<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>0035-0052</journal-id>
<journal-title><![CDATA[Revista mexicana de pediatría]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. mex. pediatr.]]></abbrev-journal-title>
<issn>0035-0052</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Mexicana de Pediatría A.C.]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S0035-00522020000300111</article-id>
<article-id pub-id-type="doi">10.35366/94842</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Hemangioendotelioma kaposiforme gigante con fenómeno de Kasabach-Merritt]]></article-title>
<article-title xml:lang="en"><![CDATA[Kaposiform haemangioendothelioma with Kasabach-Merritt phenomenon, literature review]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Medina-López]]></surname>
<given-names><![CDATA[Yuliana Montserrat]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sánchez-Grijalva]]></surname>
<given-names><![CDATA[Claudia Ivette]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[García-López]]></surname>
<given-names><![CDATA[José Saúl]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Campos-Félix]]></surname>
<given-names><![CDATA[Lucero Beatriz]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Calderón-Alvarado]]></surname>
<given-names><![CDATA[Ana Beatriz]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto Mexicano del Seguro Social Hospital General Regional No. 1 Departamento de Pediatría]]></institution>
<addr-line><![CDATA[Ciudad Obregón Sonora]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>06</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>06</month>
<year>2020</year>
</pub-date>
<volume>87</volume>
<numero>3</numero>
<fpage>111</fpage>
<lpage>114</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_arttext&amp;pid=S0035-00522020000300111&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_abstract&amp;pid=S0035-00522020000300111&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.org.mx/scielo.php?script=sci_pdf&amp;pid=S0035-00522020000300111&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen:  Introducción:  El hemangioendotelioma kaposiforme es un tumor vascular raro de crecimiento rápido, su principal complicación es el fenómeno de Kasabach-Merritt que se caracteriza por una trombocitopenia grave, coagulopatía por consumo y púrpura.  Caso clínico: Se expone el caso de un recién nacido en quien desde el nacimiento se detectó aumento de volumen en extremidad superior izquierda. Mediante resonancia magnética se llegó al diagnóstico. Se inició manejo con esteroides y quimioterapia; sin embargo, la evolución fue tórpida y falleció en la primera semana de vida. El diagnóstico se confirmó en autopsia.  Conclusiones:  En pacientes con tumoración vascular de crecimiento rápido, se deben buscar alteraciones hematológicas y extensión de la lesión a fin de brindar tratamiento oportuno.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract:  Introduction:  Kaposiform hemangioendothelioma is a rare, fast growing vascular tumor. Its main complication is the Kasabach-Merritt phenomenon, which is characterized by severe thrombocytopenia, consumption coagulation disorder, and purpura.  Case report:  We present a male newborn in whom it was detected that the left upper limb was very thickened from birth. Using magnetic resonance imaging, the diagnosis was reached. Management with steroids and chemotherapy was started, however the evolution was torpid and he died in the first week of life. The diagnosis was confirmed at autopsy.  Conclusions:  Patients with a rapidly growing vascular tumor should look for hematological alterations its extent in order to give timely treatment.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Hemangioendotelioma]]></kwd>
<kwd lng="es"><![CDATA[Kasabach-Merritt]]></kwd>
<kwd lng="es"><![CDATA[coagulación intravascular diseminada]]></kwd>
<kwd lng="es"><![CDATA[recién nacido]]></kwd>
<kwd lng="en"><![CDATA[Haemangioendothelioma]]></kwd>
<kwd lng="en"><![CDATA[Kasabach-Merritt]]></kwd>
<kwd lng="en"><![CDATA[disseminated intravascular coagulation]]></kwd>
<kwd lng="en"><![CDATA[newborn]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Croteau]]></surname>
<given-names><![CDATA[SE]]></given-names>
</name>
<name>
<surname><![CDATA[Liang]]></surname>
<given-names><![CDATA[MG]]></given-names>
</name>
<name>
<surname><![CDATA[Kozakewich]]></surname>
<given-names><![CDATA[HP]]></given-names>
</name>
<name>
<surname><![CDATA[Alomari]]></surname>
<given-names><![CDATA[AI]]></given-names>
</name>
<name>
<surname><![CDATA[Fishman]]></surname>
<given-names><![CDATA[SJ]]></given-names>
</name>
<name>
<surname><![CDATA[Mulliken]]></surname>
<given-names><![CDATA[JB]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Kaposiform hemangioendothelioma: atypical features and risk of a Kasabach-Merritt phenomenon in 107 referrals]]></article-title>
<source><![CDATA[J Pediatr]]></source>
<year>2013</year>
<volume>162</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>142-7</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[O&#8217;Rafferty]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[O&#8217;Regan]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Irvine]]></surname>
<given-names><![CDATA[AD]]></given-names>
</name>
<name>
<surname><![CDATA[Smith]]></surname>
<given-names><![CDATA[OP]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Recent advances in the pathobiology and management of Kasabach-Merritt phenomenon]]></article-title>
<source><![CDATA[Br J Haematol]]></source>
<year>2015</year>
<volume>171</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>38-51</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Cotran]]></surname>
<given-names><![CDATA[RS]]></given-names>
</name>
<name>
<surname><![CDATA[Kumar]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Robbins]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
</person-group>
<source><![CDATA[Robbins Patología Estructural y Funcional]]></source>
<year>2005</year>
<edition>6</edition>
<publisher-loc><![CDATA[Madrid ]]></publisher-loc>
<publisher-name><![CDATA[McGraw-Hill Inc./Interamericana de España]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Adams]]></surname>
<given-names><![CDATA[DM]]></given-names>
</name>
<name>
<surname><![CDATA[Brandão]]></surname>
<given-names><![CDATA[LR]]></given-names>
</name>
<name>
<surname><![CDATA[Peterman]]></surname>
<given-names><![CDATA[CM]]></given-names>
</name>
<name>
<surname><![CDATA[Gupta]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Patel]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Fishman]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Vascular anomaly cases for the pediatric hematologist oncologists-An interdisciplinary review]]></article-title>
<source><![CDATA[Pediatr Blood Cancer]]></source>
<year>2018</year>
<volume>65</volume>
<numero>1</numero>
<issue>1</issue>
</nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Arabi,]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[López]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Hemangiomatosis neonatal difusa. Presentación de un caso y revisión de la literatura]]></article-title>
<source><![CDATA[Rev Mex Pediatr]]></source>
<year>2000</year>
<volume>67</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>270-3</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Rodríguez]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Benavides]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Sirolimus (rapamicina) en pacientes con hemangioendotelioma kaposiforme. Caso clínico]]></article-title>
<source><![CDATA[Rev Chil Pediatr]]></source>
<year>2013</year>
<volume>84</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>537-44</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
