<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0300-9041</journal-id>
<journal-title><![CDATA[Ginecología y obstetricia de México]]></journal-title>
<abbrev-journal-title><![CDATA[Ginecol. obstet. Méx.]]></abbrev-journal-title>
<issn>0300-9041</issn>
<publisher>
<publisher-name><![CDATA[Federación Mexicana de Colegios de Obstetricia y Ginecología A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0300-90412021000200151</article-id>
<article-id pub-id-type="doi">10.24245/gom.v89i2.4307</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Proteus y embarazo. Reporte de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Proteus syndrome and pregnancy. A case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Peña-Vega]]></surname>
<given-names><![CDATA[Cynthia Jazmín]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ortiz-Jarillo]]></surname>
<given-names><![CDATA[Jenny]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Zavala-Barrios]]></surname>
<given-names><![CDATA[Berenice]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital General de México Dr. Eduardo Liceaga Servicio de Ginecología y Obstetricia ]]></institution>
<addr-line><![CDATA[Cuidad de México ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital General de México Dr. Eduardo Liceaga Servicio de Ginecología y Obstetricia ]]></institution>
<addr-line><![CDATA[Cuidad de México ]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2021</year>
</pub-date>
<volume>89</volume>
<numero>2</numero>
<fpage>151</fpage>
<lpage>159</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0300-90412021000200151&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0300-90412021000200151&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0300-90412021000200151&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen:  ANTECEDENTE: El síndrome de Proteus es una rara enfermedad congénita, de carácter hamartomatoso, que puede afectar todas las estructuras del organismo. Hasta la fecha no existen reportes que evidencien sus implicaciones sexuales y reproductivas.  CASO CLÍNICO: Paciente de 21 años, primigesta, con diagnóstico de síndrome de Proteus a los 6 años, por menarquia temprana. Recibió tratamiento con inhibidores de la hormona de crecimiento, en seguimiento con un equipo multidisciplinario. En la adolescencia se estableció el diagnóstico de miopía e insuficiencia venosa periférica. En consenso se sugirió la interrupción del embarazo por vía abdominal, uso de medias de mediana compresión y ácido acetilsalicílico. En la semana 35 del embarazo tuvo preeclampsia, con criterios de severidad (175-123 mmHg), por lo que se inició tratamiento con soluciones cristaloides, antihipertensivos y esquema Zuspan, con adecuada reacción y estabilización hemodinámica. El feto tuvo anhidramnios y redistribución de flujos hemodinámicos. Siete días después del evento obstétrico se retiraron los antihipertensivos y continuó en vigilancia con el equipo multidisciplinario. La madre y su hija fueron dadas de alta del hospital, sin complicaciones aparentes.  CONCLUSIONES: Las malformaciones vasculares y las alteraciones del tejido adiposo sugieren un factor de riesgo que altera la regulación en la angiogénesis y la insuficiencia venosa supone un promotor de trombosis; a su vez, esto puede considerarse riesgo de preeclampsia, por lo que se sugiere el tratamiento multidisciplinario temprano para evitar complicaciones. Per se, deben informase y recopilarse más casos para aceptar esta hipótesis.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract:  BACKGROUND: Proteus syndrome is a rare, congenital, hamartomatous disease that can affect all the structures of the body. This disorder is not inherited. There are no case reports in the literature that show its sexual and reproductive implications.  CLINICAL CASE: 21-year-old woman, primiparous, diagnosed with Proteus syndrome at 6 years of age, due to early menarche. He received treatment with growth hormone inhibitors, followed by a multidisciplinary team. In adolescence, the diagnosis of myopia and peripheral venous insufficiency was established. In consensus, the interruption of pregnancy by abdominal route, use of medium compression media and acetylsalicylic acid was suggested. At week 35 of the pregnancy, she had preeclampsia, with severity criteria (175-123 mmHg), for which she began treatment with crystalloid solutions, antihypertensives and Zuspan, with a reaction and hemodynamic stabilization. The fetus had anhydramnios and redistribution of hemodynamic flows. Seven days after the obstetric event, the antihypertensive drugs were withdrawn and continued monitoring with the multidisciplinary team. The mother and daughter were released from the hospital without apparent complications.  