<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1405-9940</journal-id>
<journal-title><![CDATA[Archivos de cardiología de México]]></journal-title>
<abbrev-journal-title><![CDATA[Arch. Cardiol. Méx.]]></abbrev-journal-title>
<issn>1405-9940</issn>
<publisher>
<publisher-name><![CDATA[Instituto Nacional de Cardiología Ignacio Chávez]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1405-99402022000100060</article-id>
<article-id pub-id-type="doi">10.24875/acm.21000011</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Características y evolución de los pacientes con amiloidosis sistémica y compromiso cardíaco]]></article-title>
<article-title xml:lang="en"><![CDATA[Features and evolution of patients with systemic amyloidosis and cardiac involvement]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Carretero]]></surname>
<given-names><![CDATA[Marcelina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Aguirre]]></surname>
<given-names><![CDATA[María A.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Villanueva]]></surname>
<given-names><![CDATA[Eugenia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Nucifora]]></surname>
<given-names><![CDATA[Elsa]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Posadas-Martínez]]></surname>
<given-names><![CDATA[María Lourdes]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Italiano de Buenos Aires Servicio de Clínica Médica ]]></institution>
<addr-line><![CDATA[Buenos Aires ]]></addr-line>
<country>Argentina</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Italiano de Buenos Aires Servicio de Clínica Médica ]]></institution>
<addr-line><![CDATA[Buenos Aires ]]></addr-line>
<country>Argentina</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Italiano de Buenos Aires Servicio de Cardiología ]]></institution>
<addr-line><![CDATA[Buenos Aires ]]></addr-line>
<country>Argentina</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Hospital Italiano de Buenos Aires Sección de Hematología ]]></institution>
<addr-line><![CDATA[Buenos Aires ]]></addr-line>
<country>Argentina</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Hospital Italiano de Buenos Aires  ]]></institution>
<addr-line><![CDATA[Buenos Aires ]]></addr-line>
<country>Argentina</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2022</year>
</pub-date>
<volume>92</volume>
<numero>1</numero>
<fpage>60</fpage>
<lpage>67</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1405-99402022000100060&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1405-99402022000100060&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1405-99402022000100060&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Objetivos: Determinar la prevalencia de amiloidosis cardíaca en pacientes con amiloidosis sistémica. Comparar la supervivencia según sea que presenten o no compromiso cardíaco.  Métodos: Cohorte retrospectiva de pacientes con amiloidosis sistémica del Registro Institucional de Amiloidosis del Hospital Italiano de Buenos Aires, entre 2010 y 2019. Se consideró como compromiso cardíaco la presencia de síntomas o imágenes consistentes con amiloidosis no explicado por otras causas. Se evaluó la muerte por todas las causas. Se calculó la sobrevida mediante Kaplan-Meier. Los factores relacionados con mortalidad se evaluaron con un modelo de regresión de Cox. Se evaluó el trasplante cardíaco en un modelo de regresión de riesgo competitivo.  Resultados: La prevalencia de compromiso cardíaco fue del 63%. La incidencia de muerte fue de 14/1,000 personas-meses para el grupo con compromiso cardíaco y de 5/1,000 personas-meses para los pacientes sin compromiso. Los pacientes con compromiso cardíaco tuvieron una sobrevida global a los cinco años de 44% contra 67% en los que no tenían compromiso (p = 0.02). El HR crudo para el compromiso cardíaco fue de 2.09 (p = 0.02). La edad mostró un HR ajustado de 1.06 (p &lt;0.01). El modelo de regresión de riesgos competitivos estableció un sub-HR de 1.86 (IC95%, 0.99-3.49; p = 0.05).  Conclusiones: El compromiso cardíaco es un factor pronóstico importante en pacientes con amiloidosis.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Objective: To estimate the prevalence of cardiac amyloidosis in patients with systemic amyloidosis. Compare survival rates based on whether they show cardiac involvement.  Methods: A retrospective cohort study of patients with systemic amyloidosis from the Institutional Amyloidosis Registry of the Hospital Italian of Buenos Aires from 2010 to 2019. Heart involvement is considered to be the presence of symptoms and/or images consistent with amyloidosis, and there is no other reason to explain it. All deaths due to causes were evaluated. The survival rate was estimated by Kaplan-Meier. Cox regression model was used to evaluate factors related to mortality. Heart transplantation was evaluated in a competitive risk regression model.  Results: The prevalence of heart involvement is 63%. For the group with heart damage, the death rate was 14/1,000 person-months, and for patients without damage, the death rate was 5/1,000 person-months. The 5-year overall survival rate for patients with heart involvement was 44%, while that for patients without damage was 67% (p = 0.02). The original HR for heart involvement was 2.09 (p = 0.02). Age showed that HRa was 1.06 (p &lt;0.01). The sub-HR estimated by the competitive risk regression model are 1.86 (95% CI 0.99-3.49) p = 0.05.  Conclusion: Cardiac involvement is an important prognostic factor in patients with amyloidosis.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Amiloidosis]]></kwd>
<kwd lng="es"><![CDATA[Amiloidosis de cadenas ligeras de las inmunoglobulinas]]></kwd>
<kwd lng="es"><![CDATA[Amiloidosis familiar]]></kwd>
<kwd lng="es"><![CDATA[Miocardiopatía restrictiva]]></kwd>
<kwd lng="en"><![CDATA[Amyloidosis]]></kwd>
<kwd lng="en"><![CDATA[Immunoglobulin light chain amyloidosis]]></kwd>
<kwd lng="en"><![CDATA[Familial amyloidosis]]></kwd>
<kwd lng="en"><![CDATA[Restrictive cardiomyopathy]]></kwd>
</kwd-group>
</article-meta>
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