<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0028-3746</journal-id>
<journal-title><![CDATA[Neumología y cirugía de tórax]]></journal-title>
<abbrev-journal-title><![CDATA[Neumol. cir. torax]]></abbrev-journal-title>
<issn>0028-3746</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Neumología y Cirugía de Tórax; Instituto Nacional de Enfermedades Respiratorias Ismael Cosío Villegas; Sociedad Cubana de Neumología; Sociedad Paraguaya de Neumología; Sociedad Boliviana de Neumología.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0028-37462024000100013</article-id>
<article-id pub-id-type="doi">10.35366/118571</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Quilotórax secundario a malformación de conducto torácico por síndrome de Klippel-Trénaunay. Reporte de caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Chylothorax secondary to thoracic duct malformation due to Klippel-Trénaunay syndrome. Case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gámez-Saiz]]></surname>
<given-names><![CDATA[Ilse]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López-Ocampo]]></surname>
<given-names><![CDATA[Paris Samahel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Álvarez-Ramos]]></surname>
<given-names><![CDATA[Karen]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sánchez-Zazueta]]></surname>
<given-names><![CDATA[Eduardo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Mexicano del Seguro Social Centro Médico Nacional del Noroeste Hospital de Especialidades No. 2 «Lic. Luis Donaldo Colosio Murrieta»]]></institution>
<addr-line><![CDATA[Ciudad Obregón Sonora]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2024</year>
</pub-date>
<volume>83</volume>
<numero>1</numero>
<fpage>13</fpage>
<lpage>16</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0028-37462024000100013&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0028-37462024000100013&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0028-37462024000100013&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: El síndrome de Klippel-Trénaunay es un síndrome congénito raro, con una incidencia de 1/100,000 casos por año causado por una mutación somática esporádica en el gen PIK3CA. Se caracteriza por una tríada de malformaciones capilares, crecimiento anormal de tejidos blandos y huesos, normalmente afectando extremidades inferiores y várices en lugares atípicos. La presentación de quilotórax es rara y se han documentado pocos casos con alta recidiva del mismo. El diagnóstico del síndrome de Klippel-Trénaunay se realiza mediante estudio de imágenes para corroborar las malformaciones y estudio genéticos que demuestren la mutación somática. Para realizar el diagnóstico de quilotórax se requiere análisis del líquido pleural con un resultado de triglicéridos mayor de 110 mg/dL. El tratamiento para el quilotórax en el síndrome de Klippel-Trénaunay es multidisciplinario, requiriendo apoyo de nutrición, medicina interna y neumología para manejo de complicaciones, así como de cirugía cardiotorácica para tratamiento definitivo.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Klippel-Trenaunay syndrome is a rare congenital syndrome with an incidence of 1/100,000 cases per year caused by a sporadic somatic mutation in the PIK3CA gene. It is characterized by a triad of capillary malformations, abnormal growth of soft tissues and bones, usually affecting the lower extremities, and varicose veins in atypical locations. The presentation of chylothorax is rare, and few cases with high recurrence have been documented. The diagnosis of Klippel-Trenaunay syndrome is made through imaging studies to corroborate the malformations and genetic studies that demonstrate the somatic mutation. Regarding the diagnosis of chylothorax, analysis of the pleural fluid is required with a triglyceride result greater than 110 mg/dL. The treatment for chylothorax in the Klippel-Trenaunay syndrome is multidisciplinary, requiring support from nutrition, internal medicine and pulmonology to manage complications, as well as cardiothoracic surgery for definitive treatment.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[síndrome de Klippel-Trénaunay]]></kwd>
<kwd lng="es"><![CDATA[quilotórax]]></kwd>
<kwd lng="es"><![CDATA[malformaciones linfáticas]]></kwd>
<kwd lng="en"><![CDATA[Klippel-Trenaunay syndrome]]></kwd>
<kwd lng="en"><![CDATA[chylothorax]]></kwd>
<kwd lng="en"><![CDATA[lymphatic malformations]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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