CONCLUSIONS: Vascular malformations and alterations of adipose tissue suggest a risk factor that alters regulation in angiogenesis and venous insufficiency is a promoter of thrombosis; in turn, this can be considered a risk of preeclampsia, so early multidisciplinary treatment is suggested to avoid complications. So, more cases must be reported and collected to accept this hypothesis.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Proteus]]></kwd>
<kwd lng="es"><![CDATA[reproductivo]]></kwd>
<kwd lng="es"><![CDATA[hormona del crecimiento]]></kwd>
<kwd lng="es"><![CDATA[equipo multidisciplinario]]></kwd>
<kwd lng="es"><![CDATA[miopía]]></kwd>
<kwd lng="es"><![CDATA[insuficiencia venosa periférica]]></kwd>
<kwd lng="es"><![CDATA[consenso]]></kwd>
<kwd lng="es"><![CDATA[embarazo]]></kwd>
<kwd lng="es"><![CDATA[ácido acetilsalicílico]]></kwd>
<kwd lng="es"><![CDATA[preeclampsia]]></kwd>
<kwd lng="es"><![CDATA[soluciones cristaloides]]></kwd>
<kwd lng="es"><![CDATA[antihipertensivos]]></kwd>
<kwd lng="es"><![CDATA[malformaciones vasculares]]></kwd>
<kwd lng="es"><![CDATA[tejido adiposo]]></kwd>
<kwd lng="es"><![CDATA[factores de riesgo]]></kwd>
<kwd lng="es"><![CDATA[trombosis]]></kwd>
<kwd lng="en"><![CDATA[Proteus syndrome]]></kwd>
<kwd lng="en"><![CDATA[Reproductive]]></kwd>
<kwd lng="en"><![CDATA[Growth hormone]]></kwd>
<kwd lng="en"><![CDATA[Multidisciplinary team]]></kwd>
<kwd lng="en"><![CDATA[Myopia]]></kwd>
<kwd lng="en"><![CDATA[Peripheral venous failure]]></kwd>
<kwd lng="en"><![CDATA[Consensus]]></kwd>
<kwd lng="en"><![CDATA[Pregnancy]]></kwd>
<kwd lng="en"><![CDATA[Acetylsalicylic acid]]></kwd>
<kwd lng="en"><![CDATA[Preeclampsia]]></kwd>
<kwd lng="en"><![CDATA[Crystalloid solutions]]></kwd>
<kwd lng="en"><![CDATA[Antihypertensives]]></kwd>
<kwd lng="en"><![CDATA[Vascular malformations]]></kwd>
<kwd lng="en"><![CDATA[Adipose tissue]]></kwd>
<kwd lng="en"><![CDATA[Risk factors]]></kwd>
<kwd lng="en"><![CDATA[Thrombosis]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Guerra-Tapia]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Rodríguez-Vázquez]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome Proteus]]></article-title>
<source><![CDATA[Piel]]></source>
<year>2001</year>
<volume>16</volume>
<page-range>248-52</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Graetz]]></surname>
<given-names><![CDATA[I.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Über einen Fall von sogenannter &#8220;totaler halbseitiger Körperhypertrophie&#8221;]]></article-title>
<source><![CDATA[Z. Kinder-Heilk]]></source>
<year>1928</year>
<volume>45</volume>
<page-range>381-403</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Lal]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Bandyopadhyay]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Sarkar]]></surname>
<given-names><![CDATA[AK.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Unilateral hypertrophic skin lesions, hemimegalencephaly, and meningioma: The many faces of Proteus syndrome]]></article-title>
<source><![CDATA[Indian Dermatol Online J]]></source>
<year>2015</year>
<volume>6</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>348-51</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Carbajal]]></surname>
<given-names><![CDATA[LR]]></given-names>
</name>
<name>
<surname><![CDATA[Navarrete]]></surname>
<given-names><![CDATA[MJ.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Editorial: Enfermedades raras]]></article-title>
<source><![CDATA[Acta Pediatr Mex]]></source>
<year>2015</year>
<volume>36</volume>
<page-range>369-73</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Child]]></surname>
<given-names><![CDATA[FJ]]></given-names>
</name>
<name>
<surname><![CDATA[Werring]]></surname>
<given-names><![CDATA[DJ]]></given-names>
</name>
<name>
<surname><![CDATA[Vivier]]></surname>
<given-names><![CDATA[EW.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome: diagnosis in adulthood]]></article-title>
<source><![CDATA[Br J Dermatol]]></source>
<year>1998</year>
<volume>139</volume>
<page-range>132-6</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Rocha]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Estrella]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Amaral]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Barbosa]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome]]></article-title>
