<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1665-1146</journal-id>
<journal-title><![CDATA[Boletín médico del Hospital Infantil de México]]></journal-title>
<abbrev-journal-title><![CDATA[Bol. Med. Hosp. Infant. Mex.]]></abbrev-journal-title>
<issn>1665-1146</issn>
<publisher>
<publisher-name><![CDATA[Instituto Nacional de Salud, Hospital Infantil de México Federico Gómez]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1665-11462021000600612</article-id>
<article-id pub-id-type="doi">10.24875/bmhim.20000399</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Fórmulas metabólicas disponibles en México para pacientes con fenilcetonuria]]></article-title>
<article-title xml:lang="en"><![CDATA[Metabolic formulas for phenylketonuric patients available in Mexico]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López-Mejía]]></surname>
<given-names><![CDATA[Lizbeth]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Guillén-López]]></surname>
<given-names><![CDATA[Sara]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vela-Amieva]]></surname>
<given-names><![CDATA[Marcela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Nacional de Pediatrí Laboratorio de Errores Innatos del Metabolismo y Tamiz ]]></institution>
<addr-line><![CDATA[Ciudad de México ]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2021</year>
</pub-date>
<volume>78</volume>
<numero>6</numero>
<fpage>612</fpage>
<lpage>620</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1665-11462021000600612&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1665-11462021000600612&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1665-11462021000600612&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen La fenilcetonuria y otras hiperfenilalaninemias son enfermedades genéticas cuya detección actualmente es obligatoria en México, tanto en el sector público como en el privado. La detección y el tratamiento oportunos han demostrado prevenir las manifestaciones neurológicas y la discapacidad que caracterizan esta enfermedad. Por ello, es de suma importancia que el pediatra y el personal de salud involucrados en la atención de estos pacientes conozcan, comprendan e implementen el manejo nutricional de manera correcta. Aunque existen varios tratamientos, el más utilizado es la restricción dietética de fenilalanina. El tratamiento nutricio incluye el uso de la llamada «fórmula médica» o «fórmula metabólica sin fenilalanina», la cual fue concebida desde el primer tercio del siglo XX. Posteriormente, se han realizado múltiples estudios y modificaciones con el fin de mejorar el pronóstico de los pacientes. El presente trabajo describe las principales características y diferencias entre las fórmulas libres de fenilalanina de seguimiento disponibles en México, para que el personal de salud cuente con elementos para su correcta prescripción.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Hyperphenylalaninemias such as phenylketonuria are rare genetic diseases whose detection is currently mandated nationwide in both the public and private sectors in Mexico. Timely detection, diagnosis and treatment have been shown to prevent the neurological manifestations and disability that characterize this disease. Therefore, the importance of health personnel in charge of these patients to know, understand, and be able to implement an adequate nutritional management. Currently, although there are several treatments approaches, the most common has been dietary restriction of phenylalanine. Nutritional treatment includes the use of the so-called &#8220;medical formula&#8221; or &#8220;phenylalanine-free metabolic formula&#8221;, which was conceived from the first third of the 20th century. Subsequently, many studies and modifications have been performed to improve patient outcomes. This review aimed to describe the main characteristics and the differences between the metabolic follow-up formulas available in Mexico, so that health personnel have elements for their correct prescription.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Fenilcetonuria]]></kwd>
<kwd lng="es"><![CDATA[Alimentos especializados]]></kwd>
<kwd lng="es"><![CDATA[Proteína]]></kwd>
<kwd lng="es"><![CDATA[Micronutrimentos]]></kwd>
<kwd lng="en"><![CDATA[Phenylketonuria]]></kwd>
<kwd lng="en"><![CDATA[Specialized foods]]></kwd>
<kwd lng="en"><![CDATA[Proteins]]></kwd>
<kwd lng="en"><![CDATA[Micronutrients]]></kwd>
</kwd-group>
</article-meta>
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