<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1870-199X</journal-id>
<journal-title><![CDATA[Revista odontológica mexicana]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Odont. Mex]]></abbrev-journal-title>
<issn>1870-199X</issn>
<publisher>
<publisher-name><![CDATA[Universidad Nacional Autónoma de México, Facultad de Odontología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1870-199X2021000300247</article-id>
<article-id pub-id-type="doi">10.22201/fo.1870199xp.2021.25.3.83095</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Macroglosia asociada al síndrome de Beckwith-Wiedemann. Reporte de caso clínico]]></article-title>
<article-title xml:lang="en"><![CDATA[Macroglossia associated to Beckwith-Wiedemann syndrome. Clinical case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Godínez Valdespino]]></surname>
<given-names><![CDATA[Jesús A]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Nava Vera]]></surname>
<given-names><![CDATA[Bianca Yaneli]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Joya Rodríguez]]></surname>
<given-names><![CDATA[Nuria Rebeca]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Mexicano del Seguro Social  ]]></institution>
<addr-line><![CDATA[CDMX ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Instituto Politécnico Nacional  ]]></institution>
<addr-line><![CDATA[CDMX ]]></addr-line>
<country>Mexico</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidad Autónoma Metropolitana  ]]></institution>
<addr-line><![CDATA[Xochimilco Ciudad de México]]></addr-line>
<country>Mexico</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>09</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>09</month>
<year>2021</year>
</pub-date>
<volume>25</volume>
<numero>3</numero>
<fpage>247</fpage>
<lpage>256</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S1870-199X2021000300247&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S1870-199X2021000300247&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S1870-199X2021000300247&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN El síndrome de Beckwith-Wiedemann (SBW) es una patología de origen genético multifactorial, referenciado desde 1963 hasta la actualidad. Entre las características principales de este síndrome se encuentran: gigantismo, onfalocele, visceromegalia, tumores viscerales, macroglosia en 90%, la cual interfiere con la ventilación y mecánica de la deglución. El diagnóstico clínico se realiza mediante la suma de criterios mayores y menores presentes en el paciente, corroborándose con distintas pruebas genéticas. El caso clínico que se describe es de un paciente de 14 meses de edad, portador del SBW con macroglosia verdadera, intervenido quirúrgicamente por glosectomía parcial y plastia en el Departamento de Cirugía Maxilofacial Pediátrica de la UMAE Hospital General CMN La Raza. Posterior a la cirugía se consigue reducir el volumen del cuerpo lingual en 30%, creando un impacto favorable en la relación cavidad oral-lingual, aumentando el espacio hipofaríngeo y retrolingual, disminuyendo el riesgo de hipoxia por obstrucción y la interferencia en la fase mecánica de la deglución. En cuanto al mejor momento para realizar la glosectomía de reducción, consideramos que ésta depende de las condiciones generales del paciente, y el grado de interferencia con los procesos vitales, por lo que se sugiere apegarse a lo escrito en las guías de práctica clínica y protocolos hospitalarios. El SBW es una condición rara; sin embargo, presenta afección multiorgánica. La macroglosia se observa en más de 90% del total de los casos, por lo que la glosectomía en forma de «ojo de cerradura» es el procedimiento quirúrgico de elección para reducir transversal y anteroposteriormente el cuerpo lingual, por medio del cual se consigue impactar de manera positiva en la habilitación de la vía aérea y digestiva, así como en la apariencia orofacial y en la competencia de la adquisición del lenguaje oral.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Beckwith-Wiedemann syndrome (BWS) is a multifactorial genetic origin pathology, referenced from 1963 to the present. Its main characteristics are gigantism, omphalocele, visceromegaly, visceral tumors, macroglossia in 90% (which interferes with ventilation and swallowing mechanics). The clinical diagnosis is the sum of major and minor criteria present in the patient, corroborated with different genetic tests. The clinical case is of a 14-month-old male patient, carrier of BWS associated with true macroglossia. He underwent surgery for a partial glossectomy (in the pediatric maxillofacial surgery service at UMAE Hospital General CMN La Raza). After surgery, lingual body volume is reduced by 30%, creating a favorable impact on the oral-lingual cavity relationship, increasing the hypopharyngeal and retrolingual spaces, reducing hypoxia risk due to obstruction, and interference in the phase of swallowing mechanics. We think that the best time to perform the reduction glossectomy will depend on the patient's general conditions and vital processes. The recommendation is to follow what clinical practice guidelines and hospital protocols state. BWS is a rare condition. However, it has multi-organ involvement. Macroglossia is present in more than 90% of all cases. Keyhole glossectomy is the surgical procedure choice to transversely and anteroposteriorly reduce the tongue body. The positive impact is in respiratory and digestive tracts habilitation. So is in the orofacial appearance and the competence of oral language acquisition.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Beckwith-Wiedemann]]></kwd>
<kwd lng="es"><![CDATA[macroglosia]]></kwd>
<kwd lng="es"><![CDATA[glosectomía]]></kwd>
<kwd lng="es"><![CDATA[desnutrición]]></kwd>
<kwd lng="es"><![CDATA[apnea]]></kwd>
<kwd lng="en"><![CDATA[Beckwith-Wiedemann syndrome]]></kwd>
<kwd lng="en"><![CDATA[macroglossia]]></kwd>
<kwd lng="en"><![CDATA[glossectomy]]></kwd>
<kwd lng="en"><![CDATA[malnutrition]]></kwd>
<kwd lng="en"><![CDATA[apnea]]></kwd>
</kwd-group>
</article-meta>
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