<source><![CDATA[An Bras Dermatol]]></source>
<year>2017</year>
<volume>92</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>717-20</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Redondo]]></surname>
<given-names><![CDATA[P.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Malformaciones vasculares (I). Concepto, clasificación, fisiopatogenia y manifestaciones clínicas]]></article-title>
<source><![CDATA[Actas Dermo-Sifiliogr]]></source>
<year>2007</year>
<volume>98</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>141-58</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sánchez López]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Martínez Fernández]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Santamaría Carro]]></surname>
<given-names><![CDATA[A.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Manifestaciones oculares en el síndrome de Proteus]]></article-title>
<source><![CDATA[Arch Soc Esp Oftalmol]]></source>
<year>2007</year>
<volume>82</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>175-8</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Capurro]]></surname>
<given-names><![CDATA[NJ]]></given-names>
</name>
<name>
<surname><![CDATA[Carignano]]></surname>
<given-names><![CDATA[AM]]></given-names>
</name>
<name>
<surname><![CDATA[Ottino]]></surname>
<given-names><![CDATA[A.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proliferación fibrosa cerebriforme, correlación con el síndrome de Proteus]]></article-title>
<source><![CDATA[Patología]]></source>
<year>2008</year>
<volume>46</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>351-4</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bennàsar]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Ferrando]]></surname>
<given-names><![CDATA[J.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndromes de neoplasias múltiples familiares con manifestaciones cutáneas]]></article-title>
<source><![CDATA[Med Cutan Iber Lat Am]]></source>
<year>2009</year>
<volume>37</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>71-8</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Say]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Carpenter]]></surname>
<given-names><![CDATA[NJ.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Report of a case resembling the Proteus syndrome with a chromosome abnormality]]></article-title>
<source><![CDATA[Am J Med Genet]]></source>
<year>1988</year>
<volume>31</volume>
<page-range>987-9</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Vaughn]]></surname>
<given-names><![CDATA[RY]]></given-names>
</name>
<name>
<surname><![CDATA[Selinger]]></surname>
<given-names><![CDATA[AD]]></given-names>
</name>
<name>
<surname><![CDATA[Howell]]></surname>
<given-names><![CDATA[CG]]></given-names>
</name>
<name>
<surname><![CDATA[Parrish]]></surname>
<given-names><![CDATA[RA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome: diagnosis and surgical management]]></article-title>
<source><![CDATA[J Pediatr Surg]]></source>
<year>1993</year>
<volume>28</volume>
<page-range>5-10</page-range></nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Hamm]]></surname>
<given-names><![CDATA[H.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Cutaneous mosaicism of lethal mutations]]></article-title>
<source><![CDATA[Am J Med Genet]]></source>
<year>1999</year>
<volume>85</volume>
<page-range>342-5</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Happle]]></surname>
<given-names><![CDATA[R.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Lethal genes surviving by mosaicism: a possible explanation for sporadic birth defects involving the skin]]></article-title>
<source><![CDATA[J Am Acad Dermatol]]></source>
<year>1987</year>
<volume>16</volume>
<page-range>899-906</page-range></nlm-citation>
</ref>
<ref id="B15">
<label>15</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bouzas]]></surname>
<given-names><![CDATA[EA]]></given-names>
</name>
<name>
<surname><![CDATA[Krasnewich]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Koutroumanidis]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Papadimitriou]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Ophthalmologic examination in the diagnosis of Proteus syndrome]]></article-title>
<source><![CDATA[Ophthalmol]]></source>
<year>1993</year>
<volume>100</volume>
<page-range>334-8</page-range></nlm-citation>
</ref>
<ref id="B16">
