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Revista odontológica mexicana
versión impresa ISSN 1870-199X
Rev. Odont. Mex vol.10 no.4 Ciudad de México dic. 2006
https://doi.org/10.22201/fo.1870199xp.2006.10.4.15892
Casos clínicos
Dentinogénesis imperfecta: Reporte de un caso
Dentinogenesis imperfect: Case report
* Alumna. Especialidad de Odontopediatría DEPeI. Facultad de Odontología, UNAM
§ Profesor. Especialidad de Odontopediatría DEPeI. Facultad de Odontología, UNAM
II Coordinador. Especialidad de Odontopediatría DEPeI. Facultad de Odontología, UNAM
Introducción
La dentinogénesis imperfecta (DI) es una alteración hereditaria que se origina en la etapa de histodiferenciación durante la odontogénesis, constituyendo una forma de displasia mesodérmica localizada, caracterizada por una expresa alteración de las proteínas dentinarias. Se clasifica en dentinogénesis tipo I (relacionada con osteogenesis imperfecta), DI tipo II (no relacionada con OI) y DI tipo III (de Brandynwine).
Objetivo
Determinar el tipo de dentinogénesis, tendencia familiar y características clínicas del paciente, para establecer un diagnóstico temprano y el patrón hereditario que presenta.
Presentación del caso
Paciente masculino de 3 años de edad, acudió a consulta por hipersensibilidad dental y molestia durante la masticación; presentó una alteración de estructura y color de los órganos dentales presentes, abscesos, atriccion y pérdida de la dimensión vertical, radiográficamente se observa obliteración pulpar, marcada constricción cervical y raíces cortas. Después de los análisis clínico y radiográfico, historia familiar e de sexo. Se restauró con coronas de acero cromo y se realizaron las extracciones necesarias, continuando con la colocación de mantenedores de espacio y prótesis parciales removibles.
Conclusión
Debido a que en los pacientes con DI, la primera dentición se ve más afectada, es de suma importancia realizar un diagnóstico temprano para iniciar cuanto antes un tratamiento adecuado. En este tipo de pacientes es imprescindible llevar a cabo interconsulta con genetica para descartar su asociación con otras entidades.
Palabras clave: Dentinogénesis imperfecta; odontogénesis imperfecta; dentina opalescente; dentina opalescente hereditaria
Introduction
Dentinogenesis imperfect (DI) is an inherited condition originated in the histodifferentiation stage during odontogenesis, constituting a localized mesodermal dysplasia form, characterized by an expressed alteration of dentin proteins. There are three types of dentinogenesis imperfect: Type I (associated with osteogenesis imperfect Ol), type II (not associated with Ol), and type III (Brandywine's).
Objectives
To determine the type of dentinogenesis, family history trend and clinical characteristics of the patient, to establish early diagnosis and heredi tary pattern.
Case report
A 3-year-old boy patient was referred to the clinic with dental hypersensitivity and pain during mastication. He presented a structure anomaly and discoloration of erupted teeth, abscesses, attrition and loss of vertical dimenSion. Radiographs showed obliterated pulp chambers, marked cervical constriction and short roots. After clinical and radiographic analysis, family history and consultation with Genetics, there was no relation with Ol. A diagnosis of dentinogenesis imperfect type II was made, transmitted as an autosomal dominant trait, without gender predilection. Restorative treatment involved stainless steel crowns, extractions, space maintainer and removable partial denture placement.
Conclusion
Early diagnosis and treatment of DI is recommended because of the severe alterations of primary dentition. In this kind of patients it is very important to carry out consultations with Genetics to discard any association with other disorders.
Key words: Dentinogenesis imperfect; odontogenesis imperfect; opalescent dentin; hereditary opalescent dentin
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