<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0187-5337</journal-id>
<journal-title><![CDATA[Perinatología y reproducción humana]]></journal-title>
<abbrev-journal-title><![CDATA[Perinatol. Reprod. Hum.]]></abbrev-journal-title>
<issn>0187-5337</issn>
<publisher>
<publisher-name><![CDATA[Instituto Nacional de Perinatología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0187-53372022000200056</article-id>
<article-id pub-id-type="doi">10.24875/per.21000001</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Asociación MURCS: reporte de caso de un recién nacido de sexo femenino]]></article-title>
<article-title xml:lang="en"><![CDATA[MURCS association: case report in a female newborn]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ostia-Garza]]></surname>
<given-names><![CDATA[Patricia J.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Jiménez-Díaz]]></surname>
<given-names><![CDATA[Luis D.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Plaza-Benhumea]]></surname>
<given-names><![CDATA[Lautaro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Materno Perinatal Mónica Pretelini Sáenz Servicio de Neonatología ]]></institution>
<addr-line><![CDATA[Toluca de Lerdo Edo]]></addr-line>
<country>México</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Materno Perinatal Mónica Pretelini Sáenz Servicio de Genética ]]></institution>
<addr-line><![CDATA[Toluca de Lerdo Edo]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>36</volume>
<numero>2</numero>
<fpage>56</fpage>
<lpage>60</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0187-53372022000200056&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0187-53372022000200056&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0187-53372022000200056&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Antecedentes: El término MURCS se aplica a la asociación preferencial de aplasia de derivados müllerianos y renales y anomalías de vértebras cervicotorácicas. La etiología es desconocida, suele ser esporádica.  Objetivos: Describir el caso de una recién nacida de asociación MURCS con defectos adicionales y discutir posibles mecanismos patogénicos y etiología.  Discusión: El espectro de MURCS se desconoce. Las alteraciones vertebrales, urogenitales y rectales pueden explicarse por fallas en las interacciones entre los precursores embrionarios, los que tempranamente en el desarrollo tienen una estrecha relación espacial: mesodermo paraxil (columna vertebral), intermedio (uréteres y riñones) y lateral (epitelio celómico: adrenales, ovarios, útero; tabique urorrectal: ano). Se enfatiza en la importancia de la búsqueda activa de las otras anomalías diferentes a las müllerianas para lograr el diagnóstico y realizar un manejo integral e interdisciplinario.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Background: MURCS refers to the preferential association of müllerian duct and kidney aplasia and cervicothoracic vertebrae anomalies. Of unknown etiology, it is usually sporadic.  Objectives: To describe newborn female case of MURCS with additional anomalies and to discuss possible pathogenetic mechanisms and etiology.  Discussion: The spectrum of MURCS is unknown. Vertebral, urogenital and anal defects can be explained by abnormal interactions between the embryonic precursors that show a close spatial relationship during early development: paraxial (spine), intermediate (ureters, kidney), and lateral mesoderm (coelomic epithelium: adrenal glands, ovaries, uterus; uro-rectal septum: anus). We emphasize the importance of interdisciplinary care, including a clinical geneticist in the care of patients with these characteristics.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[MURCS]]></kwd>
<kwd lng="es"><![CDATA[Recurrencia]]></kwd>
<kwd lng="es"><![CDATA[Conducto de Müller]]></kwd>
<kwd lng="es"><![CDATA[Anomalías congénitas]]></kwd>
<kwd lng="es"><![CDATA[Escoliosis]]></kwd>
<kwd lng="en"><![CDATA[MURCS]]></kwd>
<kwd lng="en"><![CDATA[Recurrence]]></kwd>
<kwd lng="en"><![CDATA[Müllerian duct]]></kwd>
<kwd lng="en"><![CDATA[Congenital abnormalities]]></kwd>
<kwd lng="en"><![CDATA[Scoliosis]]></kwd>
</kwd-group>
</article-meta>
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