<label>16</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Newman]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Urbach]]></surname>
<given-names><![CDATA[AH]]></given-names>
</name>
<name>
<surname><![CDATA[Orenstein]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Dickman]]></surname>
<given-names><![CDATA[PS.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome: emphasis on the pulmonary manifestations]]></article-title>
<source><![CDATA[Pediatr Radiol]]></source>
<year>1994</year>
<volume>24</volume>
<page-range>189-93</page-range></nlm-citation>
</ref>
<ref id="B17">
<label>17</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Eberhard]]></surname>
<given-names><![CDATA[DA.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Two years old boy with Proteus syndrome and fatal pulmonary thromboembolism]]></article-title>
<source><![CDATA[Pediatr Pathol]]></source>
<year>1994</year>
<volume>14</volume>
<page-range>771-9</page-range></nlm-citation>
</ref>
<ref id="B18">
<label>18</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bale]]></surname>
<given-names><![CDATA[PM]]></given-names>
</name>
<name>
<surname><![CDATA[Watson]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Collins]]></surname>
<given-names><![CDATA[F.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Pathology of osseous and genitourinary lesions of Proteus syndrome]]></article-title>
<source><![CDATA[Pediatr Pathol]]></source>
<year>1993</year>
<volume>13</volume>
<page-range>797-809</page-range></nlm-citation>
</ref>
<ref id="B19">
<label>19</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Del Rosario Barona-Mazuera]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Hidalgo-Galván]]></surname>
<given-names><![CDATA[LR]]></given-names>
</name>
<name>
<surname><![CDATA[De la Luz Orozco-Cobarrubias]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Duran-McKinster]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome: mew findings in seven patients]]></article-title>
<source><![CDATA[Pediatr Dermatol]]></source>
<year>1997</year>
<volume>14</volume>
<page-range>1-5</page-range></nlm-citation>
</ref>
<ref id="B20">
<label>20</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Dietrich]]></surname>
<given-names><![CDATA[RB]]></given-names>
</name>
<name>
<surname><![CDATA[Glidden]]></surname>
<given-names><![CDATA[DE]]></given-names>
</name>
<name>
<surname><![CDATA[Roth]]></surname>
<given-names><![CDATA[GM]]></given-names>
</name>
<name>
<surname><![CDATA[Martin]]></surname>
<given-names><![CDATA[RA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The Proteus syndrome: CNS manifestations]]></article-title>
<source><![CDATA[Am J Neuroradiol]]></source>
<year>1998</year>
<volume>19</volume>
<page-range>987-90</page-range></nlm-citation>
</ref>
<ref id="B21">
<label>21</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Wiedemann]]></surname>
<given-names><![CDATA[HR]]></given-names>
</name>
<name>
<surname><![CDATA[Burgio]]></surname>
<given-names><![CDATA[GR]]></given-names>
</name>
<name>
<surname><![CDATA[Aldenhoff]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Kunze]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The Proteus syndrome]]></article-title>
<source><![CDATA[Eur J Pediatr]]></source>
<year>1983</year>
<volume>140</volume>
<page-range>5-12</page-range></nlm-citation>
</ref>
<ref id="B22">
<label>22</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Clark]]></surname>
<given-names><![CDATA[RD]]></given-names>
</name>
<name>
<surname><![CDATA[Donnai]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Rogers]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Cooper]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome: an expended phenotype]]></article-title>
<source><![CDATA[Am J Med Genet]]></source>
<year>1987</year>
<volume>27</volume>
<page-range>99-117</page-range></nlm-citation>
</ref>
<ref id="B23">
<label>23</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Costa]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Fitch]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Azouz]]></surname>
<given-names><![CDATA[EM]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome: report of two cases with pelvic lipomatosis]]></article-title>
<source><![CDATA[Pediatrics]]></source>
<year>1985</year>
<volume>76</volume>
<page-range>984-9</page-range></nlm-citation>
</ref>
<ref id="B24">
<label>24</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Samlaska]]></surname>
<given-names><![CDATA[CP]]></given-names>
</name>
<name>
<surname><![CDATA[Levin]]></surname>
