<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0187-5337</journal-id>
<journal-title><![CDATA[Perinatología y reproducción humana]]></journal-title>
<abbrev-journal-title><![CDATA[Perinatol. Reprod. Hum.]]></abbrev-journal-title>
<issn>0187-5337</issn>
<publisher>
<publisher-name><![CDATA[Instituto Nacional de Perinatología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0187-53372022000200051</article-id>
<article-id pub-id-type="doi">10.24875/per.22000012</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Múltiples rabdomiomas intracardiacos en vida fetal simulando atresia tricuspídea al nacimiento]]></article-title>
<article-title xml:lang="en"><![CDATA[Multiple intracardiac rhabdomyomas in fetal life mimicking tricuspid atresia at birth]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Martínez-Morales]]></surname>
<given-names><![CDATA[María Cecilia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Márquez-García]]></surname>
<given-names><![CDATA[Edna R.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Machuca-Loeza]]></surname>
<given-names><![CDATA[Maricruz G.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gómez-Rodríguez]]></surname>
<given-names><![CDATA[Guadalupe]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Mercado-García]]></surname>
<given-names><![CDATA[Arturo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Salinas-Urbina]]></surname>
<given-names><![CDATA[Karla S.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Mexicano del Seguro Social Hospital de Ginecología Unidad Médica de Alta Especialidad 48]]></institution>
<addr-line><![CDATA[León Gto]]></addr-line>
<country>México</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto Mexicano del Seguro Social Hospital de Especialidad Unidad Médica de Alta Especialidad 1]]></institution>
<addr-line><![CDATA[León Gto]]></addr-line>
<country>México</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Instituto Mexicano del Seguro Social Hospital de Ginecología y Pediatría Unidad Médica de Alta Especialidad 48]]></institution>
<addr-line><![CDATA[León Gto]]></addr-line>
<country>México</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Instituto Mexicano del Seguro Social Hospital de Ginecología y Pediatría Unidad Médica de Alta Especialidad 48]]></institution>
<addr-line><![CDATA[León Gto]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>36</volume>
<numero>2</numero>
<fpage>51</fpage>
<lpage>55</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0187-53372022000200051&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0187-53372022000200051&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0187-53372022000200051&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen El rabdomioma es el tumor intracardiaco primario más frecuente en niños. Presentamos el caso de un paciente con diagnóstico de múltiples rabdomiomas intracardiacos durante la vida fetal y al nacimiento con cianosis persistente. Se detectan ecocardiográficamente tumoraciones en atrio derecho con protrusión hacia el ventrículo derecho, obstruyendo el flujo de la válvula tricúspide. El flujo sistémico dependía del foramen oval (cortocircuito de derecha a izquierda) y el pulmonar del conducto arterioso (cortocircuito de izquierda a derecha), asemejando una atresia tricuspidea. Se inició tratamiento con sirolimus y prostaglandinas y se intentó colocar un stent en el conducto arterioso, sin éxito. Se realizó resección del rabdiomioma que obstruía la válvula tricúspide. Durante la cirugía, el paciente presentó taquicardia supraventricular y falleció por falla cardiaca poscardiotomía. Aunque la mayoría de los rabdomiomas tienen regresión espontánea o responden al manejo con inhibidores de mTOR, la afectación hemodinámica indica el manejo quirúrgico.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Rhabdomyoma is the most common primary intracardiac tumor in children. We present the case of a patient diagnosed with multiple intracardiac rhabdomyomas during fetal life and with persistent cyanosis at birth. Echocardiographically, tumors were detected in the right atrium with protrusion towards the right ventricle, obstructing the flow of the tricuspid valve. The systemic flow depended on the foramen ovale (short circuit from right to left) and the pulmonary artery from the ductus arteriosus (short circuit from left to right), resembling tricuspid atresia. Treatment started with sirolimus and prostaglandins and an attempt to place a stent in the ductus arteriosus, without success. Resection of the rhabdomyoma obstructing the tricuspid valve was performed. During surgery, the patient presented supraventricular tachycardia and died of post-cardiotomy heart failure. Although most rhabdomyomas regress spontaneously or respond to management with mTOR inhibitors, hemodynamic compromise indicates surgical management.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Rabdomioma cardiaco]]></kwd>
<kwd lng="es"><![CDATA[Recién nacido]]></kwd>
<kwd lng="es"><![CDATA[Diagnóstico prenatal]]></kwd>
<kwd lng="es"><![CDATA[Atresia tricuspídea]]></kwd>
<kwd lng="en"><![CDATA[Cardiac rhabdomyoma]]></kwd>
<kwd lng="en"><![CDATA[Newborn]]></kwd>
<kwd lng="en"><![CDATA[Prenatal diagnosis]]></kwd>
<kwd lng="en"><![CDATA[Tricuspid atresia]]></kwd>
</kwd-group>
</article-meta>
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