<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1405-0099</journal-id>
<journal-title><![CDATA[Cirujano general]]></journal-title>
<abbrev-journal-title><![CDATA[Cir. gen]]></abbrev-journal-title>
<issn>1405-0099</issn>
<publisher>
<publisher-name><![CDATA[Asociación Mexicana de Cirugía General A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1405-00992025000100037</article-id>
<article-id pub-id-type="doi">10.35366/119611</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Asociación VACTERL: Hospital Universitario de Puebla]]></article-title>
<article-title xml:lang="en"><![CDATA[VACTERL Association: Hospital Universitario de Puebla]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López Mestas]]></surname>
<given-names><![CDATA[Hilberth Cristhian]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Romero Cuevas]]></surname>
<given-names><![CDATA[Luis Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rosa Tavera]]></surname>
<given-names><![CDATA[Tania de la]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Carrasquel Valecillos]]></surname>
<given-names><![CDATA[María]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Díaz Barrientos]]></surname>
<given-names><![CDATA[Cheryl]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Universitario de Puebla  ]]></institution>
<addr-line><![CDATA[Puebla Puebla]]></addr-line>
<country>México</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Universitario de Puebla  ]]></institution>
<addr-line><![CDATA[Puebla Puebla]]></addr-line>
<country>México</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Universitario de Puebla  ]]></institution>
<addr-line><![CDATA[Puebla Puebla]]></addr-line>
<country>México</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Hospital Universitario de Puebla Servicio de Cirugía Pediátrica ]]></institution>
<addr-line><![CDATA[Puebla Puebla]]></addr-line>
<country>México</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Hospital Universitario de Puebla Servicio de Coloproctología ]]></institution>
<addr-line><![CDATA[Puebla Puebla]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2025</year>
</pub-date>
<volume>47</volume>
<numero>1</numero>
<fpage>37</fpage>
<lpage>42</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1405-00992025000100037&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1405-00992025000100037&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1405-00992025000100037&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: La asociación VACTER o VACTERL es una patología con baja prevalencia en nuestro medio, es caracterizada por diferentes malformaciones congénitas y toma su nombre del acrónimo correspondiente a este grupo de malformaciones que se presentan: Anomalías Vertebrales, Atresia Anal, Cardiovasculares, fístulas Traqueo-Esofágicas, Renales y extremidades (Limbs). La prevalencia de esta condición es de 1/10,000 nacidos vivos y en México sólo se han reportado 141 casos, por lo que el objetivo de este artículo es el reporte del primer caso clínico que se presenta en el Hospital Universitario de Puebla y su manejo quirúrgico. Se trata de paciente femenino con diagnóstico prenatal a las 32.2 semanas de gestación por resonancia magnética, con arteria umbilical única, atresia esofágica asociada a polihidramnios, atresia duodenal vs estenosis duodenal, ectrodactilia de pie izquierdo, mesomelia de miembro pélvico izquierdo, dilatación de asa intestinal y hemivértebra torácica. Durante el nacimiento se valoró por la unidad de cuidados intensivos diagnosticando ano imperforado, hipoplasia renal y comunicación interatrial, conducto arterioso permeable grande e hipertensión arterial pulmonar moderada; por lo que se considera que se trata de una asociación VACTERL. Al ser una condición poco frecuente es importante que exista un adecuado control prenatal para poder realizar un abordaje clínico y quirúrgico oportuno.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: The VACTER or VACTERL association is a pathology with low prevalence in our environment, it is characterized by different congenital malformations and takes its name from the acronym corresponding to this group of malformations that occur: Vertebral Anomalies, Anal Atresia, Cardiovascular, Tracheo-Esophageal fistula, Renal and extremities (Limbs). The prevalence of this condition is 1/10,000 live births and in Mexico only 141 cases have been reported, so the objective of this article is the report of the first clinical case presented at the University Hospital of Puebla, and its surgical management. This is a female patient with a prenatal diagnosis at 32.2 weeks of gestation by magnetic resonance imaging, with single umbilical artery, esophageal atresia associated with polyhydramnios, duodenal atresia vs duodenal stenosis, ectrodactyly of the left foot, mesomelia of the left pelvic limb, dilation of the intestinal loop and thoracic hemivertebra. During birth, the intensive care unit assessed the diagnosis of imperforate anus, renal hypoplasia, and atrial septal defect, large patent ductus arteriosus, and moderate pulmonary arterial hypertension; therefore, it is considered that it is a VACTERL association; being a rare condition, it is important that there is adequate prenatal control in order to carry out a timely clinical and surgical approach.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[VACTERL]]></kwd>
<kwd lng="es"><![CDATA[VACTER]]></kwd>
<kwd lng="es"><![CDATA[malformaciones congénitas]]></kwd>
<kwd lng="es"><![CDATA[síndromes]]></kwd>
<kwd lng="en"><![CDATA[VACTERL]]></kwd>
<kwd lng="en"><![CDATA[VACTER]]></kwd>
<kwd lng="en"><![CDATA[congenital malformations]]></kwd>
<kwd lng="en"><![CDATA[syndromes]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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