<given-names><![CDATA[SW]]></given-names>
</name>
<name>
<surname><![CDATA[James]]></surname>
<given-names><![CDATA[WD]]></given-names>
</name>
<name>
<surname><![CDATA[Benson]]></surname>
<given-names><![CDATA[PM]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome]]></article-title>
<source><![CDATA[Arch Dermatol]]></source>
<year>1989</year>
<volume>125</volume>
<page-range>1109-14</page-range></nlm-citation>
</ref>
<ref id="B25">
<label>25</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Hotamisligil]]></surname>
<given-names><![CDATA[GS.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome and hamartoses with overgrowth]]></article-title>
<source><![CDATA[Dysmorphol Clin Genet]]></source>
<year>1990</year>
<volume>4</volume>
<page-range>87-102</page-range></nlm-citation>
</ref>
<ref id="B26">
<label>26</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[DeLone]]></surname>
<given-names><![CDATA[DR]]></given-names>
</name>
<name>
<surname><![CDATA[Brown]]></surname>
<given-names><![CDATA[WD]]></given-names>
</name>
<name>
<surname><![CDATA[Gentry]]></surname>
<given-names><![CDATA[LR.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome: craniofacial and cerebral MRI]]></article-title>
<source><![CDATA[Neuroradiol]]></source>
<year>1999</year>
<volume>41</volume>
<page-range>840-3</page-range></nlm-citation>
</ref>
<ref id="B27">
<label>27</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Biesecker]]></surname>
<given-names><![CDATA[LG]]></given-names>
</name>
<name>
<surname><![CDATA[Happle]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Mulliken]]></surname>
<given-names><![CDATA[JB]]></given-names>
</name>
<name>
<surname><![CDATA[Weksberg]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Proteus syndrome: diagnostic criteria, differential diagnosis, and patient evaluation]]></article-title>
<source><![CDATA[Am J Med Genet]]></source>
<year>1999</year>
<volume>84</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>389-95</page-range></nlm-citation>
</ref>
<ref id="B28">
<label>28</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Ch]]></surname>
<given-names><![CDATA[Schnake]]></given-names>
</name>
<name>
<surname><![CDATA[Vejar]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Solar]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Ibanez]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome Proteus: Contribución a su delineación clínica]]></article-title>
<source><![CDATA[Rev Chil Pediatr]]></source>
<year>1986</year>
<volume>57</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>585-94</page-range></nlm-citation>
</ref>
<ref id="B29">
<label>29</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sapp]]></surname>
<given-names><![CDATA[JC]]></given-names>
</name>
<name>
<surname><![CDATA[Hu]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Zhao]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Gruber]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Schwartz]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Quantifying survival in patients with Proteus syndrome]]></article-title>
<source><![CDATA[Genetics in medicine. Genet Med]]></source>
<year>2017</year>
<volume>19</volume>
<numero>12</numero>
<issue>12</issue>
<page-range>1376-9</page-range></nlm-citation>
</ref>
<ref id="B30">
<label>30</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Rodenbeck]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Greyling]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Anderson]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Davis]]></surname>
<given-names><![CDATA[L.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Early Recognition of Proteus Syndrome]]></article-title>
<source><![CDATA[Pediatr Dermatol]]></source>
<year>2016</year>
<volume>33</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>e306-10</page-range></nlm-citation>
</ref>
<ref id="B31">
<label>31</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Lindhurst]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Yourick]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Yu]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
<name>
<surname><![CDATA[Savage]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Repression of AKT signaling by ARQ 092 in cells and tissues from patients with Proteus syndrome]]></article-title>
<source><![CDATA[Sci Rep.]]></source>
<year>2015</year>
<volume>11</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>17162</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
