<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0028-3746</journal-id>
<journal-title><![CDATA[Neumología y cirugía de tórax]]></journal-title>
<abbrev-journal-title><![CDATA[Neumol. cir. torax]]></abbrev-journal-title>
<issn>0028-3746</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Neumología y Cirugía de Tórax; Instituto Nacional de Enfermedades Respiratorias Ismael Cosío Villegas; Sociedad Cubana de Neumología; Sociedad Paraguaya de Neumología; Sociedad Boliviana de Neumología.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0028-37462018000400280</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Linfangiomatosis generalizada en pediatría. Reporte de un caso y revisión de la literatura]]></article-title>
<article-title xml:lang="en"><![CDATA[Pediatric generalized lymphangiomatosis. A case report and literature review]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Martínez-Martínez]]></surname>
<given-names><![CDATA[Blanca Estela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez-Velasco]]></surname>
<given-names><![CDATA[Alicia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Martínez-Muñiz]]></surname>
<given-names><![CDATA[Irma]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[González-Muñiz]]></surname>
<given-names><![CDATA[Sonia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Marín-Santana]]></surname>
<given-names><![CDATA[Juan Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Mexicano del Seguro Social Centro Médico Nacional Siglo XXI ]]></institution>
<addr-line><![CDATA[Ciudad de México ]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2018</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2018</year>
</pub-date>
<volume>77</volume>
<numero>4</numero>
<fpage>280</fpage>
<lpage>285</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0028-37462018000400280&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0028-37462018000400280&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0028-37462018000400280&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: La linfangiomatosis generalizada es una entidad poco frecuente que consiste en la proliferación difusa y multifocal de vasos linfáticos anómalos que causan obstrucción del sistema. Masculino de siete años de edad que inicia 15 días antes de su ingreso al hospital con dolor referido en hombro izquierdo que motivó a realizar una radiografía de tórax detectando cardiomegalia. A la pericardiocentesis drenó 500 ml de líquido con aspecto achocolatado y, debido a que hubo recidiva, fue referido a tercer nivel de atención médica. Se realizó ventana pericárdica cuantificando 900 ml más de líquido de aspecto asalmonado indicativo de quilotórax. La tomografía computada de tórax fue compatible con linfangiomatosis, con afectación a cuello, mediastino, hueso y bazo. Presentó derrame pleural de alto gasto a pesar de recibir nutrición parenteral y octreotide intravenoso. Manifestó loculaciones en espacio pleural, por lo que se realizó decorticación, pleurodesis con biopsia de pleura y parénquima pulmonar que reportó linfangiomatosis pulmonar y pleural.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Generalized lymphangiomatosis is a rare entity that consists of difusse and multifocal proliferation of abnormal lymphatic vessels that cause system obstruction. Seven-year-old male who start 15 days before entering a hospital with referred pain in left shoulder that motivated a chest X-ray detecting cardiomegaly. A pericardiocentesis drained 500 ml of chocolate-like liquid and was referred to a third level of medical care due to the recurrence of pericardial effusion. Pericardial window was performed quantifying an additional 900 ml salmon-like liquid with chylothorax characteristics. Computed tomography was compatible with lymphangiomatosis, affecting neck, mediastinum and bone and bazo. He presented a high-expenditure bilateral pleural effusion despite receiving parenteral nutrition and intravenous octreotide; with loculations in pleural space for which pleural decortication was performed, pleurodesis and lung and pleura biopsy that reported pulmonar and pleural lymphangiomatosis.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Linfangiomatosis generalizada]]></kwd>
<kwd lng="es"><![CDATA[quilotórax]]></kwd>
<kwd lng="es"><![CDATA[derrame pleural]]></kwd>
<kwd lng="es"><![CDATA[derrame pericárdico]]></kwd>
<kwd lng="en"><![CDATA[Generalized lymphangiomatosis]]></kwd>
<kwd lng="en"><![CDATA[chylothorax]]></kwd>
<kwd lng="en"><![CDATA[pleural efussion]]></kwd>
<kwd lng="en"><![CDATA[pericardial efussion]]></kwd>
</kwd-group>
</article-meta>
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