn>1665-1146</issn>
<publisher>
<publisher-name><![CDATA[Instituto Nacional de Salud, Hospital Infantil de México Federico Gómez]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1665-11462025000400006</article-id>
<article-id pub-id-type="doi">10.24875/bmhim.24000070</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[COVID-19 infection and intense physical activity in hypokalemic periodic paralysis]]></article-title>
<article-title xml:lang="es"><![CDATA[Infección por COVID-19 y actividad física intensa en la parálisis periódica hipopotasémica]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cammarata-Scalisi]]></surname>
<given-names><![CDATA[Francisco]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Martín]]></surname>
<given-names><![CDATA[Esteban San]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cárdenas-Tadich]]></surname>
<given-names><![CDATA[Antonio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Araya-Castillo]]></surname>
<given-names><![CDATA[Maykol]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Peralta-Aros]]></surname>
<given-names><![CDATA[Carolina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Olivares]]></surname>
<given-names><![CDATA[Víctor]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bertini]]></surname>
<given-names><![CDATA[Enrico]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Willoughby]]></surname>
<given-names><![CDATA[Colin E.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Callea]]></surname>
<given-names><![CDATA[Michele]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Regional de Antofagasta Pediatrics Service ]]></institution>
<addr-line><![CDATA[Antofagasta ]]></addr-line>
<country>Chile</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Regional de Concepción Adult Genetics Unit ]]></institution>
<addr-line><![CDATA[Antofagasta ]]></addr-line>
<country>Chile</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Regional de Antofagasta Clinical Laboratory ]]></institution>
<addr-line><![CDATA[Antofagasta ]]></addr-line>
<country>Chile</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Bambino Gesù Children’s Research Hospital IRCCS Unit of Neuromuscular and Neurodegenerative Disease ]]></institution>
<addr-line><![CDATA[Rome ]]></addr-line>
<country>Italy</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Ulster University Biomedical Sciences Research Institute Genomic Medicine]]></institution>
<addr-line><![CDATA[Northern Ireland ]]></addr-line>
<country>UK</country>
</aff>
<aff id="Af6">
<institution><![CDATA[,University of Florence Postgraduate Program in Oral Surgery ]]></institution>
<addr-line><![CDATA[Florence ]]></addr-line>
<country>Italy</country>
</aff>
<aff id="Af7">
<institution><![CDATA[,University of Nova Gorica Doctoral Program in Molecular Genetics and Biotechnology ]]></institution>
<addr-line><![CDATA[Nova Gorica ]]></addr-line>
<country>Slovenia</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>08</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>08</month>
<year>2025</year>
</pub-date>
<volume>82</volume>
<numero>4</numero>
<fpage>252</fpage>
<lpage>257</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1665-11462025000400006&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1665-11462025000400006&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1665-11462025000400006&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Background: Hypokalemic periodic paralysis (HPP) is a rare genetic neuromuscular disorder characterized by an autosomal dominant inheritance pattern and a variable clinical phenotype. It is associated with low potassium levels due to defects in muscle ion channels. HPP can be life-threatening, but it can be completely reversed if diagnosed and treated promptly and correctly. Pathogenic variants in a heterozygous in the CACNA1S or SCN4A genes lead to HPP.  Clinical case: We present a 16-year-old male with a clinical history of flaccid paralysis associated with hypokalemia following intense physical activity and subsequent COVID-19 infection. During this evaluation, his 12-year-old maternal half-brother exhibited similar symptoms related to intense physical exercise. The affected mother, maternal aunt, and maternal grandfather have variable clinical histories. Genetic testing identified a heterozygous pathogenic variation in the CACNA1S gene (c.2700G&gt;A; p.Arg900Ser) in the patient, his mother, and maternal half-brother.  Conclusion: The availability of a positive family history facilitates diagnostic guidance and provides insight into the factors triggering crises. Education is the first step in contributing to prevention and management. Furthermore, understanding the etiological cause is crucial for offering available therapeutic options and providing family genetic counseling.]]></p></abstract>
<abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Introducción: La parálisis periódica hipopotasémica (PPH) es un trastorno genético neuromuscular raro con un patrón de herencia autosómico dominante y un fenotipo clínico variable que se relaciona con niveles bajos de potasio secundarios a un defecto en los canales iónicos musculares. La PPH puede poner en peligro la vida, pero puede revertirse por completo si se diagnostica y trata de manera oportuna y correcta. Las variantes patogénicas en heterocigosis en los genes CACNA1S o SCN4A dan como resultado PPH.  Caso clínico: Se presenta el caso de un varón de 16 años con antecedentes clínicos de parálisis fláccida asociada a hipopotasemia después de una actividad física intensa con COVID-19. Durante esta evaluación, su hermano materno de 12 años manifestó síntomas similares asociados al ejercicio físico intenso. La madre, la tía materna y el abuelo materno estaban afectados con antecedentes clínicos variables. El estudio genético identificó una variación patogénica en heterocigosis en el gen CACNA1S (c.2700G&gt;A; p.Arg900Ser) en el paciente, su madre y el hermano materno.  Conclusiones: La disponibilidad de antecedentes familiares positivos facilita la orientación diagnóstica y agrega información sobre las causas que desencadenan las crisis, siendo la educación el primer paso para contribuir a la prevención y el manejo. Asimismo, se destaca la importancia de conocer la etiología para brindar las opciones terapéuticas disponibles y ofrecer un consejo genético familiar.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Hypokalemic periodic paralysis]]></kwd>
<kwd lng="en"><![CDATA[COVID-19]]></kwd>
<kwd lng="en"><![CDATA[CACNA1S]]></kwd>
<kwd lng="en"><![CDATA[Management]]></kwd>
<kwd lng="es"><![CDATA[Parálisis periódica hipopotasémica]]></kwd>
<kwd lng="es"><![CDATA[COVID-19]]></kwd>
<kwd lng="es"><![CDATA[CACNA1S]]></kwd>
<kwd lng="es"><![CDATA[Manejo]]></kwd>
</kwd-group>
</article-meta>
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