<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2448-9190</journal-id>
<journal-title><![CDATA[Revista alergia México]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. alerg. Méx.]]></abbrev-journal-title>
<issn>2448-9190</issn>
<publisher>
<publisher-name><![CDATA[Colegio Mexicano de Inmunología Clínica y Alergia A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2448-91902017000100034</article-id>
<article-id pub-id-type="doi">10.29262/ram.v64i1.216</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Manifestaciones clínicas de la deficiencia de IgA]]></article-title>
<article-title xml:lang="en"><![CDATA[Clinical symptoms in IgA deficiency]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Oliveira-Serra]]></surname>
<given-names><![CDATA[Flavio Augusto De]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Mosca]]></surname>
<given-names><![CDATA[Tainá]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Menezes]]></surname>
<given-names><![CDATA[Maria da Conceição Santos de]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Forte]]></surname>
<given-names><![CDATA[Wilma Carvalho-Neves]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Santa Casa de São Paulo Facultad de Ciencias Médicas ]]></institution>
<addr-line><![CDATA[ São Paulo]]></addr-line>
<country>Brazil</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Santa Casa de São Paulo Facultad de Ciencias Médicas Departamento de Ciencias Patológicas]]></institution>
<addr-line><![CDATA[ São Paulo]]></addr-line>
<country>Brazil</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Irmandade da Santa Casa de Misericórdia de São Paulo Departamento de Pediatría y Puericultura Sector de Alergia e Inmunodeficiencias]]></institution>
<addr-line><![CDATA[ São Paulo]]></addr-line>
<country>Brasil</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2017</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2017</year>
</pub-date>
<volume>64</volume>
<numero>1</numero>
<fpage>34</fpage>
<lpage>39</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S2448-91902017000100034&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S2448-91902017000100034&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S2448-91902017000100034&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen:  Antecedentes:  La deficiencia de inmunoglobulina A (IgA) es la inmunodeficiencia primaria más frecuente. El diagnóstico oportuno y el seguimiento clínico pueden mejorar la calidad de vida de los portadores. Para ello, deben estudiarse y entenderse las manifestaciones clínicas de este trastorno.  Objetivo:  Determinar las manifestaciones clínicas de la deficiencia de IgA.  Métodos:  Estudio transversal, retrospectivo, exploratorio, realizado mediante análisis de expedientes de 39 pacientes con deficiencia de IgA. Resultados: De los pacientes analizados, 10 fueron diagnosticados con deficiencia total de IgA y 29 con deficiencia parcial. Las principales manifestaciones clínicas fueron rinoconjuntivitis y asma alérgicas. En los pacientes con deficiencia total de IgA, además de las enfermedades alérgicas se observó un mayor número de cuadros infecciosos de rinosinusitis, amigdalitis y conjuntivitis (p &lt; 0.05).  Conclusión:  En el presente estudio, las principales manifestaciones clínicas de la deficiencia de IgA fueron los cuadros alérgicos de rinoconjuntivitis y el asma; además, los pacientes portadores de deficiencia total de IgA presentaron aumento significativo de cuadros infecciosos de rinosinusitis, amigdalitis y conjuntivitis, comparados con los pacientes con deficiencia parcial de IgA.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract:  Background:  IgA deficiency is the most common primary immunodeficiency. Early diagnosis and clinical follow-up may improve the quality of life of patients with IgA deficiency. To this end, IgA deficiency should be further studied and better understood on its clinical manifestations.  Objective:  To determine IgA deficiency clinical manifestations. Methods: Cross-sectional, retrospective, exploratory study, where the medical records of 39 patients with IgA deficiency were analyzed.  Results:  Among the analyzed cases, 10 patients were diagnosed with total IgA deficiency and 29 patients with partial IgA deficiency. Partial and total IgA deficiency main clinical manifestations were allergic rhinoconjunctivitis and allergic asthma. In total IgA deficiency, in addition to allergic diseases, a statistically significant number (p &lt; 0.05) of cases of infection-related rhinosinusitis, tonsillitis and conjunctivitis were also observed.  Conclusion:  This study showed that the main clinical manifestations in IgA deficiency were allergic rhinoconjunctivitis and allergic asthma. In addition, patients with total IgA deficiency showed a significant increase in infection-related rhinosinusitis, tonsillitis and conjunctivitis, when compared with patients with partial IgA deficiency.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Inmunodeficiencias primarias]]></kwd>
<kwd lng="es"><![CDATA[Deficiencia de inmunoglobulina A]]></kwd>
<kwd lng="es"><![CDATA[Deficiencia de anticuerpos]]></kwd>
<kwd lng="en"><![CDATA[Primary immunodeficiency]]></kwd>
<kwd lng="en"><![CDATA[IgA deficiency]]></kwd>
<kwd lng="en"><![CDATA[Antibody deficiency]]></kwd>
</kwd-group>
</article-meta>
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<article-title xml:lang=""><![CDATA[Selective IgA deficiency in early life: Association to infections and allergic diseases during childhood]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Janzi]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Kull]]></surname>
<given-names><![CDATA[I]]></given-names>
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<name>
<surname><![CDATA[Sjöberg]]></surname>
<given-names><![CDATA[R]]></given-names>
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<surname><![CDATA[Wan]]></surname>
<given-names><![CDATA[J]]></given-names>
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<surname><![CDATA[Bayat]]></surname>
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<source><![CDATA[Clin Immunol]]></source>
<year>2009</year>
<volume>133</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>78-85</page-range></nlm-citation>
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</article>
