<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0035-0052</journal-id>
<journal-title><![CDATA[Revista mexicana de pediatría]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. mex. pediatr.]]></abbrev-journal-title>
<issn>0035-0052</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Pediatría A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0035-00522021000600244</article-id>
<article-id pub-id-type="doi">10.35366/105427</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Perfil neuropsicológico de un paciente con síndrome de Krabbe de inicio infantil tardío y agnosia visual]]></article-title>
<article-title xml:lang="en"><![CDATA[Neuropsychological profile of a patient with late infantile Krabbe disease and visual agnosia]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Robles-Bermejo]]></surname>
<given-names><![CDATA[Fernando]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fournier-del Castillo]]></surname>
<given-names><![CDATA[María Concepción]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gutiérrez-Solana]]></surname>
<given-names><![CDATA[Luis González]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López-Marín]]></surname>
<given-names><![CDATA[Laura]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Universitario Central de la Defensa Gómez Ulla  ]]></institution>
<addr-line><![CDATA[Madrid ]]></addr-line>
<country>España</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Infantil Universitario Niño Jesús  ]]></institution>
<addr-line><![CDATA[Madrid ]]></addr-line>
<country>España</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2021</year>
</pub-date>
<volume>88</volume>
<numero>6</numero>
<fpage>244</fpage>
<lpage>248</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0035-00522021000600244&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0035-00522021000600244&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0035-00522021000600244&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: La enfermedad de Krabbe es un tipo de leucodistrofia lisosomal autosómica recesiva provocada por la deficiencia de la enzima galactosilceramidasa. Se presentan los resultados de la evaluación neuropsicológica en un niño de tres años, que presenta agnosia visual aperceptiva y prosopagnosia.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Krabbe disease is a type of autosomal recessive lysosomal leukodystrophy caused by deficiency of the enzyme galactosylceramidase. The results of the neuropsychological evaluation in a three-year-old boy with apperceptive visual agnosia and prosopagnosia are presented.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Agnosia aperceptiva]]></kwd>
<kwd lng="es"><![CDATA[deterioro cognitivo]]></kwd>
<kwd lng="es"><![CDATA[enfermedad de Krabbe]]></kwd>
<kwd lng="es"><![CDATA[evaluación neuropsicológica]]></kwd>
<kwd lng="es"><![CDATA[prosopagnosia]]></kwd>
<kwd lng="en"><![CDATA[Apperceptive agnosia]]></kwd>
<kwd lng="en"><![CDATA[cognitive decline]]></kwd>
<kwd lng="en"><![CDATA[Krabbe&#8217;s disease]]></kwd>
<kwd lng="en"><![CDATA[neuropsychological assessment]]></kwd>
<kwd lng="en"><![CDATA[prosopagnosia]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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